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The skin is frequently involved with a wide variety of cutaneous manifestations, most of which are non-specific. Recognition of skin lesions in AIDs may sometimes provide clues for a correct diagnosis. In this review, the cutaneous involvements of &gt;20 selected AIDs were summarized and organized into different categories based on their characteristic manifestations, such as urticarial dermatosis, neutrophilic dermatosis, granulomatosis, chilblain, lipodystrophy, and hyperkeratosis. With this classification scheme, cutaneous manifestations in AIDs could be more easily identified to facilitate diagnosis in clinical practice.<\/jats:p>","DOI":"10.2478\/rir-2021-0030","type":"journal-article","created":{"date-parts":[[2022,2,21]],"date-time":"2022-02-21T15:52:06Z","timestamp":1645458726000},"page":"217-225","source":"Crossref","is-referenced-by-count":8,"title":["Cutaneous manifestations of autoinflammatory diseases"],"prefix":"10.2478","volume":"2","author":[{"given":"Di","family":"Wu","sequence":"first","affiliation":[{"name":"Department of Rheumatology and Clinical Immunology , State Key Laboratory of Complex Severe and Rare Diseases , Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID) , Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education , Beijing , China"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Min","family":"Shen","sequence":"additional","affiliation":[{"name":"Department of Rheumatology and Clinical Immunology , State Key Laboratory of Complex Severe and Rare Diseases , Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID) , Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education , Beijing , China"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Qingping","family":"Yao","sequence":"additional","affiliation":[{"name":"Division of Rheumatology , Allergy, and Immunology, Stony Brook University School of Medicine , Stony Brook , NY , USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"374","published-online":{"date-parts":[[2021,12,31]]},"reference":[{"key":"2026070915583843476_j_rir-2021-0030_ref_001","doi-asserted-by":"crossref","unstructured":"Nigrovic PA, Lee PY, Hoffman HM. 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