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Chen X, Prosser R, Simonetti S, Sadlock J, Jagiello G, Schon EA. Rearranged mitochondrial genomes are present in human oocytes. Am J Hum Genet 57: 239-247, 1995."},{"key":"9","unstructured":"9. Van Goethem G, Martin JJ, Van Broeckhoven C. Progressive external ophthalmoplegia characterized by multiple deletions of mitochondrial DNA: unraveling the pathogenesis of human mitochondrial DNA instability and the initiation of a genetic classification. Neuromolecular Med 3: 129-146, 2003."},{"key":"10","doi-asserted-by":"crossref","unstructured":"10. Bose H, Lingappa VR, Miller WL. Rapid regulation of steroidogenesis by mitochondrial protein import. Nature 417: 87-91, 2002.","DOI":"10.1038\/417087a"},{"key":"11","doi-asserted-by":"crossref","unstructured":"11. Melberg A, Arnell H, Dahl N, et al. Anticipation of autosomal dominant progressive external ophthalmoplegia with hypogonadism. 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