{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,12]],"date-time":"2026-09-12T01:36:11Z","timestamp":1789176971935,"version":"build-2803163510"},"reference-count":17,"publisher":"American Dental Society of Anesthesiology (ADSA)","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2014]]},"abstract":"<jats:title>Abstract<\/jats:title>\n        <jats:p>Klippel-Feil syndrome (KFS) is a rare disease characterized by a classic triad comprising a short neck, a low posterior hairline, and restricted motion of the neck due to fused cervical vertebrae. We report repeated anesthetic management for orthognathic surgeries for a KFS patient with micrognathia. Because KFS can be associated with a number of other anomalies, we therefore performed a careful preoperative evaluation to exclude them. The patient had an extremely small mandible, significant retrognathia, and severe limitation of cervical mobility due to cervical vertebral fusion. As difficult intubation was predicted, awake nasal endotracheal intubation with a fiberoptic bronchoscope was our first choice for gaining control of the patient's airway. Moreover, the possibility of respiratory distress due to postoperative laryngeal edema was considered because of the surgeries on the mandible. In the operating room, tracheotomy equipment was always kept ready if a perioperative surgical airway control was required. Three orthognathic surgeries and their associated anesthetics were completed without a fatal outcome, although once the patient was transferred to the intensive care unit for precautionary postoperative airway management and observation. Careful preoperative examination and preparation for difficult airway management are important for KFS patients with micrognathia.<\/jats:p>","DOI":"10.2344\/0003-3006-61.3.103","type":"journal-article","created":{"date-parts":[[2014,9,5]],"date-time":"2014-09-05T19:07:48Z","timestamp":1409944068000},"page":"103-106","source":"Crossref","is-referenced-by-count":11,"title":["Repeated Anesthetic Management for a Patient With Klippel-Feil Syndrome"],"prefix":"10.2344","volume":"61","author":[{"given":"Yuri","family":"Hase","sequence":"first","affiliation":[{"name":"Department of Dental Anesthesiology, Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nobuhito","family":"Kamekura","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Toshiaki","family":"Fujisawa","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kazuaki","family":"Fukushima","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1191","reference":[{"key":"i0003-3006-61-3-103-b01","series-title":"Spine","first-page":"E798","article-title":"Classification of congenitally fused cervical patterns in Klippel-Feil patients","volume":"31","author":"Samartzis\n              D,","year":"2006","unstructured":"Samartzis\n              D, \n            \n              Herman\n              J, \n            \n              Lubicky\n              JP, \n            \n              Shen\n              FH. \n          \n          Classification of congenitally fused cervical patterns in Klippel-Feil patients. Spine. 2006;31:E798\u2013E804."},{"key":"i0003-3006-61-3-103-b02","series-title":"Anesth Analg","first-page":"1220","article-title":"Crisis resource management of the airway in a patient with Klippel-Feil syndrome, congenital deafness, and aortic dissection","volume":"108","author":"Khawaja\n              OM,","year":"2009","unstructured":"Khawaja\n              OM, \n            \n              Reed\n              JT, \n            \n              Shaefi\n              S, \n            \n              Chitilian\n              HV, \n            \n              Sandberg\n              WS. \n          \n          Crisis resource management of the airway in a patient with Klippel-Feil syndrome, congenital deafness, and aortic dissection. 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Indian J Anaesth. 2006;50:128\u2013130."},{"key":"i0003-3006-61-3-103-b13","series-title":"Anaesth Intensive Care","first-page":"124","article-title":"Adult Klippel-Feil syndrome: haemodynamic instability in the prone position and postoperative respiratory failure","volume":"35","author":"Teoh\n              DCA,","year":"2007","unstructured":"Teoh\n              DCA, \n            \n              Williams\n              DL. \n          \n          Adult Klippel-Feil syndrome: haemodynamic instability in the prone position and postoperative respiratory failure. 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The influence of orthognathic surgery on ventilation during sleep. Int J Oral Maxillofac Surg. 2011;40:146\u2013149."}],"container-title":["Anesthesia Progress"],"original-title":[],"link":[{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/view\/journals\/anpr\/61\/3\/article-p103.xml","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/meridian.allenpress.com\/anesthesia-progress\/article-pdf\/61\/3\/103\/2101239\/0003-3006-61_3_103.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/downloadpdf\/journals\/anpr\/61\/3\/article-p103.xml","content-type":"text\/html","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/downloadpdf\/journals\/anpr\/61\/3\/article-p103.xml","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,10,7]],"date-time":"2024-10-07T12:32:08Z","timestamp":1728304328000},"score":1,"resource":{"primary":{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/view\/journals\/anpr\/61\/3\/article-p103.xml"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2014]]},"references-count":17,"journal-issue":{"issue":"3"},"URL":"https:\/\/doi.org\/10.2344\/0003-3006-61.3.103","relation":{},"ISSN":["0003-3006","1878-7177"],"issn-type":[{"value":"0003-3006","type":"print"},{"value":"1878-7177","type":"electronic"}],"subject":[],"published":{"date-parts":[[2014]]}}}