{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,2]],"date-time":"2026-10-02T17:44:01Z","timestamp":1790963041859,"version":"4.1.0"},"reference-count":17,"publisher":"Japanese Society of Internal Medicine","issue":"5","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Intern. Med."],"published-print":{"date-parts":[[2016]]},"DOI":"10.2169\/internalmedicine.55.5047","type":"journal-article","created":{"date-parts":[[2016,2,29]],"date-time":"2016-02-29T22:07:54Z","timestamp":1456783674000},"page":"497-501","source":"Crossref","is-referenced-by-count":32,"title":["A Patient with Idiopathic Pleuroparenchymal Fibroelastosis Showing a Sustained Pulmonary Function due to Treatment with Pirfenidone"],"prefix":"10.2169","volume":"55","author":[{"given":"Seidai","family":"Sato","sequence":"first","affiliation":[{"name":"Department of Respiratory Medicine & Rheumatology, Institute of Biomedical Sciences, Tokushima University Graduate School, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Masaki","family":"Hanibuchi","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine & Rheumatology, Institute of Biomedical Sciences, Tokushima University Graduate School, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mikiko","family":"Takahashi","sequence":"additional","affiliation":[{"name":"Department of Analytic Human Pathology, Nippon Medical School, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yuh","family":"Fukuda","sequence":"additional","affiliation":[{"name":"Department of Analytic Human Pathology, Nippon Medical School, Japan"},{"name":"Division of Diagnostic Pathology, Itabashi Chuo Medical Center, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shun","family":"Morizumi","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine & Rheumatology, Institute of Biomedical Sciences, Tokushima University Graduate School, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yuko","family":"Toyoda","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine & Rheumatology, Institute of Biomedical Sciences, Tokushima University Graduate School, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hisatsugu","family":"Goto","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine & Rheumatology, Institute of Biomedical Sciences, Tokushima University Graduate School, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yasuhiko","family":"Nishioka","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine & Rheumatology, Institute of Biomedical Sciences, Tokushima University Graduate School, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"962","reference":[{"key":"1","doi-asserted-by":"crossref","unstructured":"1. Frankel SK, Cool CD, Lynch DA, Brown KK. Idiopathic pleuroparenchymal fibroelastosis: description of a novel clinicopathologic entity. Chest 126: 2007-2013, 2004.","DOI":"10.1378\/chest.126.6.2007"},{"key":"2","unstructured":"2. Nei T, Kawamoto M, Satoh E, et al. A case of suspected idiopathic pulmonary upper lobe fibrosis (Amitani disease) with acute exacerbation. Nihon Kokyuki Gakkai Zasshi 47: 116-121, 2009 (in Japanese, Abstract in English)."},{"key":"3","unstructured":"3. Morimoto A, Mochizuki Y, Nakahara Y, Kawamura T, Sakaki S, Kobashi Y. A case of idiopathic pulmonary upper lobe fibrosis. Nihon Kokyuki Gakkai Zasshi 48: 944-949, 2010 (in Japanese, Abstract in English)."},{"key":"4","unstructured":"4. Amitani R, Niimi A, Kuze F. Idiopathic pulmonary upper lobe fibrosis. Kokyu (Journal of Respiration Research Foundation) 11: 693-699, 1992 (in Japanese)."