{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,5,17]],"date-time":"2025-05-17T04:07:21Z","timestamp":1747454841502,"version":"3.40.5"},"reference-count":10,"publisher":"Scientific Scholar","content-domain":{"domain":["surgicalneurologyint.com"],"crossmark-restriction":true},"short-container-title":[],"abstract":"<jats:sec id=\"st1\">\n<jats:title>Background: <\/jats:title>\n<jats:p>Hypertrophic pachymeningitis (HP) is a rare neurological disorder characterized by dural thickening. Here, we discuss the diagnosis and surgical management of a 38-year-old whose myelopathy was attributed to dorsally compressive HP extending from the lower cerebellar fossa to C3.<\/jats:p>\n<\/jats:sec>\n<jats:sec id=\"st2\">\n<jats:title>Case Description: <\/jats:title>\n<jats:p>A 38-year-old male with Sj\u00f6gren\u2019s syndrome presented with cervical pain, upper limb paresis, dysphagia, and left-sided tongue\/palate paralysis. The cervical magnetic resonance (MR) showed a dorsally compressive lower cerebellar fossa to C3 lesion. When the biopsy revealed HP, and once conservative treatment failed, the patient successfully underwent a posterior surgical decompression, lesion debulking, and craniocervical fusion.<\/jats:p>\n<\/jats:sec>\n<jats:sec id=\"st3\">\n<jats:title>Conclusion: <\/jats:title>\n<jats:p>Cervical HPs should be diagnosed early on MR, and those with significant myelopathy, aggressively surgically treated.<\/jats:p>\n<\/jats:sec>","DOI":"10.25259\/sni_179_2025","type":"journal-article","created":{"date-parts":[[2025,5,16]],"date-time":"2025-05-16T11:01:47Z","timestamp":1747393307000},"page":"179","update-policy":"https:\/\/doi.org\/10.25259\/crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Craniocervical hypertrophic pachymeningitis"],"prefix":"10.25259","volume":"16","author":[{"given":"Murilo dos Santos","family":"Mancilha","sequence":"first","affiliation":[{"name":"Department of Neurosurgery, Anhembi Morumbi University, S\u00e3o Jos\u00e9 dos Campos, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Filipi Fim","family":"Andre\u00e3o","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Federal University of Rio de Janeiro, Rio de Janeiro, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"B\u00e1rbara de \u00c1vila","family":"Costa Janu\u00e1rio","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Anhembi Morumbi University, S\u00e3o Jos\u00e9 dos Campos, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Filipe Virgilio","family":"Ribeiro","sequence":"additional","affiliation":[{"name":"Department of Medicine, Bar\u00e3o de Mau\u00e1 University Center, Faculty of Medicine, Ribeir\u00e3o Preto, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Matheus","family":"Nepomuceno Fernandes","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Anhembi Morumbi University, S\u00e3o Jos\u00e9 dos Campos, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Luis Flavio","family":"Fabrini Paleare","sequence":"additional","affiliation":[{"name":"Department of Medicine and Life Sciences, Pontifical Catholic University of Paran\u00e1, Curitiba, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bruno Pasqualino Aguilar","family":"da Silva","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Neurosolution Clinic, S\u00e3o Jos\u00e9 dos Campos, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marcelo Medeiros","family":"Felippe","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Neurosolution Clinic, S\u00e3o Jos\u00e9 dos Campos, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Danilo Gomes","family":"Quadros","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Nucleo Oscar Freire, Salvador, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"10894","published-online":{"date-parts":[[2025,5,16]]},"reference":[{"key":"10.25259\/SNI_179_2025\/ref-1","doi-asserted-by":"crossref","first-page":"169","DOI":"10.14245\/kjs.2015.12.3.169","article-title":"Idiopathic hypertrophic pachymeningitis in the craniocervical junction","volume":"12","author":"Bang","year":"2015","journal-title":"Korean J Spine"},{"key":"10.25259\/SNI_179_2025\/ref-2","first-page":"211","article-title":"Rapid recurrence of spinal idiopathic hypertrophic pachymeningitis: A case report","volume":"5","author":"Choi","year":"2008","journal-title":"Korean J Spine"},{"key":"10.25259\/SNI_179_2025\/ref-3","doi-asserted-by":"crossref","first-page":"199","DOI":"10.1007\/s10143-004-0321-1","article-title":"Idiopathic intracranial hypertrophic pachymeningitis: Two case reports and review of the 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Neuroradiol"},{"key":"10.25259\/SNI_179_2025\/ref-7","first-page":"590","article-title":"Idiopathic hypertrophic spinal pachymeningitis: Report of two cases with typical MR imaging findings","volume":"28","author":"Pai","year":"2007","journal-title":"AJNR Am J Neuroradiol"},{"key":"10.25259\/SNI_179_2025\/ref-8","doi-asserted-by":"crossref","first-page":"S636","DOI":"10.1007\/s00586-015-3958-2","article-title":"Idiopathic hypertrophic spinal pachymeningitis: A case report and review of literature","volume":"24","author":"Qin","year":"2015","journal-title":"Eur Spine J"},{"key":"10.25259\/SNI_179_2025\/ref-9","doi-asserted-by":"crossref","first-page":"195","DOI":"10.3171\/2011.4.SPINE1037","article-title":"Idiopathic hypertrophic spinal pachymeningitis","volume":"15","author":"Ranasinghe","year":"2011","journal-title":"J Neurosurg 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