{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,10,8]],"date-time":"2024-10-08T04:15:59Z","timestamp":1728360959178},"reference-count":9,"publisher":"American Dental Society of Anesthesiology (ADSA)","issue":"4","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2016]]},"abstract":"<jats:p>Emanuel syndrome is associated with supernumerary chromosome, which consists of the extra genetic material from chromosome 11 and 22. The frequency of this syndrome has been reported as 1 in 110,000. It is a rare anomaly associated with multiple systemic malformations such as micrognathia and congenital heart disease. In addition, patients with Emanuel syndrome may have seizure disorders. We experienced anesthetic management of a patient with Emanuel syndrome who underwent palatoplasty. This patient had received tracheotomy due to micrognathia. In addition, he had atrial septal defect, mild pulmonary artery stenosis, and cleft palate. Palatoplasty was performed without any complication during anesthesia. Close attention was directed to cardiac function, seizure, and airway management.<\/jats:p>","DOI":"10.2344\/16-00028.1","type":"journal-article","created":{"date-parts":[[2016,12,14]],"date-time":"2016-12-14T21:58:50Z","timestamp":1481752730000},"page":"201-203","source":"Crossref","is-referenced-by-count":1,"title":["Anesthetic Management of a Patient With Emanuel Syndrome"],"prefix":"10.2344","volume":"63","author":[{"given":"Masanori","family":"Tsukamoto","sequence":"first","affiliation":[{"name":"Department of Dental Anesthesiology, Kyushu University Hospital, Fukuoka, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takashi","family":"Hitosugi","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Faculty of Dental Science, Kyushu University, Fukuoka, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kanako","family":"Esaki","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Kyushu University Hospital, Fukuoka, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takeshi","family":"Yokoyama","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Faculty of Dental Science, Kyushu University, Fukuoka, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1191","reference":[{"key":"i0003-3006-63-4-201-b01","series-title":"AM J Med Genet A","first-page":"1712","article-title":"Phenotypic delineation of Emanuel syndrome (supernumerary derivative 22 syndrome): clinical features of 63 individuals","volume":"149","author":"Carter \n              MT,","year":"2009","unstructured":"Carter \n              MT, \n            \n            \n              St. Pierre \n              SA, \n            \n            \n              Zackai \n              EH, \n            \n            \n              Emanuel \n              BS, \n            \n            \n              Boycott \n              KM. \n            \n          \n          Phenotypic delineation of Emanuel syndrome (supernumerary derivative 22 syndrome): clinical features of 63 individuals. AM J Med Genet A. 2009;149:1712\u20131721."},{"key":"i0003-3006-63-4-201-b02","series-title":"Pediatrics Int","first-page":"462","article-title":"Prevalence of Emanuel syndrome: theoretical frequency and surveillance result","volume":"56","author":"Ohye \n              T,","year":"2014","unstructured":"Ohye \n              T, \n            \n            \n              Inagaki \n              H, \n            \n            \n              Kato \n              T, \n            \n            \n              Tsutsumi \n              M, \n            \n            \n              Kurahashi \n              H. \n            \n          \n          Prevalence of Emanuel syndrome: theoretical frequency and surveillance result. Pediatrics Int. 2014;56:462\u2013466."},{"key":"i0003-3006-63-4-201-b03","series-title":"J Pediatr Neurosci","first-page":"194","article-title":"Emanuel syndrome: a rare disorder that is often confused with Kabuki syndrome","volume":"10","author":"Kapoor \n              S,","year":"2015","unstructured":"Kapoor \n              S, \n            \n          \n          Emanuel syndrome: a rare disorder that is often confused with Kabuki syndrome. J Pediatr Neurosci. 2015;10:194\u2013195."},{"key":"i0003-3006-63-4-201-b04","series-title":"J Anesth","first-page":"450","article-title":"Anesthetic management of pediatric patients with Emanuel syndrome","volume":"29","author":"Nishinarita \n              R,","year":"2015","unstructured":"Nishinarita \n              R, \n            \n            \n              Mihara \n              T, \n            \n            \n              Nakamura \n              N, \n            \n            \n              Miyamoto \n              Y, \n            \n            \n              Ka \n              K. \n            \n          \n          Anesthetic management of pediatric patients with Emanuel syndrome. J Anesth. 