{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,18]],"date-time":"2026-08-18T14:04:43Z","timestamp":1787061883908,"version":"build-2736575974"},"reference-count":151,"publisher":"Informa UK Limited","license":[{"start":{"date-parts":[[2022,10,1]],"date-time":"2022-10-01T00:00:00Z","timestamp":1664582400000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/3.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["JIR"],"DOI":"10.2147\/jir.s343261","type":"journal-article","created":{"date-parts":[[2022,10,9]],"date-time":"2022-10-09T15:45:15Z","timestamp":1665330315000},"page":"5739-5755","source":"Crossref","is-referenced-by-count":15,"title":["Improving Diagnosis and Clinical Management of Acquired Systemic Autoinflammatory Diseases"],"prefix":"10.2147","volume":"Volume 15","author":[{"given":"Adam","family":"Al-Hakim","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anoop","family":"Mistry","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7910-0554","authenticated-orcid":true,"given":"Sinisa","family":"Savic","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"301","published-online":{"date-parts":[[2022,10]]},"reference":[{"key":"ref1","doi-asserted-by":"publisher","first-page":"222","DOI":"10.1038\/s41584-020-0377-5","volume":"16","author":"Savic","year":"2020","journal-title":"Nat Rev Rheumatol"},{"key":"ref2","doi-asserted-by":"publisher","first-page":"86336","DOI":"10.1172\/jci.insight.86336","volume":"1","author":"Harrison","year":"2016","journal-title":"JCI Insight"},{"key":"ref3","doi-asserted-by":"publisher","first-page":"2628","DOI":"10.1056\/NEJMoa2026834","volume":"383","author":"Beck","year":"2020","journal-title":"N Engl J Med"},{"key":"ref4","doi-asserted-by":"publisher","first-page":"1410","DOI":"10.3389\/fimmu.2017.01410","volume":"8","author":"Rowczenio","year":"2017","journal-title":"Front Immunol"},{"key":"ref5","doi-asserted-by":"publisher","first-page":"907","DOI":"10.1136\/annrheumdis-2021-221801","volume":"81","author":"Romano","year":"2022","journal-title":"Ann Rheum Dis"},{"key":"ref6","doi-asserted-by":"publisher","first-page":"100863","DOI":"10.1016\/j.mam.2020.100863","volume":"76","author":"Bauer","year":"2020","journal-title":"Mol Aspects Med"},{"key":"ref7","doi-asserted-by":"publisher","first-page":"1135","DOI":"10.1038\/ng.3066","volume":"46","author":"Romberg","year":"2014","journal-title":"Nat Genet"},{"key":"ref8","doi-asserted-by":"publisher","first-page":"2385","DOI":"10.1084\/jem.20141091","volume":"211","author":"Kitamura","year":"2014","journal-title":"J Exp Med"},{"key":"ref9","doi-asserted-by":"publisher","first-page":"1140","DOI":"10.1038\/ng.3089","volume":"46","author":"Canna","year":"2014","journal-title":"Nat Genet"},{"key":"ref10","doi-asserted-by":"publisher","first-page":"498","DOI":"10.1177\/1093526616686890","volume":"20","author":"Liang","year":"2017","journal-title":"Pediatr Dev Pathol"},{"key":"ref11","doi-asserted-by":"publisher","first-page":"447","DOI":"10.1002\/art.39960","volume":"69","author":"Kawasaki","year":"2017","journal-title":"Arthritis Rheumatol"},{"key":"ref12","volume":"2022","author":"Wang","year":"2022","journal-title":"Ann Rheum Dis"},{"key":"ref13","doi-asserted-by":"publisher","first-page":"692","DOI":"10.1002\/art.41999","volume":"74","author":"Ionescu","year":"2022","journal-title":"Arthritis Rheumatol"},{"key":"ref14","doi-asserted-by":"publisher","first-page":"727","DOI":"10.1038\/ni.2913","volume":"15","author":"Franklin","year":"2014","journal-title":"Nat Immunol"},{"key":"ref15","doi-asserted-by":"publisher","first-page":"738","DOI":"10.1038\/ni.2919","volume":"15","author":"Baroja-Mazo","year":"2014","journal-title":"Nat