{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,2,21]],"date-time":"2025-02-21T23:34:25Z","timestamp":1740180865850,"version":"3.37.3"},"reference-count":13,"publisher":"Consilium Medicum","issue":"8","license":[{"start":{"date-parts":[[2021,8,15]],"date-time":"2021-08-15T00:00:00Z","timestamp":1628985600000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-sa\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Terapevticheskii arkhiv"],"abstract":"<jats:p>The article presents a clinical case of a 23-year-old patient with an extremely severe congenital form of chronic intestinal pseudoobstruction coupled with a neuromyopathy,colon malrotation, malabsorption, bacterial overgrowth syndrome, cholelithiasis and gastrostasis, which excluded bowel transplantation. Long-term treatment in the intensive care unit with combined, mainly parenteral nutrition for 6 months, using antibiotics, prokinetics, intestinal decompression allowed to achieve partial stabilization of the patients condition and transfer to home treatment with the continuation of adequate complex therapy.<\/jats:p>","DOI":"10.26442\/3660.2021.08.200976","type":"journal-article","created":{"date-parts":[[2021,9,8]],"date-time":"2021-09-08T11:37:07Z","timestamp":1631101027000},"page":"936-942","source":"Crossref","is-referenced-by-count":0,"title":["Chronic intestinal pseudoobstruction: difficulties in diagnosis and treatment. Case report"],"prefix":"10.26442","volume":"93","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-3107-3731","authenticated-orcid":false,"given":"Igor E.","family":"Khatkov","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5169-2199","authenticated-orcid":false,"given":"Viktor V.","family":"Tsvirkun","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9782-4860","authenticated-orcid":false,"given":"Asfold I.","family":"Parfenov","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4010-6761","authenticated-orcid":false,"given":"Olga V.","family":"Akhmadullina","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-0692-7133","authenticated-orcid":false,"given":"Larisa M.","family":"Krums","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-0921-7199","authenticated-orcid":false,"given":"Valerii V.","family":"Subbotin","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9576-2953","authenticated-orcid":false,"given":"Svetlana V.","family":"Bykova","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2800-6503","authenticated-orcid":false,"given":"Tatiana N.","family":"Kuzmina","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9118-4017","authenticated-orcid":false,"given":"Elena V.","family":"Novikova","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-0010-5294","authenticated-orcid":false,"given":"Kirill V.","family":"Shishin","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4308-8009","authenticated-orcid":false,"given":"Sergei G.","family":"Khomeriki","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4550-1509","authenticated-orcid":false,"given":"Daniil A.","family":"Degterev","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Zoia P.","family":"Lashchenkova","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"18344","published-online":{"date-parts":[[2021,8,15]]},"reference":[{"key":"ref1","unstructured":"Dudley HA, Sinclair IS, Mclaren IF, et al. 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II \u0447\u0430\u0441\u0442\u044c. \u041f\u0435\u0440\u0432\u0438\u0447\u043d\u044b\u0435 \u0438 \u0432\u0442\u043e\u0440\u0438\u0447\u043d\u044b\u0435 \u0445\u0440\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u0438\u0435 \u043f\u0441\u0435\u0432\u0434\u043e\u043e\u0431\u0441\u0442\u0440\u0443\u043a\u0442\u0438\u0432\u043d\u044b\u0435 \u0441\u0438\u043d\u0434\u0440\u043e\u043c\u044b \u0443 \u0434\u0435\u0442\u0435\u0439 \u0438 \u0432\u0437\u0440\u043e\u0441\u043b\u044b\u0445. \u0420\u043e\u0441\u0441\u0438\u0439\u0441\u043a\u0438\u0439 \u0432\u0435\u0441\u0442\u043d\u0438\u043a \u0434\u0435\u0442\u0441\u043a\u043e\u0439 \u0445\u0438\u0440\u0443\u0440\u0433\u0438\u0438, \u0430\u043d\u0435\u0441\u0442\u0435\u0437\u0438\u043e\u043b\u043e\u0433\u0438\u0438 \u0438 \u0440\u0435\u0430\u043d\u0438\u043c\u0430\u0446\u0438\u0438. 2016;6(2):102-11 [Averyanova YuV, Razumovsky AYu, Stepanov AE. Etiology and pathophysiology of chronic intestinal syndrome of pseudo-obstruction in children. Part II. Primary and secondary chronic syndrome of pseudo-obstruction in children and adults. 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