{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,28]],"date-time":"2026-01-28T11:20:45Z","timestamp":1769599245138,"version":"3.49.0"},"reference-count":21,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2011,9]]},"abstract":"<jats:p>Encephalocraniocutaneous lipomatosis (ECCL) is a rare neurocutaneous syndrome whose hallmark lesions are benign lipomas of the brain and spinal cord. The authors present a case of a male infant with ECCL who had extensive brainstem and spinal cord lipomas. The management of this patient's hydrocephalus, cervicomedullary compression, tethered cord, and scoliosis over the course of his first 2 years of life is described. This case report and review of the literature is presented to provide a synopsis of the problems likely to be encountered by neurosurgeons who treat patients with this syndrome.<\/jats:p>","DOI":"10.3171\/2011.6.peds11138","type":"journal-article","created":{"date-parts":[[2011,9,1]],"date-time":"2011-09-01T19:51:09Z","timestamp":1314906669000},"page":"316-320","source":"Crossref","is-referenced-by-count":14,"title":["Encephalocraniocutaneous lipomatosis: a review of its clinical pathology and neurosurgical indications"],"prefix":"10.3171","volume":"8","author":[{"given":"Robert E.","family":"Ayer","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alexander","family":"Zouros","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"b1-0080316","series-title":"Pediatr Neurol","doi-asserted-by":"publisher","first-page":"380","DOI":"10.1016\/0887-8994(86)90084-6","article-title":"Spinal cord involvement in encephalocraniocutaneous lipomatosis","volume":"2","author":"Alfonso","year":"1986"},{"key":"b2-0080316","series-title":"Cornea","doi-asserted-by":"publisher","first-page":"389","DOI":"10.1097\/00003226-200305000-00023","article-title":"Encephalocraniocutaneous lipomatosis: case report and review of the literature","volume":"22","author":"Almer","year":"2003"},{"key":"b3-0080316","series-title":"Spine (Phila Pa 1976)","doi-asserted-by":"publisher","first-page":"2505","DOI":"10.1097\/01.BRS.0000092381.05229.87","article-title":"Scoliosis associated with Chiari 1 malformations: the effect of suboccipital decompression on scoliosis curve progression: a preliminary study","volume":"28","author":"Brockmeyer","year":"2003"},{"key":"b4-0080316","series-title":"Spine (Phila Pa 1976)","doi-asserted-by":"publisher","first-page":"1775","DOI":"10.1097\/BRS.0b013e3181b07914","article-title":"Neurosurgical management of spinal dysraphism and neurogenic scoliosis","volume":"34","author":"Cardoso","year":"2009"},{"key":"b5-0080316","series-title":"Brain Dev","doi-asserted-by":"publisher","first-page":"355","DOI":"10.1016\/S0387-7604(01)00219-4","article-title":"Encephalocraniocutaneous lipomatosis associated with iris coloboma, chorioretinitis and spinal cord involvement: a case report","volume":"23","author":"Deda","year":"2001"},{"key":"b6-0080316","series-title":"J Child Neurol","doi-asserted-by":"publisher","first-page":"186","DOI":"10.1177\/088307388700200303","article-title":"Encephalocraniocutaneous lipomatosis","volume":"2","author":"Fishman","year":"1987"},{"key":"b7-0080316","series-title":"Neuroradiology","doi-asserted-by":"publisher","first-page":"175","DOI":"10.1007\/s002340100692","article-title":"Intracranial lipoma with extracranial extension through foramen ovale in a patient with encephalocraniocutaneous lipomatosis syndrome","volume":"44","author":"Fitoz","year":"2002"},{"key":"b8-0080316","series-title":"Pediatr Neurol","doi-asserted-by":"publisher","first-page":"207","DOI":"10.1016\/j.pediatrneurol.2008.05.017","article-title":"Sleep-disordered breathing in Chiari malformation type 1","volume":"39","author":"Gosalakkal","year":"2008"},{"key":"b9-0080316","series-title":"Arch Neurol","doi-asserted-by":"publisher","first-page":"144","DOI":"10.1001\/archneur.1970.00480200050005","article-title":"Encephalocraniocutaneous lipomatosis. 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