Immunol"},{"key":"ref16","doi-asserted-by":"publisher","first-page":"974","DOI":"10.1182\/blood-2017-10-810366","volume":"131","author":"Rowczenio","year":"2018","journal-title":"Blood"},{"key":"ref17","doi-asserted-by":"publisher","first-page":"1254","DOI":"10.1016\/j.jaci.2019.11.035","volume":"145","author":"Louvrier","year":"2020","journal-title":"J Allergy Clin Immunol"},{"key":"ref18","doi-asserted-by":"publisher","first-page":"818","DOI":"10.1016\/j.semarthrit.2013.12.002","volume":"43","author":"Cantarini","year":"2014","journal-title":"Semin Arthritis Rheum"},{"key":"ref19","doi-asserted-by":"publisher","first-page":"2044","DOI":"10.1002\/art.39683","volume":"68","author":"Rowczenio","year":"2016","journal-title":"Arthritis Rheumatol"},{"key":"ref20","doi-asserted-by":"publisher","DOI":"10.1002\/mgg3.791","volume":"7","author":"Kontzias","year":"2019","journal-title":"Mol Genet Genomic Med"},{"key":"ref21","doi-asserted-by":"publisher","first-page":"3035","DOI":"10.1002\/art.39770","volume":"68","author":"Mensa-Vilaro","year":"2016","journal-title":"Arthritis Rheumatol"},{"key":"ref22","doi-asserted-by":"publisher","first-page":"562","DOI":"10.1111\/all.12129","volume":"68","author":"Simon","year":"2013","journal-title":"Allergy Eur J Allergy Clin Immunol"},{"key":"ref23","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1186\/2045-7022-4-41","volume":"4","author":"De Koning","year":"2014","journal-title":"Clin Transl Allergy"},{"key":"ref24","doi-asserted-by":"publisher","first-page":"2121","DOI":"10.1002\/art.41030","volume":"71","author":"Pathak","year":"2019","journal-title":"Arthritis Rheumatol"},{"key":"ref25","doi-asserted-by":"publisher","DOI":"10.1111\/all.15411","author":"Louvrier","year":"2022","journal-title":"Allergy"},{"key":"ref26","doi-asserted-by":"publisher","first-page":"2522","DOI":"10.1182\/blood-2012-09-457101","volume":"121","author":"Varettoni","year":"2013","journal-title":"Blood"},{"key":"ref27","doi-asserted-by":"publisher","first-page":"115","DOI":"10.1038\/nature09671","volume":"470","author":"Ngo","year":"2011","journal-title":"Nature"},{"key":"ref28","doi-asserted-by":"publisher","first-page":"3","DOI":"10.4049\/jimmunol.1203103","volume":"190","author":"Warner","year":"2013","journal-title":"J Immunol"},{"key":"ref29","doi-asserted-by":"publisher","first-page":"875","DOI":"10.1016\/j.jacc.2017.12.037","volume":"71","author":"Sano","year":"2018","journal-title":"J Am Coll Cardiol"},{"key":"ref30","doi-asserted-by":"publisher","first-page":"e393","DOI":"10.1016\/S2352-3026(18)30109-1","volume":"5","author":"Basiorka","year":"2018","journal-title":"Lancet Haematol"},{"key":"ref31","doi-asserted-by":"publisher","first-page":"2960","DOI":"10.1182\/blood-2016-07-730556","volume":"128","author":"Basiorka","year":"2016","journal-title":"Blood"},{"key":"ref32","doi-asserted-by":"publisher","first-page":"1380","DOI":"10.1007\/s10875-021-01038-y","volume":"41","author":"Claves","year":"2021","journal-title":"J Clin Immunol"},{"key":"ref33","doi-asserted-by":"publisher","first-page":"704","DOI":"10.55563\/clinexprheumatol\/1r3i7i","volume":"39","author":"Paladini","year":"2021","journal-title":"Clin Exp Rheumatol"},{"key":"ref34","doi-asserted-by":"publisher","first-page":"636","DOI":"10.1016\/j.semarthrit.2020.05.002","volume":"50","author":"Betrains","year":"2020","journal-title":"Semin Arthritis Rheum"},{"key":"ref35","doi-asserted-by":"publisher","first-page":"2486","DOI":"10.1016\/j.jaip.2021.01.024","volume":"9","author":"Bonnekoh","year":"2021","journal-title":"J