{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,11]],"date-time":"2026-05-11T23:32:00Z","timestamp":1778542320700,"version":"3.51.4"},"reference-count":11,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2013,7]]},"abstract":"<jats:p>In this paper the authors report the case of a complex dural arteriovenous fistula (dAVF) with high-risk features in a 14-year-old girl with Bannayan-Riley-Ruvalcaba syndrome (BRRS), a phosphatase and tensin homolog\u2013associated syndrome, presenting with signs and symptoms of increased intracranial pressure (ICP) that had previously been attributed to pseudotumor cerebri. This fistula was obliterated following 2 stages of embolization, and the patient experienced immediate symptomatic improvement. At the 2-month follow-up evaluation, the fistula remained angiographically occluded, and her symptoms continue to improve. This is the third reported case of an intracranial dAVF in a patient with BRRS. Because high-risk dAVFs can result in devastating morbidity, early detection with vascular imaging is crucial for patients with BRRS presenting with signs of increased ICP. Goals of treatment should include complete fistula obliteration whenever possible.<\/jats:p>","DOI":"10.3171\/2013.3.peds12551","type":"journal-article","created":{"date-parts":[[2013,5,10]],"date-time":"2013-05-10T14:09:22Z","timestamp":1368194962000},"page":"87-92","source":"Crossref","is-referenced-by-count":15,"title":["Complex dural arteriovenous fistula in Bannayan-Riley-Ruvalcaba syndrome"],"prefix":"10.3171","volume":"12","author":[{"given":"Karam","family":"Moon","sequence":"first","affiliation":[{"name":"Division of Neurological Surgery, Barrow Neurological Institute, St. Joseph's Hospital and Medical Center; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andrew F.","family":"Ducruet","sequence":"additional","affiliation":[{"name":"Division of Neurological Surgery, Barrow Neurological Institute, St. Joseph's Hospital and Medical Center; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"R. Webster","family":"Crowley","sequence":"additional","affiliation":[{"name":"Division of Neurological Surgery, Barrow Neurological Institute, St. Joseph's Hospital and Medical Center; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kathleen","family":"Klas","sequence":"additional","affiliation":[{"name":"Barrow Neurological Institute at Phoenix Children's Hospital, Phoenix, Arizona"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ruth","family":"Bristol","sequence":"additional","affiliation":[{"name":"Division of Neurological Surgery, Barrow Neurological Institute, St. Joseph's Hospital and Medical Center; and"},{"name":"Barrow Neurological Institute at Phoenix Children's Hospital, Phoenix, Arizona"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Felipe C.","family":"Albuquerque","sequence":"additional","affiliation":[{"name":"Division of Neurological Surgery, Barrow Neurological Institute, St. Joseph's Hospital and Medical Center; and"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"b1-peds12551","series-title":"Arch Pathol","first-page":"1","article-title":"Lipomatosis, angiomatosis, and macrencephalia: a previously undescribed congenital syndrome","volume":"92","author":"Bannayan","year":"1971"},{"key":"b2-peds12551","series-title":"Radiology","doi-asserted-by":"publisher","first-page":"671","DOI":"10.1148\/radiology.194.3.7862961","article-title":"Cerebral dural arteriovenous fistulas: clinical and angiographic correlation with a revised classification of venous drainage","volume":"194","author":"Cognard","year":"1995"},{"key":"b3-peds12551","series-title":"Genes Dev","doi-asserted-by":"publisher","first-page":"2054","DOI":"10.1101\/gad.1308805","article-title":"The PTEN\/PI3K pathway governs normal vascular development and tumor angiogenesis","volume":"19","author":"Hamada","year":"2005"},{"key":"b4-peds12551","series-title":"Interv Neuroradiol","doi-asserted-by":"publisher","first-page":"179","DOI":"10.1177\/159101999600200303","article-title":"Anatomoclinical aspects of dural arteriovenous shunts in children. 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