{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,24]],"date-time":"2026-03-24T09:08:50Z","timestamp":1774343330115,"version":"3.50.1"},"reference-count":13,"publisher":"Japanese Society of Internal Medicine","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Intern. Med."],"published-print":{"date-parts":[[2015]]},"DOI":"10.2169\/internalmedicine.54.3760","type":"journal-article","created":{"date-parts":[[2015,1,14]],"date-time":"2015-01-14T22:10:09Z","timestamp":1421273409000},"page":"219-221","source":"Crossref","is-referenced-by-count":10,"title":["Successful Immune Moderation Treatment for Progressive Encephalomyelitis with Rigidity and Myoclonus"],"prefix":"10.2169","volume":"54","author":[{"given":"Shinichi","family":"Ueno","sequence":"first","affiliation":[{"name":"Department of Neurology, Juntendo University Urayasu Hospital, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nobukazu","family":"Miyamoto","sequence":"additional","affiliation":[{"name":"Department of Neurology, Juntendo University Urayasu Hospital, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hideki","family":"Shimura","sequence":"additional","affiliation":[{"name":"Department of Neurology, Juntendo University Urayasu Hospital, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yuji","family":"Ueno","sequence":"additional","affiliation":[{"name":"Department of Neurology, Juntendo University Urayasu Hospital, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Masao","family":"Watanabe","sequence":"additional","affiliation":[{"name":"Department of Neurology, Juntendo University Urayasu Hospital, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Akito","family":"Hayashi","sequence":"additional","affiliation":[{"name":"Department of Rehabilitation, Juntendo University Urayasu Hospital, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nobutaka","family":"Hattori","sequence":"additional","affiliation":[{"name":"Department of Neurology, Juntendo University School of Medicine, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takao","family":"Urabe","sequence":"additional","affiliation":[{"name":"Department of Neurology, Juntendo University Urayasu Hospital, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"962","reference":[{"key":"1","doi-asserted-by":"crossref","unstructured":"1. Meinck HM, Thompson PD. Stiff man syndrome and related conditions. Mov Disord 17: 853-866, 2002.","DOI":"10.1002\/mds.10279"},{"key":"2","doi-asserted-by":"crossref","unstructured":"2. Barker RA, Revesz T, Thom M, Marsden CD, Brown P. Review of 23 patients affected by the stiff man syndrome: clinical subdivision into stiff trunk (man) syndrome, stiff limb syndrome, and progressive encephalomyelitis with rigidity. J Neurol Neurosurg Psychiatry 65: 633-640, 1998.","DOI":"10.1136\/jnnp.65.5.633"},{"key":"3","unstructured":"3. Moersch FP, Woltman HW. Progressive fluctuating muscular rigidity and spasm (\"stiff-man\" syndrome); report of a case and some observations in 13 other cases. Proc Staff Meet Mayo Clin 31: 421-427, 1956."},{"key":"4","doi-asserted-by":"crossref","unstructured":"4. Shugaiv E, Leite MI, Sehitoglu E, et al. Progressive encephalomyelitis with rigidity and myoclonus: a syndrome with diverse clinical features and antibody responses. Eur Neurol 69: 257-262, 2013.","DOI":"10.1159\/000342237"},{"key":"5","doi-asserted-by":"crossref","unstructured":"5. Mas N, Saiz A, Leite MI, et al. Antiglycine-receptor encephalomyelitis with rigidity. J Neurol Neurosurg Psychiatry 82: 1399-1401, 2011.","DOI":"10.1136\/jnnp.2010.229104"},{"key":"6","doi-asserted-by":"crossref","unstructured":"6. McKeon A, Robinson MT, McEvoy KM, Matsumoto JY, Lennon VA, Ahlskog JE, Pittock SJ. Stiff-man syndrome and variants: clinical course, treatments, and outcomes. Arch Neurol 69: 230-238, 2012.","DOI":"10.1001\/archneurol.2011.991"},{"key":"7","doi-asserted-by":"crossref","unstructured":"7. Turner MR, Irani SR, Leite MI, Nithi K, Vincent A, Ansorge O. Progressive encephalomyelitis with rigidity and myoclonus: glycine and NMDA receptor antibodies. Neurology 77: 439-443, 2011.","DOI":"10.1212\/WNL.0b013e318227b176"},{"key":"8","doi-asserted-by":"crossref","unstructured":"8. Hutchinson M, Waters P, McHugh J, et al. Progressive encephalomyelitis, rigidity, and myoclonus: a novel glycine receptor antibody. Neurology 71: 1291-1292, 2008.","DOI":"10.1212\/01.wnl.0000327606.50322.f0"},{"key":"9","doi-asserted-by":"crossref","unstructured":"9. Carvajal-Gonzalez A, Leite MI, Waters P, et al. Glycine receptor antibodies in PERM and related syndromes: characteristics, clinical features and outcomes. Brain 137: 2178-2192, 2014.","DOI":"10.1093\/brain\/awu142"},{"key":"10","doi-asserted-by":"crossref","unstructured":"10. Ruegg SJ, Steck AJ, Fuhr P. Levetiracetam improves paroxysmal symptoms in a patient with stiff-person syndrome. Neurology 62: 338, 2004.","DOI":"10.1212\/01.WNL.0000103442.27580.5B"},{"key":"11","doi-asserted-by":"crossref","unstructured":"11. Amato AA, Cornman EW, Kissel JT. Treatment of stiff-man syndrome with intravenous immunoglobulin. Neurology 44: 1652-1654, 1994.","DOI":"10.1212\/WNL.44.9.1652"},{"key":"12","doi-asserted-by":"crossref","unstructured":"12. Fogan L. Progressive encephalomyelitis with rigidity responsive to plasmapheresis and immunosuppression. Ann Neurol 40: 451-453, 1996.","DOI":"10.1002\/ana.410400315"},{"key":"13","doi-asserted-by":"crossref","unstructured":"13. Dalakas MC, Fujii M, Li M, Lutfi B, Kyhos J, McElroy B. High-dose intravenous immune globulin for stiff-person syndrome. N Engl J Med 345: 1870-1876, 2001.","DOI":"10.1056\/NEJMoa01167"}],"container-title":["Internal Medicine"],"original-title":[],"language":"en","deposited":{"date-parts":[[2017,6,23]],"date-time":"2017-06-23T03:42:26Z","timestamp":1498189346000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.jstage.jst.go.jp\/article\/internalmedicine\/54\/2\/54_54.3760\/_article"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015]]},"references-count":13,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2015]]}},"URL":"https:\/\/doi.org\/10.2169\/internalmedicine.54.3760","relation":{},"ISSN":["0918-2918","1349-7235"],"issn-type":[{"value":"0918-2918","type":"print"},{"value":"1349-7235","type":"electronic"}],"subject":[],"published":{"date-parts":[[2015]]}}}