Allergy Clin Immunol Pract"},{"key":"ref36","doi-asserted-by":"publisher","first-page":"3847","DOI":"10.1007\/s10067-020-05204-2","volume":"39","author":"Yan","year":"2020","journal-title":"Clin Rheumatol"},{"key":"ref37","first-page":"1","volume":"13","author":"Huang","year":"2022","journal-title":"Front Immunol"},{"key":"ref38","volume-title":"Textbook of Autoinflammation","year":"2019"},{"key":"ref39","doi-asserted-by":"publisher","first-page":"1683","DOI":"10.1007\/s10067-016-3308-8","volume":"35","author":"Sfriso","year":"2016","journal-title":"Clin Rheumatol"},{"key":"ref40","doi-asserted-by":"publisher","first-page":"221","DOI":"10.2188\/jea.7.221","volume":"7","author":"Wakai","year":"1997","journal-title":"J Epidemiol"},{"key":"ref41","doi-asserted-by":"publisher","first-page":"587","DOI":"10.1136\/ard.54.7.587","volume":"54","author":"Magadur-Joly","year":"1995","journal-title":"Ann Rheum Dis"},{"key":"ref42","doi-asserted-by":"publisher","first-page":"250","DOI":"10.26444\/aaem\/132451","volume":"28","author":"Bogdan","year":"2021","journal-title":"Ann Agric Environ Med"},{"key":"ref43","doi-asserted-by":"publisher","first-page":"48","DOI":"10.1080\/03009740510026616","volume":"35","author":"Evensen","year":"2006","journal-title":"Scand J Rheumatol"},{"key":"ref44","doi-asserted-by":"publisher","first-page":"1218","DOI":"10.1136\/annrheumdis-2020-eular.1738","volume":"79","author":"Hocevar","year":"2020","journal-title":"Ann Rheum Dis"},{"key":"ref45","doi-asserted-by":"publisher","first-page":"1284","DOI":"10.1136\/annrheumdis-2015-eular.1929","volume":"74","author":"Balci","year":"2015","journal-title":"Ann Rheum Dis"},{"key":"ref46","doi-asserted-by":"publisher","first-page":"469","DOI":"10.1016\/j.semarthrit.2019.04.004","volume":"49","author":"Mehta","year":"2019","journal-title":"Semin Arthritis Rheum"},{"key":"ref47","doi-asserted-by":"publisher","first-page":"24","DOI":"10.1016\/j.jaut.2018.07.018","author":"Giacomelli","year":"2018","journal-title":"J Autoimmun"},{"key":"ref48","doi-asserted-by":"publisher","first-page":"2633","DOI":"10.3390\/jcm10122633","volume":"10","author":"Mitrovic","year":"2021","journal-title":"J Clin Med"},{"key":"ref49","doi-asserted-by":"publisher","first-page":"8","DOI":"10.1016\/j.clim.2016.05.010","volume":"169","author":"Inoue","year":"2016","journal-title":"Clin Immunol"},{"key":"ref50","doi-asserted-by":"publisher","first-page":"53","DOI":"10.1007\/s12026-014-8561-9","volume":"61","author":"Jamilloux","year":"2014","journal-title":"Immunol Res"},{"key":"ref51","doi-asserted-by":"publisher","first-page":"4844","DOI":"10.1093\/rheumatology\/keaa904","volume":"60","author":"Berardicurti","year":"2021","journal-title":"Rheumatology"},{"key":"ref52","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1038\/s41598-021-99269-x","volume":"12","author":"Kishida","year":"2022","journal-title":"Sci Rep"},{"key":"ref53","doi-asserted-by":"publisher","DOI":"10.55563\/clinexprheumatol\/0215kv","author":"Di Cola","year":"2022","journal-title":"Clin Exp Rheumatol"},{"key":"ref54","doi-asserted-by":"publisher","first-page":"749","DOI":"10.1586\/1744666X.2015.1037287","volume":"11","author":"Colafrancesco","year":"2015","journal-title":"Expert Rev Clin Immunol"},{"key":"ref55","doi-asserted-by":"publisher","first-page":"285","DOI":"10.1016\/j.jbspin.2017.05.011","volume":"85","author":"Mitrovic","year":"2018","journal-title":"Jt Bone Spine"},{"key":"ref56","doi-asserted-by":"publisher","first-page":"2735","DOI":"10.1007\/s10067-020-05041-3","volume":"39","author":"Zhou","year":"2020","journal-title":"Clin