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Macrophage activation syndrome-associated adult onset Still disease treatment: a scoping review of case reports and case series. Proc (Bayl Univ Med Cent) 38: 499-511, 2025.","DOI":"10.1080\/08998280.2025.2482315"},{"key":"5","doi-asserted-by":"crossref","unstructured":"5. Chen Y, Hu Z, Cai S, Shen G, Zhong J, Dong L. Efficacy of plasma exchange on top of standard immunosuppressive therapy in adult autoimmune inflammatory rheumatic diseases-associated macrophage activation syndrome, a single center real-world analysis. Semin Arthritis Rheum 55: 152043, 2022.","DOI":"10.1016\/j.semarthrit.2022.152043"},{"key":"6","unstructured":"6. Yamaguchi M, Ohta A, Tsunematsu T, et al. Preliminary criteria for classification of adult Still&apos;s disease. J Rheumatol 19: 424-430, 1992."},{"key":"7","unstructured":"7. 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Clinical characteristics of macrophage activation syndrome in adult-onset Still&apos;s disease. Clin Exp Rheumatol 39 (Suppl 132): 59-66, 2021.","DOI":"10.55563\/clinexprheumatol\/lp2u7g"},{"key":"11","doi-asserted-by":"crossref","unstructured":"11. Tsuboi H, Segawa S, Yagishita M, et al. Activation mechanisms of monocytes\/macrophages in adult-onset Still disease. Front Immunol 13: 953730, 2022.","DOI":"10.3389\/fimmu.2022.953730"},{"key":"12","doi-asserted-by":"crossref","unstructured":"12. Kim JW, Ahn MH, Jung JY, Suh CH, Kim HA. An update on the pathogenic role of neutrophils in systemic juvenile idiopathic arthritis and adult-onset Still&apos;s disease. Int J Mol Sci 22: 13038, 2021.","DOI":"10.3390\/ijms222313038"},{"key":"13","doi-asserted-by":"crossref","unstructured":"13. Iwata N, Nishimura K, Hara R, et al. Long-term efficacy and safety of canakinumab in the treatment of systemic juvenile idiopathic arthritis in Japanese patients: results from an open-label Phase III study. 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