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Molecular genetic survey of five Japanese families with high-molecular-weight kininogen deficiency. Blood 75: 1296-1304, 1990.","DOI":"10.1182\/blood.V75.6.1296.1296"},{"key":"9","unstructured":"9. Krijanovski Y, Proulle V, Mahdi F, et al. Characterization of molecular defects of Fitzgerald trait and another novel high-molecular-weight kininogen-deficient patient: insights into structural requirements for kininogen expression. Blood 101: 4430-4436, 2003."},{"key":"10","unstructured":"10. Shigekiyo T, Miyagi J, Shirakami A, et al. Isolated high-molecular-weight kininogen deficiency: a novel frameshift mutation in exon 10. Blood 109: 5062-5063, 2007."},{"key":"11","unstructured":"11. Siegerink B, Rosendaal FR, Algra A. High molecular weight kininogen and the risk of myocardial infarction and ischemic stroke in young women: the ratio case-control study. J Thromb Haemost 10: 2409-2412, 2012."},{"key":"12","doi-asserted-by":"crossref","unstructured":"12. Chavakis T, Boeckel N, Santoso S, et al. Inhibition of platelet adhesion and aggregation by a defined region (Gly-486-Lys-502) of high molecular weight kininogen. J Biol Chem 277: 23157-23164, 2002.","DOI":"10.1074\/jbc.M202529200"},{"key":"13","doi-asserted-by":"crossref","unstructured":"13. Puri RN, Zhou F, Hu CJ, et al. High molecular weight kininogen inhibits thrombin-induced platelet aggregation and cleavage of aggregin by inhibiting binding of thrombin to platelets. Blood 77: 500-507, 1991.","DOI":"10.1182\/blood.V77.3.500.500"},{"key":"14","doi-asserted-by":"crossref","unstructured":"14. Ratnoff OD. The demise of John Hageman. N Engl J Med 279: 760-761, 1968.","DOI":"10.1056\/NEJM196810032791407"},{"key":"15","doi-asserted-by":"crossref","unstructured":"15. Cheung PP, Kunapuli SP, Scott CF, et al. Genetic basis of total kininogen deficiency in Williams' trait. 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