Rheumatol"},{"key":"ref57","doi-asserted-by":"publisher","first-page":"621","DOI":"10.1016\/j.semarthrit.2015.10.003","volume":"45","author":"Hofheinz","year":"2016","journal-title":"Semin Arthritis Rheum"},{"key":"ref58","doi-asserted-by":"publisher","first-page":"194","DOI":"10.1097\/00005792-200205000-00003","volume":"81","author":"Fautrel","year":"2002","journal-title":"Medicine"},{"key":"ref59","doi-asserted-by":"publisher","first-page":"578","DOI":"10.1016\/j.semarthrit.2017.07.005","volume":"47","author":"Lebrun","year":"2018","journal-title":"Semin Arthritis Rheum"},{"key":"ref60","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1155\/2019\/3293145","volume":"2019","author":"Gaggiano","year":"2019","journal-title":"Mediators Inflamm"},{"key":"ref61","doi-asserted-by":"publisher","first-page":"2021","DOI":"10.1007\/s10067-018-4178-z","volume":"37","author":"Li","year":"2018","journal-title":"Clin Rheumatol"},{"key":"ref62","doi-asserted-by":"publisher","first-page":"15970","DOI":"10.1073\/pnas.1520779112","volume":"112","author":"Ombrello","year":"2015","journal-title":"Proc Natl Acad Sci U S A"},{"key":"ref63","doi-asserted-by":"publisher","first-page":"102562","DOI":"10.1016\/j.jaut.2020.102562","volume":"116","author":"Teng","year":"2021","journal-title":"J Autoimmun"},{"key":"ref64","doi-asserted-by":"publisher","first-page":"1469","DOI":"10.1002\/art.1780241203","volume":"24","author":"Terkeltaub","year":"1981","journal-title":"Arthritis Rheum"},{"key":"ref65","doi-asserted-by":"publisher","first-page":"415","DOI":"10.1002\/art.1780290316","volume":"29","author":"Wouters","year":"1986","journal-title":"Arthritis Rheum"},{"key":"ref66","doi-asserted-by":"publisher","first-page":"1398","DOI":"10.1093\/rheumatology\/40.12.1398","volume":"40","author":"Fujii","year":"2001","journal-title":"Rheumatology"},{"key":"ref67","doi-asserted-by":"publisher","first-page":"1479","DOI":"10.1084\/jem.20050473","volume":"201","author":"Pascual","year":"2005","journal-title":"J Exp Med"},{"key":"ref68","doi-asserted-by":"publisher","DOI":"10.1155\/2012\/156890","volume":"2012","author":"Colafrancesco","year":"2012","journal-title":"Int J Inflam"},{"key":"ref69","first-page":"11","volume":"30","author":"Choi","year":"2003","journal-title":"J Rheumatol"},{"key":"ref70","first-page":"2189","volume":"31","author":"Chen","year":"2004","journal-title":"J Rheumatol"},{"key":"ref71","first-page":"1162","volume":"77","author":"Frediani","year":"2018","journal-title":"Ann Rheum Dis"},{"key":"ref72","doi-asserted-by":"publisher","first-page":"102793","DOI":"10.1016\/j.jaut.2022.102793","volume":"127","author":"Ma","year":"2022","journal-title":"J Autoimmun"},{"key":"ref73","doi-asserted-by":"publisher","first-page":"86","DOI":"10.1038\/emboj.2012.328","volume":"32","author":"Nystr\u00f6m","year":"2013","journal-title":"EMBO J"},{"key":"ref74","doi-asserted-by":"publisher","first-page":"34474","DOI":"10.1074\/jbc.M112.401406","volume":"287","author":"Gurung","year":"2012","journal-title":"J Biol Chem"},{"key":"ref75","doi-asserted-by":"publisher","first-page":"13038","DOI":"10.3390\/ijms222313038","volume":"22","author":"Kim","year":"2021","journal-title":"Int J Mol Sci"},{"key":"ref76","doi-asserted-by":"publisher","first-page":"528","DOI":"10.1038\/s41584-018-0058-9","volume":"14","author":"Austermann","year":"2018","journal-title":"Nat Rev Rheumatol"},{"key":"ref77","doi-asserted-by":"publisher","first-page":"236","DOI":"10.3390\/cells11020236","volume":"11","author":"Sprenkeler","year":"2022","journal-title":"Cells"},{"key":"ref78","doi-asserted-by":"publisher","first-page":"883","DOI":"10.1002\/art.24349","volume":"60","author":"Frosch","year":"2009","journal-title":"Arthritis