{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T14:50:59Z","timestamp":1787755859105,"version":"build-2784847793"},"reference-count":12,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"4","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"abstract":"<jats:sec>\n                    <jats:title>Case:<\/jats:title>\n                    <jats:p>Vohwinkel syndrome is a rare, inherited condition marked by defective keratinization. The disorder may feature digital constriction bands (pseudoainhum) which can lead to autoamputation. Surgical excision is the only treatment of pseudoainhum; however, it is fraught with recurrence. We present a 10-year-old boy with pseudoainhum of the right long and small fingers at the distal interphalangeal joints. He underwent 180-degree band excision and z-plasty.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion:<\/jats:title>\n                    <jats:p>Since establishing care 8 years ago, he has undergone treatment of 5 constriction bands with only 1 recurrence. We believe this success can at least be partially attributed to the technique described by Upton.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.2106\/jbjs.cc.24.00251","type":"journal-article","created":{"date-parts":[[2024,11,7]],"date-time":"2024-11-07T14:00:38Z","timestamp":1730988038000},"update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":1,"title":["Long-Term Surgical Success in Treating Vohwinkel Syndrome"],"prefix":"10.2106","volume":"14","author":[{"given":"Kirby W.","family":"Bonvillain","sequence":"first","affiliation":[{"name":"Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute\u2014Carolinas Medical Center, Charlotte, North Carolina"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9918-373X","authenticated-orcid":false,"given":"Andrew B.","family":"Rees","sequence":"additional","affiliation":[{"name":"Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute\u2014Carolinas Medical Center, Charlotte, North Carolina"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5315-1978","authenticated-orcid":false,"given":"Katherine D.","family":"Drexelius","sequence":"additional","affiliation":[{"name":"Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute\u2014Carolinas Medical Center, Charlotte, North Carolina"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0009-0009-8787-378X","authenticated-orcid":false,"given":"Ryan","family":"Serbin","sequence":"additional","affiliation":[{"name":"Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute\u2014Carolinas Medical Center, Charlotte, North Carolina"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4408-9209","authenticated-orcid":false,"given":"Michael W.","family":"Aversano","sequence":"additional","affiliation":[{"name":"OrthoCarolina Hand Center, Charlotte, North Carolina"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7601-8571","authenticated-orcid":false,"given":"R. Glenn","family":"Gaston","sequence":"additional","affiliation":[{"name":"Department of Orthopaedic Surgery, Atrium Health Musculoskeletal Institute\u2014Carolinas Medical Center, Charlotte, North Carolina"},{"name":"OrthoCarolina Hand Center, Charlotte, North Carolina"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2024,10]]},"reference":[{"issue":"4","key":"bib1-20241107","doi-asserted-by":"crossref","first-page":"365","DOI":"10.4103\/idoj.IDOJ_367_18","article-title":"Hereditary palmoplantar keratoderma: a practical approach to the diagnosis","volume":"10","author":"Dev","year":"2019","journal-title":"Indian Dermatol Online J."},{"issue":"2","key":"bib3-20241107","doi-asserted-by":"crossref","first-page":"235","DOI":"10.1177\/1753193408098901","article-title":"Keratoderma hereditarium mutilans (Vohwinkel syndrome)","volume":"34","author":"Sinha","year":"2009","journal-title":"J Hand Surg Eur."},{"issue":"5","key":"bib4-20241107","doi-asserted-by":"crossref","first-page":"1276","DOI":"10.1097\/00006534-200110000-00027","article-title":"Keratoderma hereditarium mutilans (Vohwinkel syndrome): an unsolved surgical mystery","volume":"108","author":"Atabay","year":"2001","journal-title":"Plast Reconstr Surg."},{"issue":"3","key":"bib5-20241107","doi-asserted-by":"crossref","first-page":"338","DOI":"10.1016\/S0266-7681(05)80090-7","article-title":"Surgical correction of pseudoainhum in Vohwinkel syndrome","volume":"20","author":"Pisoh","year":"1995","journal-title":"J Hand Surg Br."},{"issue":"2","key":"bib6-20241107","doi-asserted-by":"crossref","first-page":"269","DOI":"10.1016\/S0363-5023(86)80068-5","article-title":"Keratoderma hereditarium mutilans: report of a case with successful surgical treatment","volume":"11","author":"Luk","year":"1986","journal-title":"J Hand Surg Am."},{"issue":"4","key":"bib7-20241107","doi-asserted-by":"crossref","first-page":"8868","DOI":"10.4081\/or.2020.8868","article-title":"What's the resolutive surgery for pseudoainhum in Vohwinkel syndrome? A case report and review of the literature","volume":"12","author":"Rovere","year":"2021","journal-title":"Orthop Rev (Pavia)."},{"issue":"6","key":"bib8-20241107","doi-asserted-by":"crossref","first-page":"e2762","DOI":"10.1097\/MD.0000000000002762","article-title":"Using a distant abdominal skin flap to treat digital constriction bands: a case report for Vohwinkel syndrome","volume":"95","author":"Zhang","year":"2016","journal-title":"Medicine (Baltimore)."},{"issue":"4","key":"bib9-20241107","doi-asserted-by":"crossref","first-page":"444","DOI":"10.1111\/ced.13770","article-title":"Loricrin palmoplantar keratoderma: full-thickness skin grafting for pseudoainhum","volume":"44","author":"Zamiri","year":"2019","journal-title":"Clin Exp Dermatol."},{"issue":"1","key":"bib10-20241107","doi-asserted-by":"crossref","first-page":"102","DOI":"10.1007\/s11552-012-9458-5","article-title":"Successful surgical management of keratoderma hereditaria mutilans","volume":"8","author":"Liebman","year":"2013","journal-title":"HAND."},{"issue":"1","key":"bib11-20241107","doi-asserted-by":"crossref","first-page":"128e","DOI":"10.1097\/PRS.0b013e3181a80777","article-title":"Reconstruction of congenital differences of the hand","volume":"124","author":"Bates","year":"2009","journal-title":"Plast Reconstr Surg."},{"issue":"5","key":"bib12-20241107","doi-asserted-by":"crossref","first-page":"947","DOI":"10.1016\/S0363-5023(10)80166-2","article-title":"Correction of constriction rings","volume":"16","author":"Upton","year":"1991","journal-title":"J Hand Surg Am."},{"issue":"10","key":"bib13-20241107","doi-asserted-by":"crossref","first-page":"1012","DOI":"10.1016\/j.jdcr.2020.07.029","article-title":"Surgical management of pseudoainhum in loricrin keratoderma","volume":"6","author":"Singh","year":"2020","journal-title":"JAAD Case Rep."}],"container-title":["JBJS Case Connector"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.2106\/JBJS.CC.24.00251","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T13:52:44Z","timestamp":1787752364000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/10.2106\/JBJS.CC.24.00251"}},"subtitle":["A Case Report"],"short-title":[],"issued":{"date-parts":[[2024,10]]},"references-count":12,"journal-issue":{"issue":"4","published-online":{"date-parts":[[2024]]}},"URL":"https:\/\/doi.org\/10.2106\/jbjs.cc.24.00251","relation":{},"ISSN":["2160-3251"],"issn-type":[{"value":"2160-3251","type":"electronic"}],"subject":[],"published":{"date-parts":[[2024,10]]}}}