{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,9]],"date-time":"2026-10-09T03:34:52Z","timestamp":1791516892879,"version":"4.3.4"},"reference-count":8,"publisher":"American Dental Society of Anesthesiology (ADSA)","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2021,10,1]]},"abstract":"Rett syndrome (RTT) is a rare genetic disorder that can present challenges in airway management during general anesthesia. This is a case report involving a 23-year-old woman with RTT who received an intubated general anesthetic 3 times for dental treatment. The patient also had severe scoliosis, was bedridden, and had dysphagia. These contributing factors likely led to the development of postoperative respiratory complications including pneumonia after the first case. As a result, several changes were incorporated into the 2 subsequent anesthetic plans in efforts to reduce the risk of such complications. Despite these measures, the patient was suspected of having bronchitis postoperatively after the second anesthetic, although the third occurred uneventfully. Anesthetic management alterations included use of desflurane for anesthetic maintenance and postoperatively delaying oral intake and instituting active postural changes.<\/jats:p>","DOI":"10.2344\/anpr-68-02-07","type":"journal-article","created":{"date-parts":[[2021,10,5]],"date-time":"2021-10-05T16:42:39Z","timestamp":1633452159000},"page":"163-167","source":"Crossref","is-referenced-by-count":6,"title":["Anesthetic Management of a Rett Syndrome Patient at High Risk for Respiratory Complications"],"prefix":"10.2344","volume":"68","author":[{"given":"Nobuhito","family":"Kamekura","sequence":"first","affiliation":[{"name":"Department of Dental Anesthesiology, Faculty of Dental Medicine and Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Takayuki","family":"Hojo","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Faculty of Dental Medicine and Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yukie","family":"Nitta","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Faculty of Dental Medicine and Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yuri","family":"Hase","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Faculty of Dental Medicine and Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Toshiaki","family":"Fujisawa","sequence":"additional","affiliation":[{"name":"Department of Dental Anesthesiology, Faculty of Dental Medicine and Graduate School of Dental Medicine, Hokkaido University, Sapporo, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1191","published-online":{"date-parts":[[2021,10,4]]},"reference":[{"key":"2021100419041605000_i0003-3006-68-3-163-b01","doi-asserted-by":"crossref","unstructured":"Krajnc\n N.\n \n \n Management of epilepsy in patients with Rett syndrome: perspectives and considerations.\n\t\t\t\t\tTher Clin Risk Manag.\n\t\t\t\t\t2015;\n\t\t\t\t\t11:\n\t\t\t\t\t925\u2013\n\t\t\t\t\t932.","DOI":"10.2147\/TCRM.S55896"},{"key":"2021100419041605000_i0003-3006-68-3-163-b02","doi-asserted-by":"crossref","unstructured":"Neul\n JL,\n \n \n Kaufmann\n WE,\n \n \n Glaze\n DG,\n \n et al;\n \n RettSearch Consortium. Rett syndrome: revised diagnostic criteria and nomenclature.\n\t\t\t\t\tAnn Neurol.\n\t\t\t\t\t2010;\n\t\t\t\t\t68:\n\t\t\t\t\t944\u2013\n\t\t\t\t\t950.","DOI":"10.1002\/ana.22124"},{"key":"2021100419041605000_i0003-3006-68-3-163-b03","unstructured":"Kako\n H,\n \n \n Martin\n DP,\n \n \n Cartabuke\n R,\n \n \n Beebe\n A,\n \n \n Klamar\n J,\n \n \n Tobias\n JD.