Rheum"},{"key":"ref79","doi-asserted-by":"publisher","DOI":"10.1186\/s40348-018-0085-2","volume":"5","author":"Holzinger","year":"2018","journal-title":"Mol Cell Pediatr"},{"key":"ref80","doi-asserted-by":"publisher","first-page":"974","DOI":"10.1136\/annrheumdis-2011-200598","volume":"71","author":"Holzinger","year":"2012","journal-title":"Ann Rheum Dis"},{"key":"ref81","doi-asserted-by":"publisher","DOI":"10.1186\/s12969-020-0398-2","volume":"18","author":"Aljaberi","year":"2020","journal-title":"Pediatr Rheumatol Online J"},{"key":"ref82","doi-asserted-by":"publisher","first-page":"1399","DOI":"10.3899\/jrheum.120079","volume":"39","author":"Kim","year":"2012","journal-title":"J Rheumatol"},{"key":"ref83","doi-asserted-by":"publisher","first-page":"1342","DOI":"10.3390\/ijms17081342","volume":"17","author":"Kim","year":"2016","journal-title":"Int J Mol Sci"},{"key":"ref84","doi-asserted-by":"publisher","first-page":"3924","DOI":"10.1002\/art.24137","volume":"58","author":"Wittkowski","year":"2008","journal-title":"Arthritis Rheum"},{"key":"ref85","doi-asserted-by":"publisher","first-page":"2403","DOI":"10.3899\/jrheum.140651","volume":"41","author":"Bae","year":"2014","journal-title":"J Rheumatol"},{"key":"ref86","doi-asserted-by":"publisher","first-page":"842","DOI":"10.1136\/annrheumdis-2019-216699","volume":"79","author":"Hu","year":"2020","journal-title":"Ann Rheum Dis"},{"key":"ref87","doi-asserted-by":"publisher","first-page":"736","DOI":"10.1093\/rheumatology\/key414","volume":"58","author":"Ladhari","year":"2019","journal-title":"Rheumatology"},{"key":"ref88","doi-asserted-by":"publisher","first-page":"119","DOI":"10.3389\/fimmu.2019.00119","volume":"10","author":"Crayne","year":"2019","journal-title":"Front Immunol"},{"key":"ref89","first-page":"927","volume":"151","author":"Eloseily","year":"2018","journal-title":"Microbiome Rheum Dis Infect"},{"key":"ref90","doi-asserted-by":"publisher","first-page":"1","DOI":"10.3390\/jcm10061164","volume":"10","author":"Di Cola","year":"2021","journal-title":"J Clin Med"},{"key":"ref91","doi-asserted-by":"publisher","first-page":"2337","DOI":"10.1182\/blood.2020009499","volume":"137","author":"Chaturvedi","year":"2021","journal-title":"Blood"},{"key":"ref92","doi-asserted-by":"publisher","first-page":"4195","DOI":"10.1182\/blood-2021-146770","volume":"138","author":"Grom","year":"2021","journal-title":"Blood"},{"key":"ref93","doi-asserted-by":"publisher","first-page":"1811","DOI":"10.1056\/NEJMoa1911326","volume":"382","author":"Locatelli","year":"2020","journal-title":"N Engl J Med"},{"key":"ref94","doi-asserted-by":"publisher","first-page":"421","DOI":"10.1136\/adc.85.5.421","volume":"85","author":"Sawhney","year":"2001","journal-title":"Arch Dis Child"},{"key":"ref95","first-page":"459","volume":"63","author":"Moradinejad","year":"2011","journal-title":"Minerva Pediatr"},{"key":"ref96","doi-asserted-by":"publisher","first-page":"1686","DOI":"10.1093\/rheumatology\/ken342","volume":"47","author":"Fukaya","year":"2008","journal-title":"Rheumatology"},{"key":"ref97","doi-asserted-by":"publisher","first-page":"351","DOI":"10.1080\/1744666X.2018.1465821","volume":"14","author":"Mitrovic","year":"2018","journal-title":"Expert Rev Clin Immunol"},{"key":"ref98","first-page":"1133","volume":"34","author":"Behrens","year":"2007","journal-title":"J