{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,14]],"date-time":"2026-09-14T20:20:34Z","timestamp":1789417234596,"version":"build-2803163510"},"reference-count":15,"publisher":"The Angle Orthodontist (EH Angle Education & Research Foundation)","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2009,1,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Cleidocranial dysostosis is a rare congenital skeletal disorder, associated with clavicular hypoplasia or aplasia, delayed closure of cranial fontanels, brachycephalic skull, delayed exfoliation of primary dentition, eruption of permanent teeth, and multiple supernumerary and morphologic abnormalities of the maxilla and mandible. The disorder is caused by mutation in the CBFA1 gene, on the short arm of chromosome 6p21. The prevalence of cleidocranial dysostosis is estimated one per million, without sex or ethnic group predilection. The purpose of this paper is to describe the orthodontic treatment in a patient with cleidocranial dysostosis. Therapy may include removal of supernumerary teeth, surgical exposure of impacted teeth, and orthodontic treatment.<\/jats:p>","DOI":"10.2319\/111307-393.1","type":"journal-article","created":{"date-parts":[[2008,8,1]],"date-time":"2008-08-01T18:01:59Z","timestamp":1217613719000},"page":"178-185","source":"Crossref","is-referenced-by-count":44,"title":["Orthodontic Treatment in a Patient with Cleidocranial Dysostosis"],"prefix":"10.2319","volume":"79","author":[{"given":"Giampietro","family":"Farronato","sequence":"first","affiliation":[{"name":"a\u2009Full Professor, Department of Orthodontics, Dental and Stomatologic Clinic, ICP, School of Dentistry, University of Milan, Milan, Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cinzia","family":"Maspero","sequence":"first","affiliation":[{"name":"b\u2009Assistant Professor, Department of Orthodontics, Dental and Stomatologic Clinic, ICP, School of Dentistry, University of Milan, Milan, Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Davide","family":"Farronato","sequence":"first","affiliation":[{"name":"c\u2009Researcher, Department of Oral Surgery, Dental and Stomatologic Clinic, ICP, School of Dentistry, University of Milan, Milan, Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Silvia","family":"Giovent\u00f9","sequence":"first","affiliation":[{"name":"d\u2009Resident, Department of Orthodontics, Dental and Stomatologic Clinic, ICP, School of Dentistry, University of Milan, Milan, Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1164","reference":[{"key":"2020042118074327400_i0003-3219-079-01-0178-b1","first-page":"456","article-title":"Sur un d\u00e9placement naturel de la clavicule.","volume":"23","author":"Martin","year":"1765","journal-title":"J Med Chir Pharmacol"},{"key":"2020042118074327400_i0003-3219-079-01-0178-b2","first-page":"93","article-title":"Kombination rudimentarer 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