},{"key":"5","doi-asserted-by":"crossref","unstructured":"5. Kusagaya H, Nakamura Y, Kono M, et al. Idiopathic pleuroparenchymal fibroelastosis: consideration of a clinicopathological entity in a series of Japanese patients. BMC Pulm Med 12: 72, 2012.","DOI":"10.1186\/1471-2466-12-72"},{"key":"6","doi-asserted-by":"crossref","unstructured":"6. Watanabe K, Nagata N, Kitasato Y, et al. Rapid decrease in forced vital capacity in patients with idiopathic pulmonary upper lobe fibrosis. Respir Investig 50: 88-97, 2012.","DOI":"10.1016\/j.resinv.2012.06.003"},{"key":"7","doi-asserted-by":"crossref","unstructured":"7. Piciucchi S, Tomassetti S, Casoni G, et al. High resolution CT and histological findings in idiopathic pleuroparenchymal fibroelastosis: features and differential diagnosis. Respir Res 12: 111, 2011.","DOI":"10.1186\/1465-9921-12-111"},{"key":"8","doi-asserted-by":"crossref","unstructured":"8. Travis WD, Costabel U, Hansell DM, et al; ATS\/ERS Committee on Idiopathic Interstitial Pneumonias. An official American Thoracic Society\/European Respiratory Society statement: update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med 188: 733-748, 2013.","DOI":"10.1164\/rccm.201308-1483ST"},{"key":"9","doi-asserted-by":"crossref","unstructured":"9. Reddy TL, Tominaga M, Hansell DM, et al. Pleuroparenchymal fibroelastosis: a spectrum of histopathological and imaging phenotypes. Eur Respir J 40: 377-385, 2012.","DOI":"10.1183\/09031936.00165111"},{"key":"10","unstructured":"10. Kobayashi Y, Sakurai M, Kushiya M, et al. Idiopathic pulmonary fibrosis of the upper lobe: a case report. Nihon Kokyuki Gakkai Zasshi 37: 812-816, 1999 (in Japanese, Abstract in English)."},{"key":"11","doi-asserted-by":"crossref","unstructured":"11. Harada T, Yoshida Y, Kitasato Y, et al. The thoracic cage becomes flattened in the progression of pleuroparenchymal fibroelastosis. Eur Respir Rev 23: 263-266, 2014.","DOI":"10.1183\/09059180.00006713"},{"key":"12","doi-asserted-by":"crossref","unstructured":"12. Sato S, Hanibuchi M, Fukuya A, et al. Idiopathic pleuroparenchymal fibroelastosis is characterized by an elevated serum level of surfactant protein-D, but not Krebs von den Lungen-6. Lung 192: 711-717, 2014.","DOI":"10.1007\/s00408-014-9599-0"},{"key":"13","doi-asserted-by":"crossref","unstructured":"13. King TE Jr, Bradford WZ, Castro-Bernardini S, et al; ASCEND Study Group. A phase 3 trial of pirfenidone in patients with idiopathic pulmonary fibrosis. N Engl J Med 370: 2083-2092, 2014.","DOI":"10.1056\/NEJMoa1402582"},{"key":"14","unstructured":"14. U.S. Food and Drug Administration. FDA approves Esbriet to treat idiopathic pulmonary fibrosis. [Internet]. [cited 2014 Oct 15]. Available from: http:\/\/www.fda.gov\/NewsEvents\/Newsroom\/PressAnnouncements\/ucm418991.htm"},{"key":"15","doi-asserted-by":"crossref","unstructured":"15. Dosanjh A. Pirfenidone: anti-fibrotic agent with a potential therapeutic role in the management of transplantation patients. Eur J Pharmacol 536: 219-222, 2006.","DOI":"10.1016\/j.ejphar.2006.03.007"},{"key":"16","doi-asserted-by":"crossref","unstructured":"16. Oda T, Ogura T, Kitamura H, et al. Distinct characteristics of pleuroparenchymal fibroelastosis with usual interstitial pneumonia compared with idiopathic pulmonary fibrosis. Chest 146: 1248-1255, 2014.","DOI":"10.1378\/chest.13-2866"},{"key":"17","doi-asserted-by":"crossref","unstructured":"17. Enomoto N, Kusagaya H, Oyama Y, et al. Quantitative analysis of lung elastic fibers in idiopathic pleuroparenchymal fibroelastosis (IPPFE): comparison of clinical, radiological, and pathological findings with those of idiopathic pulmonary fibrosis (IPF). BMC Pulm Med 14: 91, 2014.","DOI":"10.1186\/1471-2466-14-91"}],"container-title":["Internal Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.jstage.jst.go.jp\/article\/internalmedicine\/55\/5\/55_55.5047\/_pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2017,6,24]],"date-time":"2017-06-24T07:15:13Z","timestamp":1498288513000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.jstage.jst.go.jp\/article\/internalmedicine\/55\/5\/55_55.5047\/_article"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016]]},"references-count":17,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2016]]}},"URL":"https:\/\/doi.org\/10.2169\/internalmedicine.55.5047","relation":{},"ISSN":["0918-2918","1349-7235"],"issn-type":[{"value":"0918-2918","type":"print"},{"value":"1349-7235","type":"electronic"}],"subject":[],"published":{"date-parts":[[2016]]}}}