Rheumatol"},{"key":"ref99","doi-asserted-by":"publisher","first-page":"1645","DOI":"10.1093\/rheumatology\/keq133","volume":"49","author":"Shimizu","year":"2010","journal-title":"Rheumatology"},{"key":"ref100","doi-asserted-by":"publisher","first-page":"2421","DOI":"10.1093\/rheumatology\/keaa634","volume":"60","author":"Mizuta","year":"2021","journal-title":"Rheumatology"},{"key":"ref101","doi-asserted-by":"publisher","first-page":"1","DOI":"10.3389\/fimmu.2021.750114","volume":"12","author":"Shiga","year":"2021","journal-title":"Front Immunol"},{"key":"ref102","doi-asserted-by":"publisher","first-page":"1722","DOI":"10.1136\/annrheumdis-2019-216040","volume":"78","author":"Saper","year":"2019","journal-title":"Ann Rheum Dis"},{"key":"ref103","doi-asserted-by":"publisher","first-page":"1943","DOI":"10.1002\/art.41073","volume":"71","author":"Schulert","year":"2019","journal-title":"Arthritis Rheumatol"},{"key":"ref104","doi-asserted-by":"publisher","DOI":"10.1186\/s13075-020-02245-5","volume":"22","author":"Ruscitti","year":"2020","journal-title":"Arthritis Res Ther"},{"key":"ref105","doi-asserted-by":"publisher","first-page":"2255","DOI":"10.1056\/NEJMra2026131","volume":"383","author":"Fajgenbaum","year":"2020","journal-title":"The New England Journal of Medicine"},{"key":"ref106","doi-asserted-by":"publisher","first-page":"820","DOI":"10.1002\/acr2.11331","volume":"3","author":"Reiff","year":"2021","journal-title":"ACR Open Rheumatol"},{"key":"ref107","doi-asserted-by":"publisher","first-page":"279","DOI":"10.1016\/j.semarthrit.2010.12.006","volume":"41","author":"Colina","year":"2011","journal-title":"Semin Arthritis Rheum"},{"key":"ref108","doi-asserted-by":"publisher","first-page":"1015","DOI":"10.1007\/s10067-010-1516-1","volume":"29","author":"Kong","year":"2010","journal-title":"Clin Rheumatol"},{"key":"ref109","first-page":"373","volume":"26","author":"Fautrel","year":"1999","journal-title":"J Rheumatol"},{"key":"ref110","doi-asserted-by":"publisher","first-page":"33","DOI":"10.2147\/TCRM.S64951","volume":"11","author":"Jamilloux","year":"2015","journal-title":"Ther Clin Risk Manag"},{"key":"ref111","doi-asserted-by":"publisher","DOI":"10.3389\/fphar.2017.00369","volume":"8","author":"Colafrancesco","year":"2017","journal-title":"Front Pharmacol"},{"key":"ref112","doi-asserted-by":"publisher","first-page":"1659","DOI":"10.1002\/art.38398","volume":"66","author":"Ortiz-Sanju\u00e1n","year":"2014","journal-title":"Arthritis Rheumatol"},{"key":"ref113","doi-asserted-by":"publisher","first-page":"137","DOI":"10.1016\/j.semarthrit.2020.10.011","volume":"51","author":"Laskari","year":"2021","journal-title":"Semin Arthritis Rheum"},{"key":"ref114","doi-asserted-by":"publisher","first-page":"1090","DOI":"10.1136\/annrheumdis-2020-217155","volume":"79","author":"Kedor","year":"2020","journal-title":"Ann Rheum Dis"},{"key":"ref115","doi-asserted-by":"publisher","first-page":"840","DOI":"10.1136\/annrheumdis-2017-212608","volume":"77","author":"Gabay","year":"2018","journal-title":"Ann Rheum Dis"},{"key":"ref116","doi-asserted-by":"publisher","first-page":"1573","DOI":"10.4161\/cc.19978","volume":"11","author":"Moudry","year":"2012","journal-title":"Cell Cycle"},{"key":"ref117","doi-asserted-by":"publisher","first-page":"3682","DOI":"10.1182\/blood.2020010177","volume":"137","author":"Bourbon","year":"2021","journal-title":"Blood"},{"key":"ref118","doi-asserted-by":"publisher","first-page":"3676","DOI":"10.1182\/blood.2020010286","volume":"137","author":"Poulter","year":"2021","journal-title":"Blood"},{"key":"ref119","doi-asserted-by":"publisher","first-page":"3591","DOI":"10.1182\/blood.2021011455","volume":"137","author":"Grayson","year":"2021","journal-title":"Blood"},{"key":"ref120","doi-asserted-by":"publisher","first-page":"1648","DOI":"10.1007\/s10875-021-01070-y","volume":"41","author":"Grey","year":"2021","journal-title":"J