\n \n \n Perioperative management of a patient with Rett syndrome.\n\t\t\t\t\tInt J Clin Exp Med.\n\t\t\t\t\t2013;\n\t\t\t\t\t6:\n\t\t\t\t\t393\u2013\n\t\t\t\t\t403."},{"key":"2021100419041605000_i0003-3006-68-3-163-b04","doi-asserted-by":"crossref","unstructured":"Motomura\n Y,\n \n \n Idei\n M,\n \n \n Sato\n H,\n \n \n Goto\n T.\n \n \n Anesthetic management of a Rett syndrome patient with apnea and epilepsy: a case report.\n\t\t\t\t\tJA Clin Rep.\n\t\t\t\t\t2018;\n\t\t\t\t\t4:\n\t\t\t\t\t32\u2013\n\t\t\t\t\t35.","DOI":"10.1186\/s40981-018-0169-y"},{"key":"2021100419041605000_i0003-3006-68-3-163-b05","doi-asserted-by":"crossref","unstructured":"Lawrence\n VA,\n \n \n Cornell\n JE,\n \n \n Smetana\n GW.\n \n \n Strategies to reduce postoperative pulmonary complications after noncardiothoracic surgery: systematic review for the American College of Physicians.\n\t\t\t\t\tAnn Intern Med.\n\t\t\t\t\t2006;\n\t\t\t\t\t144:\n\t\t\t\t\t596\u2013\n\t\t\t\t\t608.","DOI":"10.7326\/0003-4819-144-8-200604180-00011"},{"key":"2021100419041605000_i0003-3006-68-3-163-b06","doi-asserted-by":"crossref","unstructured":"Akashiba\n T,\n \n \n Ishikawa\n Y,\n \n \n Ishihara\n H,\n \n et al.\n\t\t\t\t\t\n The Japanese Respiratory Society Noninvasive Positive Pressure ventilation (NPPV) guidelines (second revised edition).\n\t\t\t\t\tRespir Investig.\n\t\t\t\t\t2017;\n\t\t\t\t\t55:\n\t\t\t\t\t83\u2013\n\t\t\t\t\t92.","DOI":"10.1016\/j.resinv.2015.11.007"},{"key":"2021100419041605000_i0003-3006-68-3-163-b07","doi-asserted-by":"crossref","unstructured":"Costa Leme\n A,\n \n \n Hajjar\n LA,\n \n \n Volpe\n MS,\n \n et al.\n\t\t\t\t\t\n Effect of intensive vs moderate alveolar recruitment strategies added to lung-protective ventilation on postoperative pulmonary complications: a randomized clinical trial.\n\t\t\t\t\tJAMA.\n\t\t\t\t\t2017;\n\t\t\t\t\t317:\n\t\t\t\t\t1422\u2013\n\t\t\t\t\t1432.","DOI":"10.1001\/jama.2017.2297"},{"key":"2021100419041605000_i0003-3006-68-3-163-b08","doi-asserted-by":"crossref","unstructured":"Hedenstierna\n G,\n \n \n Edmark\n L.\n \n \n Protective ventilation during anesthesia: is it meaningful?\n \n Anesthesiology\n .\n\t\t\t\t\t2016;\n\t\t\t\t\t125:\n\t\t\t\t\t1079\u2013\n\t\t\t\t\t1082.","DOI":"10.1097\/ALN.0000000000001382"}],"container-title":["Anesthesia Progress"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/meridian.allenpress.com\/anesthesia-progress\/article-pdf\/68\/3\/163\/2919570\/i0003-3006-68-3-163.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"http:\/\/meridian.allenpress.com\/anesthesia-progress\/article-pdf\/68\/3\/163\/2919570\/i0003-3006-68-3-163.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,1,18]],"date-time":"2024-01-18T19:51:24Z","timestamp":1705607484000},"score":1,"resource":{"primary":{"URL":"https:\/\/anesthesiaprogress.kglmeridian.com\/view\/journals\/anpr\/68\/3\/article-p163.xml"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,10,1]]},"references-count":8,"journal-issue":{"issue":"3","published-online":{"date-parts":[[2021,10,4]]},"published-print":{"date-parts":[[2021,10,1]]}},"URL":"https:\/\/doi.org\/10.2344\/anpr-68-02-07","relation":{},"ISSN":["1878-7177","0003-3006"],"issn-type":[{"value":"1878-7177","type":"electronic"},{"value":"0003-3006","type":"print"}],"subject":[],"published":{"date-parts":[[2021,10,1]]}}}