{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,30]],"date-time":"2026-04-30T06:23:39Z","timestamp":1777530219494,"version":"3.51.4"},"reference-count":50,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2012,2]]},"abstract":"<jats:p>Chiari malformation Type I (CM-I) is associated with syndromic and nonsyndromic craniosynostosis in pediatric patients, and the surgical management of CM-I in such cases is controversial. Previous guidelines have recommended simultaneous cranial vault expansion and suboccipital decompression. However, spontaneous resolution of CM-I has been observed, and the combined procedure carries additional surgical risks. The authors report the case of a 6-month-old boy with Crouzon syndrome, CM-I, and a cervical syrinx who underwent posterior cranial vault release without suboccipital decompression. Imaging at the 3-month follow-up visit demonstrated complete resolution of the CM-I, improvement in CSF flow, and reduction in the size of the syrinx. This case suggests that up-front suboccipital decompression may not be necessary in patients with craniosynostosis and CM-I. A strategy of initial cranial vault release, followed by watchful waiting and radiographic surveillance, is proposed.<\/jats:p>","DOI":"10.3171\/2011.11.peds11268","type":"journal-article","created":{"date-parts":[[2012,2,1]],"date-time":"2012-02-01T16:41:15Z","timestamp":1328114475000},"page":"111-115","source":"Crossref","is-referenced-by-count":34,"title":["Resolution of syndromic craniosynostosis-associated Chiari malformation Type I without suboccipital decompression after posterior cranial vault release"],"prefix":"10.3171","volume":"9","author":[{"given":"Michael R.","family":"Levitt","sequence":"first","affiliation":[{"name":"Department of Neurosurgery,"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Toba N.","family":"Niazi","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery,"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Richard A.","family":"Hopper","sequence":"additional","affiliation":[{"name":"Division of Plastic Surgery, and"},{"name":"Craniofacial Center, University of Washington School of Medicine, Seattle Children's Hospital, Seattle, Washington"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Richard G.","family":"Ellenbogen","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery,"},{"name":"Craniofacial Center, University of Washington School of Medicine, Seattle Children's Hospital, Seattle, Washington"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jeffrey G.","family":"Ojemann","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery,"},{"name":"Craniofacial Center, University of Washington School of Medicine, Seattle Children's Hospital, Seattle, Washington"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"b1-0090111","series-title":"Paediatr Anaesth","doi-asserted-by":"publisher","first-page":"879","DOI":"10.1111\/j.1460-9592.2009.03096.x","article-title":"A retrospective analysis of anesthesiologic complications in pediatric neurosurgery","volume":"19","author":"Aleksic","year":"2009"},{"issue":"1 Suppl","key":"b2-0090111","series-title":"J Neurosurg","first-page":"53","article-title":"Complications of intracranial pressure monitoring in children with head trauma","volume":"101","author":"Anderson","year":"2004"},{"key":"b3-0090111","series-title":"J Neurosurg","doi-asserted-by":"publisher","first-page":"708","DOI":"10.3171\/jns.1996.84.4.0708","article-title":"Resolution of spinal syringes and Chiari I malformation in a child. 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