Clin Immunol"},{"key":"ref121","doi-asserted-by":"publisher","first-page":"e117","DOI":"10.1093\/rheumatology\/keab866","volume":"61","author":"Cordts","year":"2021","journal-title":"Rheumatology"},{"key":"ref122","doi-asserted-by":"publisher","first-page":"665","DOI":"10.1002\/art.41992","volume":"74","author":"Muratore","year":"2022","journal-title":"Arthritis Rheumatol"},{"key":"ref123","doi-asserted-by":"publisher","first-page":"1886","DOI":"10.1002\/art.41743","volume":"73","author":"Ferrada","year":"2021","journal-title":"Arthritis Rheumatol"},{"key":"ref124","doi-asserted-by":"publisher","first-page":"58","DOI":"10.1097\/MOH.0b013e32834da9d2","volume":"19","author":"Lazarchick","year":"2012","journal-title":"Curr Opin Hematol"},{"key":"ref125","doi-asserted-by":"publisher","first-page":"886","DOI":"10.1038\/leu.2008.389","volume":"23","author":"Houwerzijl","year":"2009","journal-title":"Leukemia"},{"key":"ref126","doi-asserted-by":"publisher","first-page":"3685","DOI":"10.1182\/blood.2021010811","volume":"137","author":"Gurnari","year":"2021","journal-title":"Blood"},{"key":"ref127","doi-asserted-by":"publisher","first-page":"13","DOI":"10.1016\/j.leukres.2016.02.005","author":"Fraison","year":"2016","journal-title":"Leuk Res"},{"key":"ref128","doi-asserted-by":"publisher","first-page":"998","DOI":"10.1182\/bloodadvances.2021004749","volume":"6","author":"Diarra","year":"2022","journal-title":"Blood Adv"},{"key":"ref129","doi-asserted-by":"publisher","first-page":"247","DOI":"10.1053\/j.seminhematol.2021.10.003","volume":"58","author":"Oganesyan","year":"2021","journal-title":"Semin Hematol"},{"key":"ref130","doi-asserted-by":"publisher","first-page":"3616","DOI":"10.1182\/blood-2013-08-518886","volume":"122","author":"Papaemmanuil","year":"2013","journal-title":"Blood"},{"key":"ref131","doi-asserted-by":"publisher","first-page":"2391","DOI":"10.1182\/blood-2016-03-643544","volume":"127","author":"Arber","year":"2016","journal-title":"Blood"},{"key":"ref132","doi-asserted-by":"publisher","DOI":"10.1038\/s41408-021-00547-8","volume":"11","author":"Chakraborty","year":"2021","journal-title":"Blood Cancer J"},{"key":"ref133","doi-asserted-by":"publisher","DOI":"10.1084\/jem.20200560","volume":"218","author":"Higa","year":"2021","journal-title":"J Exp Med"},{"key":"ref134","doi-asserted-by":"publisher","DOI":"10.3389\/fimmu.2021.610019","volume":"12","author":"Watad","year":"2021","journal-title":"Front Immunol"},{"key":"ref135","doi-asserted-by":"publisher","first-page":"291","DOI":"10.1093\/rheumatology\/kev294","volume":"55","author":"Mekinian","year":"2015","journal-title":"Rheumatology"},{"key":"ref136","doi-asserted-by":"publisher","first-page":"123","DOI":"10.3904\/kjim.2014.29.1.123","volume":"29","author":"Kook","year":"2014","journal-title":"Korean J Intern Med"},{"key":"ref137","doi-asserted-by":"publisher","first-page":"216","DOI":"10.1016\/j.jbspin.2014.10.011","volume":"82","author":"Simonetta","year":"2015","journal-title":"J Bone Spine"},{"key":"ref138","doi-asserted-by":"publisher","first-page":"264","DOI":"10.1080\/08916934.2019.1680649","volume":"52","author":"Alix","year":"2019","journal-title":"Autoimmunity"},{"key":"ref139","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1186\/s13075-020-02318-5","volume":"22","author":"Darrieutort-Laffite","year":"2020","journal-title":"Arthritis Res