{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,18]],"date-time":"2026-08-18T03:56:34Z","timestamp":1787025394411,"version":"build-2736575974"},"reference-count":8,"publisher":"Scientific Scholar","content-domain":{"domain":["surgicalneurologyint.com"],"crossmark-restriction":true},"short-container-title":[],"abstract":"<jats:sec id=\"st1\">\n                    <jats:title>Background:<\/jats:title>\n                    <jats:p>Achondroplasia is a rare genetic disorder affecting bone development, resulting in disproportionate short stature. The coexistence of os odontoideum (OO) in individuals with achondroplasia is exceptionally uncommon.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec id=\"st2\">\n                    <jats:title>Case Description:<\/jats:title>\n                    <jats:p>We present the case of a 29-year-old female with achondroplasia who experienced progressive weakness in the extremities, ultimately leading to difficulty in ambulation. Radiographic evaluation revealed an atlantoaxial dislocation secondary to an unstable OO. Surgical stabilization of C1\u2013C2 resulted in gradual yet significant neurological recovery.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec id=\"st3\">\n                    <jats:title>Conclusion:<\/jats:title>\n                    <jats:p>Since the first reported case in 1974, only a limited number of achondroplastic individuals with atlantoaxial dislocation due to OO have been documented.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.25259\/sni_219_2026","type":"journal-article","created":{"date-parts":[[2026,5,22]],"date-time":"2026-05-22T06:29:54Z","timestamp":1779431394000},"page":"295","update-policy":"https:\/\/doi.org\/10.25259\/crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["OS odontoideum in an achondroplastic adult \u2013 A case report and review"],"prefix":"10.25259","volume":"17","author":[{"given":"Reza","family":"Mollahouseini","sequence":"first","affiliation":[{"name":"Department Neurosurgery, Firoozgar Hospital, Iran University of Medical Sciences, Tehran, Iran"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Abolfazl","family":"Rahimizadeh","sequence":"additional","affiliation":[{"name":"Pars Advanced and Minimally Invasive Medical Manners Research Center, Pars Hospital, Iran University of Medical Sciences, Tehran, Iran"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Walter","family":"Wiliamson","sequence":"additional","affiliation":[{"name":"The Office of Clinical Research (OCR), Baylor College of Medicine, Houston, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"10894","published-online":{"date-parts":[[2026,5,22]]},"reference":[{"key":"10.25259\/SNI_219_2026\/ref-1","doi-asserted-by":"crossref","first-page":"394","DOI":"10.3171\/jns.1974.40.3.0394","article-title":"Atlantoaxial dislocation with quadriparesis in achondroplasia. Case report","volume":"40","author":"Gulati","year":"1974","journal-title":"J Neurosurg"},{"key":"10.25259\/SNI_219_2026\/ref-2","doi-asserted-by":"crossref","first-page":"219","DOI":"10.1186\/s13023-023-02795-2","article-title":"European achondroplasia forum guiding principles for the detection and management of foramen magnum stenosis","volume":"18","author":"Irving","year":"2023","journal-title":"Orphanet J Rare Dis"},{"key":"10.25259\/SNI_219_2026\/ref-3","doi-asserted-by":"crossref","first-page":"443","DOI":"10.4103\/0259-1162.158514","article-title":"Anesthesia for an achondroplastic individual with coexisting atlantoaxial dislocation","volume":"9","author":"Kaushal","year":"2015","journal-title":"Anesth Essays Res"},{"key":"10.25259\/SNI_219_2026\/ref-4","doi-asserted-by":"crossref","first-page":"284","DOI":"10.1159\/000335433","article-title":"Atlanto-axial instability in achondroplastic dwarfs: A report of two cases and literature review","volume":"47","author":"Mohindra","year":"2012","journal-title":"Pediatr Neurosurg"},{"key":"10.25259\/SNI_219_2026\/ref-5","first-page":"142586","article-title":"Atlantoaxial subluxation due to an os odontoideum in an achondroplastic adult: Report of a case and review of the literature","volume":"2015","author":"Rahimizadeh","year":"2015","journal-title":"Case Rep Orthop"},{"key":"10.25259\/SNI_219_2026\/ref-6","first-page":"1","article-title":"Os odontoideum: Review article","volume":"2","author":"Rahimizadeh","year":"2016","journal-title":"Orthop Res Traumatol Open J"},{"key":"10.25259\/SNI_219_2026\/ref-7","doi-asserted-by":"crossref","first-page":"70","DOI":"10.25259\/SNI_101_2022","article-title":"Symptomatic thoracic ossified ligamentum flavum in achondroplasia: A case report and literature review","volume":"13","author":"Rahimizadeh","year":"2022","journal-title":"Surg Neurol Int"},{"key":"10.25259\/SNI_219_2026\/ref-8","doi-asserted-by":"crossref","first-page":"103","DOI":"10.1097\/BPB.0b013e3282f54a55","article-title":"Os odontoideum in achondroplasia: A case report","volume":"17","author":"Yukata","year":"2008","journal-title":"J Pediatr Orthop B"}],"container-title":["Surgical Neurology International"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/surgicalneurologyint.com\/os-odontoideum-in-an-achondroplastic-adult-a-case-report-and-review\/","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/surgicalneurologyint.com\/surgicalint-articles\/os-odontoideum-in-an-achondroplastic-adult-a-case-report-and-review\/","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,5,22]],"date-time":"2026-05-22T06:29:55Z","timestamp":1779431395000},"score":1,"resource":{"primary":{"URL":"http:\/\/surgicalneurologyint.com\/surgicalint-articles\/os-odontoideum-in-an-achondroplastic-adult-a-case-report-and-review\/"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,5,22]]},"references-count":8,"alternative-id":["10.25259\/SNI_219_2026"],"URL":"https:\/\/doi.org\/10.25259\/sni_219_2026","relation":{},"ISSN":["2152-7806","2229-5097"],"issn-type":[{"value":"2152-7806","type":"electronic"},{"value":"2229-5097","type":"print"}],"subject":[],"published":{"date-parts":[[2026,5,22]]},"article-number":"295"}}