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Haematologica doi: 10. 3324\/haematol. 2012. 073031 (in press)."},{"key":"6","doi-asserted-by":"crossref","unstructured":"6. Watanabe O, Maruyama I, Arimura K, et al. Overproduction of vascular endothelial growth factor\/vascular permeability factor is causative in Crow-Fukase (POEMS) syndrome. Muscle Nerve 21: 1390-1397, 1998.","DOI":"10.1002\/(SICI)1097-4598(199811)21:11<1390::AID-MUS5>3.0.CO;2-4"},{"key":"7","doi-asserted-by":"crossref","unstructured":"7. Nobile-Orazio E, Terenghi F, Giannotta C, Gallia F, Nozza A. Serum VEGF levels in POEMS syndrome and in immune-mediated neuropathies. Neurology 72: 1024-1026, 2009.","DOI":"10.1212\/01.wnl.0000344569.13496.ff"},{"key":"8","doi-asserted-by":"crossref","unstructured":"8. Niimi H, Arimura K, Jonosono M, et al. VEGF is causative for pulmonary hypertension in a patient with Crow-Fukase (POEMS) syndrome. Intern Med 39: 1101-1104, 2000.","DOI":"10.2169\/internalmedicine.39.1101"},{"key":"9","doi-asserted-by":"crossref","unstructured":"9. D'Souza A, Hayman SR, Buadi F, et al. The utility of plasma vascular endothelial growth factor levels in the diagnosis and follow-up of patients with POEMS syndrome. Blood 118: 4663-4665, 2011.","DOI":"10.1182\/blood-2011-06-362392"},{"key":"10","unstructured":"10. Paulus WJ, Tsch&ouml;pe C, Sanderson JE, et al. How to diagnose diastolic heart failure: a consensus statement on the diagnosis of heart failure with normal left ventricular ejection fraction by heart failure and echocardiography associations of European society of cardiology. Eur Heart J 28: 2539-2550, 2007."},{"key":"11","unstructured":"11. Gali&egrave; N, Hoeper MM, Humbert M, et al. Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Heart J 30: 2493-2537, 2009."},{"key":"12","doi-asserted-by":"crossref","unstructured":"12. Okura H, Gohma I, Hatta K, Imanaka T. Thiamine difiency and pulmonary hypertension in Crow-Fukase syndrome. Intern Med 34: 674-675, 1995.","DOI":"10.2169\/internalmedicine.34.674"},{"key":"13","doi-asserted-by":"crossref","unstructured":"13. Araki T, Konno T, Soma R, et al. Crow-Fukase syndrome associated with high output heart failure. Intern Med 41: 638-641, 2002.","DOI":"10.2169\/internalmedicine.41.638"},{"key":"14","unstructured":"14. Shiraki T, Satoh S, Sugiyama H, et al. Highly concentrated vascular endothelial growth factor in Crow-Fukase syndrome with high output heart failure: a case report. J Cardiol 45: 75-80, 2005."},{"key":"15","doi-asserted-by":"crossref","unstructured":"15. Rached S, Athanazio RA, Dias SA Jr, Jardim C, Souza R. Systemic corticosteroids as first-line treatment in pulmonary hypertension associated with the POEMS syndrome. J Bras Pneumol 35: 804-808, 2009.","DOI":"10.1590\/S1806-37132009000800013"},{"key":"16","doi-asserted-by":"crossref","unstructured":"16. Shimomura Y, Hara M, Mizote I, et al. Sildenafil and steroid therapy effectively improved POEMS syndrome-associated pulmonary arterial hypertension. Int J Hematol 92: 774-776, 2010.","DOI":"10.1007\/s12185-010-0722-6"},{"key":"17","doi-asserted-by":"crossref","unstructured":"17. Jouve P, Humbert M, Chauveheid MP, Ja&iuml;s X, Papo T. POEMS syndrome-related pulmonary hypertension is steroid-responsive. Respir Med 101: 353-355, 2007.","DOI":"10.1016\/j.rmed.2006.04.026"},{"key":"18","doi-asserted-by":"crossref","unstructured":"18. Iwasaki H, Ogawa K, Yoshida H, et al. Crow-Fukase syndrome associated with pulmonary hypertension. Intern Med 32: 556-560, 1993.","DOI":"10.2169\/internalmedicine.32.556"},{"key":"19","doi-asserted-by":"crossref","unstructured":"19. Shimizu N, Goya M, Akimoto H, et al. Cardiomyopathy in a case of Crow-Fukase syndrome. Jpn Heart J 38: 877-880, 1997.","DOI":"10.1536\/ihj.38.877"},{"key":"20","doi-asserted-by":"crossref","unstructured":"20. Barst RJ, Gibbs JS, Ghofrani HA, et al. Updated evidence-based treatment algorithm in pulmonary arterial hypertension. J Am Coll Cardiol 54: S78-S84, 2009.","DOI":"10.1016\/j.jacc.2009.04.017"},{"key":"21","doi-asserted-by":"crossref","unstructured":"21. Li J, Zhang W, Jiao L, et al. Combination of melphalan and dexamethasone for patients with newly diagnosed POEMS syndrome. Blood 117: 6445-6449, 2011.","DOI":"10.1182\/blood-2010-12-328112"},{"key":"22","doi-asserted-by":"crossref","unstructured":"22. Leuchte HH, Holzapfel M, Baumgartner RA, Neurohr C, Vogeser M, Behr J. Characterization of brain natriuretic peptie in long-term follow-up of pulmonary arterial hypertension. Chest 128: 2368-2374, 2005.","DOI":"10.1378\/chest.128.4.2368"},{"key":"23","doi-asserted-by":"crossref","unstructured":"23. Byrd RP Jr, Roy TM, Bentz W, Mehta JB. Plasmacytoma as a cause of obstructive sleep apnea. Chest 109: 1657-1659, 1996.","DOI":"10.1378\/chest.109.6.1657"},{"key":"24","doi-asserted-by":"crossref","unstructured":"24. 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