{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,3,29]],"date-time":"2022-03-29T20:15:42Z","timestamp":1648584942288},"reference-count":15,"publisher":"Consilium Medicum","issue":"7","license":[{"start":{"date-parts":[[2019,7,15]],"date-time":"2019-07-15T00:00:00Z","timestamp":1563148800000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Terapevticheskii arkhiv"],"abstract":"<jats:p>The article presents a brief description of a rare disease - thrombotic thrombocytopenic purpura (Moshkovits - disease), which is based on the deficiency of ADAMTS-13 metalloproteinase, leading to the development of thrombotic microangiopathy with the defeat of vital organs. The article also describes the clinical observation of a patient with the Moshkovits - disease. The features of the above observation are involvement in the pathological process of the kidneys and intestines, while in the classical descriptions of the disease there is a predominant lesion of the Central nervous system, as well as the genetic form of the disease.<\/jats:p>","DOI":"10.26442\/00403660.2019.07.000131","type":"journal-article","created":{"date-parts":[[2019,8,4]],"date-time":"2019-08-04T22:18:01Z","timestamp":1564957081000},"page":"106-110","source":"Crossref","is-referenced-by-count":0,"title":["Clinical observation of a patient with thrombotic thrombocytopenic purpura with renal and intestinal lesions"],"prefix":"10.26442","volume":"91","author":[{"given":"A G","family":"Stolyar","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P V","family":"Avdonin","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"I E","family":"Valamina","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"E S","family":"Stolyarevich","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"18344","published-online":{"date-parts":[[2019,7,15]]},"reference":[{"key":"ref1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2016-10-709857"},{"key":"ref2","unstructured":"Thrombotic thrombocytopenic purpura. https:\/\/emedicine.medscape.com\/ article\/206598-overview#a5 \u0441\u0441\u044b\u043b\u043a\u0430 \u0430\u043a\u0442\u0438\u0432\u043d\u0430 \u043d\u0430 04.07.2018"},{"key":"ref3","unstructured":"Moschcowitz E. https:\/\/en.wikipedia.org\/wiki\/Eli_Moschcowitz \u0441\u0441\u044b\u043b\u043a\u0430 \u0430\u043a\u0442\u0438\u0432\u043d\u0430 \u043d\u0430 04.07.2018"},{"key":"ref4","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMra020528"},{"key":"ref5","doi-asserted-by":"publisher","DOI":"10.1160\/TH07-12-0761"},{"key":"ref6","doi-asserted-by":"crossref","unstructured":"Feng Y, Li X, Xiao J, Li W, Liu J, Zeng X, Chen X, Chen S. 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Am J Hematol. 2016;28(10):24311. doi: 10.1002\/ ajh.24311"},{"key":"ref10","doi-asserted-by":"publisher","DOI":"10.1007\/s12185-015-1849-2"},{"key":"ref11","doi-asserted-by":"publisher","DOI":"10.1111\/bjh.13564"},{"key":"ref12","doi-asserted-by":"publisher","DOI":"10.1002\/jca.21366"},{"key":"ref13","doi-asserted-by":"publisher","DOI":"10.3109\/09537104.2014.904504"},{"key":"ref14","doi-asserted-by":"publisher","DOI":"10.1016\/S2352-3026(16)30018-7"},{"key":"ref15","doi-asserted-by":"publisher","DOI":"10.1097\/01.ede.000011327"}],"container-title":["Terapevticheskii arkhiv"],"original-title":[],"link":[{"URL":"https:\/\/ter-arkhiv.ru\/0040-3660\/article\/viewFile\/33642\/pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/ter-arkhiv.ru\/0040-3660\/article\/viewFile\/33642\/pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,10,13]],"date-time":"2021-10-13T21:42:14Z","timestamp":1634161334000},"score":1,"resource":{"primary":{"URL":"https:\/\/ter-arkhiv.ru\/0040-3660\/article\/view\/33642"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,7,15]]},"references-count":15,"journal-issue":{"issue":"7","published-online":{"date-parts":[[2019,7,15]]}},"URL":"https:\/\/doi.org\/10.26442\/00403660.2019.07.000131","relation":{},"ISSN":["2309-5342","0040-3660"],"issn-type":[{"value":"2309-5342","type":"electronic"},{"value":"0040-3660","type":"print"}],"subject":[],"published":{"date-parts":[[2019,7,15]]}}}