Ther"},{"key":"ref140","doi-asserted-by":"publisher","first-page":"152024","DOI":"10.1016\/j.semarthrit.2022.152024","volume":"55","author":"Sutera","year":"2022","journal-title":"Semin Arthritis Rheum"},{"key":"ref141","doi-asserted-by":"publisher","DOI":"10.3389\/fimmu.2021.717388","volume":"12","author":"Hadjadj","year":"2021","journal-title":"Front Immunol"},{"key":"ref142","doi-asserted-by":"publisher","DOI":"10.1182\/blood.2022016642","author":"Heiblig","year":"2022","journal-title":"Blood"},{"key":"ref143","doi-asserted-by":"publisher","first-page":"969","DOI":"10.1111\/bjh.17893","volume":"196","author":"Comont","year":"2022","journal-title":"Br J Haematol"},{"key":"ref144","doi-asserted-by":"publisher","first-page":"1698","DOI":"10.1016\/j.jaci.2016.10.022","volume":"139","author":"Canna","year":"2017","journal-title":"J Allergy Clin Immunol"},{"key":"ref145","doi-asserted-by":"crossref","unstructured":"Booshehri LM, Hoffman HM. CAPS and NLRP3. J Clin Immunol. 2019;15;39(3):277\u201386.","DOI":"10.1007\/s10875-019-00638-z"},{"key":"ref146","doi-asserted-by":"crossref","unstructured":"Agostini L, Martinon F, Burns K, McDermott MF, Hawkins PN, Tschopp J. NALP3 forms an IL-1beta-processing inflammasome with increased activity in Muckle-Wells autoinflammatory disorder. 2004;20(3):319\u201325. doi: 10.1016\/s1074-7613(04)00046-9","DOI":"10.1016\/S1074-7613(04)00046-9"},{"key":"ref147","doi-asserted-by":"crossref","unstructured":"Kon\u00e9-Paut I, Galeotti C. Anakinra for cryopyrin-associated periodic syndrome. Expert Rev Clin Immunol. 2014;10(1):7\u201318.","DOI":"10.1586\/1744666X.2014.861325"},{"key":"ref148","doi-asserted-by":"crossref","unstructured":"Kieffer C, Cribier B, Lipsker D. Neutrophilic urticarial dermatosis: a variant of neutrophilic urticaria strongly associated with systemic disease. Report of 9 new cases and review of the literature. Medicine (Baltimore). 2009;88(1):23\u201331.","DOI":"10.1097\/MD.0b013e3181943f5e"},{"key":"ref149","doi-asserted-by":"crossref","unstructured":"Poulter JA, Savic S. Genetics of somatic auto-inflammatory disorders. Semin Hematol. 2021;58(4):212\u2013217.","DOI":"10.1053\/j.seminhematol.2021.10.001"},{"key":"ref150","doi-asserted-by":"crossref","unstructured":"Zhou Q, Aksentijevich I, Wood GM, Walts AD, Hoffmann P, Remmers EF, et al. Brief Report: Cryopyrin-Associated Periodic Syndrome Caused by a Myeloid-Restricted Somatic NLRP3 Mutation. Arthritis Rheumatol (Hoboken, NJ). 2015;67(9):2482\u20132486.","DOI":"10.1002\/art.39190"},{"key":"ref151","doi-asserted-by":"crossref","unstructured":"Stackowicz J, Gaudenzio N, Serhan N, Conde E, Godon O, Marichal T, et al. Neutrophil-specific gain-of-function mutations in Nlrp3 promote development of cryopyrin-associated periodic syndrome. J Exp Med. 2021 Sep 3;218(10).","DOI":"10.1084\/jem.20201466"}],"container-title":["Journal of Inflammation Research"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.dovepress.com\/getfile.php?fileID=84523","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/www.dovepress.com\/getfile.php?fileID=84523","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,10,9]],"date-time":"2022-10-09T15:45:33Z","timestamp":1665330333000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.dovepress.com\/improving-diagnosis-and-clinical-management-of-acquired-systemic-autoi-peer-reviewed-fulltext-article-JIR"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,10]]},"references-count":151,"URL":"https:\/\/doi.org\/10.2147\/jir.s343261","relation":{},"ISSN":["1178-7031"],"issn-type":[{"value":"1178-7031","type":"electronic"}],"subject":[],"published":{"date-parts":[[2022,10]]}}}