{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T14:18:30Z","timestamp":1787753910322,"version":"build-2784847793"},"reference-count":12,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"abstract":"<jats:sec>\n                    <jats:title>Case:<\/jats:title>\n                    <jats:p>A 40-month-old nonambulatory girl with Aicardi-Gouti\u00e8res syndrome presented with spastic dystonic quadriplegia and painful right hip dislocation. Radiographs showed right hip dislocation with acetabular dysplasia. She underwent adductor tenotomy, open reduction, and proximal femur varus derotation osteotomy, achieving stable hip containment. Acetabular index and migration percentage improved from 42\u00b0 and 100% at presentation to 26\u00b0 and 31%, respectively, at the 40-month follow-up.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion:<\/jats:title>\n                    <jats:p>This is the first report of spastic hip dislocation in Aicardi-Gouti\u00e8res syndrome. The case underscores the importance of structured hip surveillance to detect early hip migration in children with severe spasticity and prevent late dislocation.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.2106\/jbjs.cc.25.00482","type":"journal-article","created":{"date-parts":[[2026,4,15]],"date-time":"2026-04-15T18:00:30Z","timestamp":1776276030000},"update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":0,"title":["Spastic Hip Dislocation in a Child With Aicardi-Gouti\u00e8res Syndrome"],"prefix":"10.2106","volume":"16","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6474-4285","authenticated-orcid":false,"given":"Vivek","family":"Sodhai","sequence":"first","affiliation":[{"name":"Department of Paediatric Orthopaedics, Sancheti Institute for Orthopaedics and Rehabilitation, Pune, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Amit","family":"Wakekar","sequence":"additional","affiliation":[{"name":"Department of Paediatric Orthopaedics, Sancheti Institute for Orthopaedics and Rehabilitation, Pune, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8536-6153","authenticated-orcid":false,"given":"Abhijeet","family":"Botre","sequence":"additional","affiliation":[{"name":"Department of Paediatric Neurology, KEM Hospital and Research Centre, Pune, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8821-9730","authenticated-orcid":false,"given":"Sandeep","family":"Patwardhan","sequence":"additional","affiliation":[{"name":"Department of Paediatric Orthopaedics, Sancheti Institute for Orthopaedics and Rehabilitation, Pune, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2026,4]]},"reference":[{"issue":"7","key":"bib2-20260415","doi-asserted-by":"crossref","first-page":"429","DOI":"10.1038\/nri3850","article-title":"Aicardi-Gouti\u00e8res syndrome and the type I interferonopathies","volume":"15","author":"Crow","year":"2015","journal-title":"Nat Rev Immunol."},{"issue":"1","key":"bib3-20260415","doi-asserted-by":"crossref","first-page":"35","DOI":"10.1186\/s12969-016-0094-4","article-title":"Type I interferonopathies in pediatric rheumatology. 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