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Ehlers-Danlos National Foundation (USA) and Ehlers-Danlos Support Group (UK). <i>Am J Med Genet<\/i> 77: 31-37, 1998","DOI":"10.1002\/(SICI)1096-8628(19980428)77:1<31::AID-AJMG8>3.3.CO;2-P"},{"key":"5","doi-asserted-by":"crossref","unstructured":"5) Pepin M, Schwarze U, Superti-Furga A, Byers PH: Clinical and genetic features of Ehlers-Danlos syndrome type IV, the vascular type. <i>N Engl J Med<\/i> 342: 673-680, 2000","DOI":"10.1056\/NEJM200003093421001"},{"key":"6","doi-asserted-by":"crossref","unstructured":"6) Schievink WI, Limburg M, Oorthuys JW, Fleury P, Pope FM: Cerebrovascular disease in Ehlers-Danlos syndrome type IV. <i>Stroke<\/i> 21: 626-632, 1990","DOI":"10.1161\/01.STR.21.4.626"},{"key":"7","unstructured":"7) Freeman RK, Swegle J, Sise MJ: The surgical complications of Ehlers-Danlos syndrome. <i>Am Surg<\/i> 62: 869-873, 1996"},{"key":"8","unstructured":"8) Horowitz MB, Purdy PD, Valentine RJ, Morrill K: Remote vascular catastrophes after neurovascular interventional 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<i>Neuroradiology<\/i> 47: 300-304, 2005","DOI":"10.1007\/s00234-005-1378-4"},{"key":"12","doi-asserted-by":"crossref","unstructured":"12) Hollands JK, Santarius T, Kirkpatrick PJ, Higgins JN: Treatment of a direct carotid-cavernous fistula in a patient with type IV Ehlers-Danlos syndrome: a novel approach. <i>Neuroradiology<\/i> 48: 491-494, 2006","DOI":"10.1007\/s00234-006-0084-1"},{"key":"13","doi-asserted-by":"crossref","unstructured":"13) Van Overmeire O, De Keukeleire K, Van Langenhove P, Defreyne L: Carotid-cavernous fistula in Ehlers-Danlos syndrome by pure transvenous approach. <i>Interv Neuroradiol<\/i> 12: 45-51, 2006","DOI":"10.1177\/159101990601200109"},{"key":"14","doi-asserted-by":"crossref","unstructured":"14) Usinskiene J, Mazighi M, Bisdorff A, Houdart E: Fatal peritoneal bleeding following embolization of a carotid-cavernous fistula in Ehlers-Danlos syndrome type IV. <i>Cardiovasc Interv Radiol<\/i> 29: 1104-1106, 2006","DOI":"10.1007\/s00270-005-0331-6"},{"key":"15","doi-asserted-by":"crossref","unstructured":"15) Mammen S, Keshava SN, Danda S, Raju R, Chacko AG: Endovascular management of carotid-cavernous fistula in Ehlers-Danlos syndrome Type IV. <i>Neurol India<\/i> 60: 119-121, 2012","DOI":"10.4103\/0028-3886.93616"},{"key":"16","doi-asserted-by":"crossref","unstructured":"16) Wang Q, Chen G: Endovascular treatment of bilateral multiple carotid-cavernous fistulas in a patient with Ehlers-Danlos syndrome. <i>J Neurol Surg A Cent Eur Neurosurg<\/i> 74 Suppl 1: e41-e44, 2013","DOI":"10.1055\/s-0032-1322595"},{"key":"17","doi-asserted-by":"crossref","unstructured":"17) Asai K, Toyota S, Hayakawa K, et al.: [Carotid cavernous fistula in a patient with Ehlers-Danlos syndrome type IV: a case report]. <i>J Neuroendovasc Ther<\/i> 7: 94-100, 2013 (Japanese)","DOI":"10.5797\/jnet.7.94"},{"key":"18","doi-asserted-by":"crossref","unstructured":"18) Kim JG, Cho WS, Kang HS, Kim JE: Spontaneous carotid-cavernous fistula in the type IV Ehlers-Danlos syndrome. <i>J Korean Neurosurg Soc<\/i> 55: 92-95, 2014","DOI":"10.3340\/jkns.2014.55.2.92"},{"key":"19","doi-asserted-by":"crossref","unstructured":"19) Tanaka T, Hayakawa M, Sadato A, et al.: Transvenous embolization for carotid-cavernous fistula in a patient with vascular type of Ehlers-Danlos syndrome--direct superior ophthalmic vein approach: case report. <i>Neurol Med Chir (Tokyo)<\/i> 54: 155-160, 2014","DOI":"10.2176\/nmc.cr.2013-0007"},{"key":"20","doi-asserted-by":"crossref","unstructured":"20) Nakagawa I, Park HS, Wada T, et al.: A novel approach to the treatment of a direct carotid-cavernous fistula in a patient with Ehlers-Danlos syndrome type IV. <i>BMJ Case Rep<\/i> 2014: bcr2014011414, 2014","DOI":"10.1136\/bcr-2014-011414"},{"key":"21","doi-asserted-by":"crossref","unstructured":"21) Kojima A, Saga I, Tomio R, Kosho T, Hatamochi A: Aggressive change of a carotid-cavernous fistula in a patient with Ehlers-Danlos syndrome type IV. <i>Interv Neuroradiol<\/i> 21: 341-345, 2015","DOI":"10.1177\/1591019915582380"},{"key":"22","unstructured":"22) Sato S, Niimi Y, Moteki Y, Inoue T, Shima S, Okada Y: [Transvenous embolization for carotid cavernous fistula in a patient with vascular Ehlers-Danlos syndrome: a case report]. <i>NKC<\/i> 3: 14-20, 2018 (Japanese)"},{"key":"23","doi-asserted-by":"crossref","unstructured":"23) Masson-Roy J, Savard M, Mackey A: Carotid cavernous fistula in a patient with type IV Ehlers-Danlos syndrome. <i>Can J Neurol Sci<\/i> 44: 427-428, 2017","DOI":"10.1017\/cjn.2016.456"},{"key":"24","doi-asserted-by":"crossref","unstructured":"24) Ito Y, Satow T, Matsubara H, Kataoka H, Takahashi JC: Selective shunt occlusion of direct carotid-cavernous fistula with vascular Ehlers-Danlos syndrome by multidevice technique: a case report and technical note. <i>World Neurosurg<\/i> 122: 123-128, 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