{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,6,1]],"date-time":"2025-06-01T04:23:35Z","timestamp":1748751815239},"reference-count":11,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2011,1]]},"abstract":"<jats:p>The authors report a case of concurrent moyamoya disease and glycogen storage disease Type 1a that was successfully managed with bypass surgery. This 7-year-old Japanese girl, diagnosed with glycogen storage disease Type 1a at the age of 2 years, presented with repeated transient ischemic attacks. Cerebral angiography revealed severe stenosis at the terminal portions of the bilateral internal carotid arteries, with typical moyamoya vessels. The patient underwent superficial temporal artery\u2013middle cerebral artery anastomosis and encephalomyosynangiosis bilaterally, in 2 staged procedures at an interval of 4 months. Despite perioperative administration of glucose, hypoglycemia and metabolic acidosis occurred after both surgeries. The symptoms were milder after the second surgery, in which an increased dose of glucose was used. The patient tolerated the perioperative conditions well under intensified medical treatment, and no further ischemic symptoms occurred.<\/jats:p>","DOI":"10.3171\/2010.10.peds10175","type":"journal-article","created":{"date-parts":[[2010,12,31]],"date-time":"2010-12-31T14:36:41Z","timestamp":1293806201000},"page":"11-14","source":"Crossref","is-referenced-by-count":2,"title":["Surgical treatment and perioperative management of moyamoya disease associated with glycogen storage disease Type 1a"],"prefix":"10.3171","volume":"7","author":[{"given":"Yusuke","family":"Egashira","sequence":"first","affiliation":[{"name":"Department of Neurosurgery, National Cerebral and Cardiovascular Center, Suita, Osaka;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jun C.","family":"Takahashi","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, National Cerebral and Cardiovascular Center, Suita, Osaka;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hiroyuki","family":"Ohnishi","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, National Cerebral and Cardiovascular Center, Suita, Osaka;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yukako","family":"Kawasaki","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Yamada Red Cross Hospital, Ise, Mie; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Masamune","family":"Higashigawa","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Yamada Red Cross Hospital, Ise, Mie; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Koji","family":"Iihara","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, National Cerebral and Cardiovascular Center, Suita, Osaka;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Susumu","family":"Miyamoto","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"b1-0070011","series-title":"Surg Neurol","doi-asserted-by":"publisher","first-page":"138","DOI":"10.1016\/S0090-3019(96)00358-8","article-title":"Current state of study on moyamoya disease in Japan","volume":"47","author":"Fukui","year":"1997"},{"key":"b2-0070011","series-title":"Neuropediatrics","doi-asserted-by":"publisher","first-page":"133","DOI":"10.1055\/s-2007-973688","article-title":"Moyamoya disease in a child with glycogen storage disease type Ia","volume":"28","author":"Gouti\u00e8res","year":"1997"},{"key":"b3-0070011","series-title":"Stroke","doi-asserted-by":"publisher","first-page":"1358","DOI":"10.1161\/01.STR.22.11.1358","article-title":"Systemic vascular changes in spontaneous occlusion of the circle of Willis","volume":"22","author":"Ikeda","year":"1991"},{"key":"b4-0070011","series-title":"Neurosurgery","first-page":"1120","article-title":"The relevance of hemodynamic factors to perioperative ischemic complications in childhood moyamoya disease","volume":"38","author":"Iwama","year":"1996"},{"key":"b5-0070011","series-title":"Surg Neurol","doi-asserted-by":"publisher","first-page":"343","DOI":"10.1016\/0090-3019(91)90022-2","article-title":"Perioperative complications of encephalo-duro-arterio-synangiosis: prevention and treatment","volume":"36","author":"Matsushima","year":"1991"},{"issue":"Suppl 72","key":"b6-0070011","series-title":"Acta Neurol Scand Suppl","first-page":"434","article-title":"Clinical and cerebral blood flow study in moyamoya disease with TIA","volume":"60","author":"Nishimoto","year":"1983"},{"key":"b7-0070011","series-title":"J Inherit Metab Dis","doi-asserted-by":"publisher","first-page":"790","DOI":"10.1023\/A:1005319818015","article-title":"Treatment with lowdose diazoxide in two growth-retarded prepubertal girls with glycogen storage disease type Ia resulted in catch-up growth","volume":"20","author":"Nuoffer","year":"1997"},{"key":"b8-0070011","series-title":"J Jpn Soc Clin Anesth","doi-asserted-by":"publisher","first-page":"360","DOI":"10.2199\/jjsca.5.360","article-title":"[The effects of arterial carbon dioxide tension on cerebral blood flow and on cerebral function in \u201cmoyamoya\u201d disease.]","volume":"5","author":"Oku","year":"1985"},{"key":"b9-0070011","series-title":"Pediatrics","doi-asserted-by":"publisher","first-page":"341","DOI":"10.1542\/peds.65.2.341","article-title":"Type I glycogen storage disease with focal nodular hyperplasia of the liver and vasoconstrictive pulmonary hypertension","volume":"65","author":"Pizzo","year":"1980"},{"issue":"Suppl 1","key":"b10-0070011","series-title":"Eur J Pediatr","doi-asserted-by":"publisher","first-page":"S20","DOI":"10.1007\/BF02679990","article-title":"Glycogen storage disease type I: diagnosis, management, clinical course and outcome. 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