2015;29:450\u2013452."},{"key":"i0003-3006-63-4-201-b05","series-title":"J APOS","first-page":"211","article-title":"de Alba Campomanes AG. Lipodermoid in a patient with Emanuel syndrome","volume":"11","author":"Glase \n              TS,","year":"2012","unstructured":"Glase \n              TS, \n            \n            \n              Rauen \n              KA, \n            \n            \n              Jeng \n              LJB, \n            \n          \n          de Alba Campomanes AG. Lipodermoid in a patient with Emanuel syndrome. J APOS. 2012;11:211\u2013213."},{"key":"i0003-3006-63-4-201-b06","series-title":"Anaesthesia","first-page":"147","article-title":"Intubation of infants with Pierre Robin syndrome: the use of the paraglossal approach combined with a gum-elastic bougie in six consecutive cases","volume":"63","author":"Semjen \n              F,","year":"2008","unstructured":"Semjen \n              F, \n            \n            \n              Bordes \n              M, \n            \n            \n              Cros \n              AM. \n            \n          \n          Intubation of infants with Pierre Robin syndrome: the use of the paraglossal approach combined with a gum-elastic bougie in six consecutive cases. Anaesthesia. 2008;63:147\u2013150."},{"key":"i0003-3006-63-4-201-b07","series-title":"Br J Anaesth","first-page":"517","article-title":"Working Group on Non-invasive Haemodynamic Monitoring in Paediatrics. Cardiac output measurement in children: comparison of Aesculon\u00ae cardiac output monitor and thermodilution","volume":"100","author":"Tomaske \n              M,","year":"2008","unstructured":"Tomaske \n              M, \n            \n            \n              Knirsch \n              W, \n            \n            \n              Kretschmar \n              O, \n            \n            et al;\n          \n          Working Group on Non-invasive Haemodynamic Monitoring in Paediatrics. Cardiac output measurement in children: comparison of Aesculon\u00ae cardiac output monitor and thermodilution. Br J Anaesth. 2008;100:517\u2013520."},{"key":"i0003-3006-63-4-201-b08","series-title":"Anesth Analg","first-page":"517","article-title":"The effects of sevoflurane and hyperventilation on electrocorticogram spike activity in patients with refractory epilepsy","volume":"101","author":"Kurita \n              N,","year":"2005","unstructured":"Kurita \n              N, \n            \n            \n              Kawaguchi \n              M, \n            \n            \n              Hoshida \n              T, \n            \n            \n              Nakase \n              H, \n            \n            \n              Sakaki \n              T, \n            \n            \n              Furuya \n              H. \n            \n          \n          The effects of sevoflurane and hyperventilation on electrocorticogram spike activity in patients with refractory epilepsy. Anesth Analg. 2005;101:517\u2013523."},{"key":"i0003-3006-63-4-201-b09","series-title":"J Clin Anesth","first-page":"674","article-title":"Anesthetic management of Pallister-Killian syndrome using a Bispectral Index monitor in a patient with severe seizures","volume":"23","author":"Kira \n              S.","year":"2011","unstructured":"Kira \n              S. \n            \n          \n          Anesthetic management of Pallister-Killian syndrome using a Bispectral Index monitor in a patient with severe seizures. J Clin Anesth. 2011;23:674\u2013676."}],"container-title":["Anesthesia Progress"],"original-title":[],"link":[{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/view\/journals\/anpr\/63\/4\/article-p201.xml","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/meridian.allenpress.com\/anesthesia-progress\/article-pdf\/63\/4\/201\/2101437\/16-00028_1.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/downloadpdf\/journals\/anpr\/63\/4\/article-p201.xml","content-type":"text\/html","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/downloadpdf\/journals\/anpr\/63\/4\/article-p201.xml","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,10,7]],"date-time":"2024-10-07T12:37:13Z","timestamp":1728304633000},"score":1,"resource":{"primary":{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/view\/journals\/anpr\/63\/4\/article-p201.xml"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016]]},"references-count":9,"journal-issue":{"issue":"4"},"URL":"https:\/\/doi.org\/10.2344\/16-00028.1","relation":{},"ISSN":["0003-3006","1878-7177"],"issn-type":[{"type":"print","value":"0003-3006"},{"type":"electronic","value":"1878-7177"}],"subject":[],"published":{"date-parts":[[2016]]}}}