{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,30]],"date-time":"2026-06-30T19:55:14Z","timestamp":1782849314524,"version":"3.54.5"},"reference-count":23,"publisher":"Consilium Medicum","issue":"5","license":[{"start":{"date-parts":[[2026,6,13]],"date-time":"2026-06-13T00:00:00Z","timestamp":1781308800000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Terapevticheskii arkhiv"],"abstract":"<jats:p>Aim. To describe a Russian cohort of patients with IgG4-related retroperitoneal fibrosis (RPF).\r\nMaterials and methods. This retrospective single-center study included 36 patients diagnosed with IgG4-related RPF according to the revised 2020 diagnostic criteria. Clinical, laboratory, instrumental, and pathomorphological data were analyzed.\r\nResults. The cohort of 36 patients with IgG4-related RPF predominantly comprised males (4:1 ratio), with a median onset age of 52 years and median time to diagnosis of 8 months. The disease most presented with low back or lower abdominal pain (75%), renal dysfunction (44%), elevated serum IgG41.35 g\/L (82%), and increased ESR\/CRP. Urinary tract infection was detected in 44% due to frequent ureteral catheterization. Isolated retroperitoneal involvement occurred in 72% of cases, with typical infrarenal periaortitis in 58%; atypical sites included perirenal, periureteral, and presacral localizations. Biopsy (n=23) revealed lymphoplasmacytic infiltrate (100%), fibrosis (87%), IgG4+\/CD138+40% (71%), with obliterative phlebitis (26%) and tissue eosinophilia (26%) less common.\r\nConclusion. Compared to international data, our findings reveal a higher prevalence of atypical localizations and concomitant urinary tract infections, necessitating their consideration in diagnostic algorithms and treatment planning for RPF patients.<\/jats:p>","DOI":"10.26442\/00403660.2026.05.203608","type":"journal-article","created":{"date-parts":[[2026,6,15]],"date-time":"2026-06-15T09:09:37Z","timestamp":1781514577000},"page":"306-313","source":"Crossref","is-referenced-by-count":0,"title":["Immunoglobulin G4-related retroperitoneal fibrosis: clinical, laboratory, imaging, and histopathological features in a Russian single-center cohort"],"prefix":"10.26442","volume":"98","author":[{"ORCID":"https:\/\/orcid.org\/0009-0003-7621-5833","authenticated-orcid":false,"given":"Aleksei S.","family":"Veretennikov","sequence":"additional","affiliation":[{"name":"Nasonova Research Institute of Rheumatology"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8099-2107","authenticated-orcid":false,"given":"Anna V.","family":"Torgashina","sequence":"additional","affiliation":[{"name":"Nasonova Research Institute of Rheumatology"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4188-3578","authenticated-orcid":false,"given":"Bogdan D.","family":"Chaltsev","sequence":"additional","affiliation":[{"name":"Nasonova Research Institute of Rheumatology"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1082-8659","authenticated-orcid":false,"given":"Alla M.","family":"Kovrigina","sequence":"additional","affiliation":[{"name":"National Medical Research Center for Hematology"},{"name":"Sechenov First Moscow State Medical University (Sechenov University)"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2314-1466","authenticated-orcid":false,"given":"Julia I.","family":"Khvan","sequence":"additional","affiliation":[{"name":"Nasonova Research Institute of Rheumatology"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3183-0464","authenticated-orcid":false,"given":"Danil A.","family":"Dibrov","sequence":"additional","affiliation":[{"name":"Nasonova Research Institute of Rheumatology"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"18344","published-online":{"date-parts":[[2026,6,13]]},"reference":[{"key":"ref1","doi-asserted-by":"publisher","DOI":"10.1093\/rheumatology\/keaf008"},{"key":"ref2","doi-asserted-by":"publisher","DOI":"10.1136\/ard-2023-223950"},{"key":"ref3","doi-asserted-by":"publisher","DOI":"10.47360\/1995-4484-2020-368-375"},{"key":"ref4","doi-asserted-by":"publisher","DOI":"10.1002\/art.41120"},{"key":"ref5","doi-asserted-by":"publisher","DOI":"10.1080\/14397595.2020.1859710"},{"key":"ref6","doi-asserted-by":"publisher","DOI":"10.1253\/circj.CJ-24-0026"},{"key":"ref7","doi-asserted-by":"publisher","DOI":"10.26442\/00403660.2019.05.000236"},{"key":"ref8","doi-asserted-by":"crossref","unstructured":"Kawano M, Zen Y, Saeki T, et al. IgG4-related disease. In: Stone JH, ed. A Clinician\u2019s Pearls & Myths in Rheumatology. 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