{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,18]],"date-time":"2026-08-18T04:02:09Z","timestamp":1787025729237,"version":"build-2736575974"},"reference-count":17,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"5","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2014,5]]},"abstract":"\n Object<\/jats:title>\n Unilateral fusion of the frontoparietal suture is the most common cause of synostotic frontal plagiocephaly. Localized fusion of the frontosphenoidal suture is rare but can lead to a similar, but subtly distinct, phenotype.<\/jats:p>\n <\/jats:sec>\n \n Methods<\/jats:title>\n A retrospective chart review of the authors' craniofacial database was performed. Patients with isolated frontosphenoidal synostosis on CT imaging were included. Demographic data, as well as the clinical and radiographic findings, were recorded.<\/jats:p>\n <\/jats:sec>\n \n Results<\/jats:title>\n Three patients were identified. All patients were female and none had an identifiable syndrome. Head circumference was normal in each patient. The mean age at presentation was 4.8 months (range 2.0\u20139.8 months); 2 fusions were on the right side. Frontal flattening and recession of the supraorbital rim on the fused side were consistent physical findings. No patient had appreciable facial angulation or orbital dystopia, and 2 patients had anterior displacement of the ipsilateral ear. All 3 patients were initially misdiagnosed with unilateral coronal synostosis, and CT imaging at a mean age of 5.4 months (range 2.1\u201310.8 months) was required to secure the correct diagnosis. Computed tomography findings included patency of the frontoparietal suture, minor to no anterior cranial base angulation, and vertical flattening of the orbit without sphenoid wing elevation on the fused side. One patient underwent CT scanning at 2.1 months of age, which demonstrated a narrow, but patent, frontosphenoidal suture. The patient's condition was assumed to be a deformational process, and she underwent 6 months of unsuccessful helmet therapy. A repeat CT scan obtained at 10.7 months of age demonstrated the synostosis. All 3 patients underwent fronto-orbital correction at mean age of 12.1 months (range 7.8\u201316.1 months). The mean duration of postoperative follow-up was 11.7 months (range 1.9\u201323.9 months).<\/jats:p>\n <\/jats:sec>\n \n Conclusions<\/jats:title>\n Isolated frontosphenoidal synostosis should be considered in the differential diagnosis of atypical frontal plagiocephaly.<\/jats:p>\n <\/jats:sec>","DOI":"10.3171\/2014.1.peds1378","type":"journal-article","created":{"date-parts":[[2014,3,7]],"date-time":"2014-03-07T09:58:54Z","timestamp":1394186334000},"page":"553-558","source":"Crossref","is-referenced-by-count":27,"title":["Isolated frontosphenoidal synostosis: a rare cause of synostotic frontal plagiocephaly"],"prefix":"10.3171","volume":"13","author":[{"given":"Tina M.","family":"Sauerhammer","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Albert K.","family":"Oh","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael","family":"Boyajian","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Suresh N.","family":"Magge","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John S.","family":"Myseros","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robert F.","family":"Keating","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gary F.","family":"Rogers","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1754","reference":[{"issue":"Suppl 51","key":"b1-peds1378","series-title":"Acta Ophthalmol Suppl","first-page":"1","article-title":"The premature synostosis of the cranial sutures","volume":"36","author":"Bertelsen","year":"1958"},{"key":"b2-peds1378","series-title":"Cleft Palate J","first-page":"28","article-title":"The natural history and pathogenesis of the cranial coronal ring articulations: implications in understanding the pathogenesis of the Crouzon craniostenotic defects","volume":"23","author":"Burdi","year":"1986"},{"key":"b3-peds1378","series-title":"AJNR Am J Neuroradiol","first-page":"643","article-title":"Premature closure of the frontozygomatic suture: unusual frontoorbital dysplasia mimicking unilateral coronal synostosis","volume":"6","author":"Currarino","year":"1985"},{"key":"b4-peds1378","series-title":"Childs Nerv Syst","doi-asserted-by":"publisher","first-page":"1431","DOI":"10.1007\/s00381-007-0469-4","article-title":"Frontosphenoidal synostosis: a rare cause of unilateral anterior plagiocephaly","volume":"23","author":"de Ribaupierre","year":"2007"},{"key":"b5-peds1378","series-title":"Plast Reconstr Surg","doi-asserted-by":"publisher","first-page":"1695","DOI":"10.1097\/01.PRS.0000142474.25114.CB","article-title":"Coronal ring involvement in patients treated for unilateral coronal craniosynostosis","volume":"114","author":"Dundulis","year":"2004"},{"key":"b6-peds1378","series-title":"J Neurosurg","doi-asserted-by":"publisher","first-page":"733","DOI":"10.3171\/jns.1995.83.4.0733","article-title":"Frontal plagiocephaly secondary to synostosis of the frontosphenoidal suture. Case report","volume":"83","author":"Francel","year":"1995"},{"key":"b7-peds1378","series-title":"J Plast Reconstr Aesthet Surg","doi-asserted-by":"publisher","first-page":"e255","DOI":"10.1016\/j.bjps.2007.12.016","article-title":"Unilateral isolated frontosphenoidal craniosynostosis causing frontal plagiocephaly","volume":"62","author":"Marucci","year":"2009"},{"key":"b8-peds1378","series-title":"Pediatr Radiol","doi-asserted-by":"publisher","first-page":"431","DOI":"10.1007\/s00247-008-0750-z","article-title":"The frontosphenoidal suture: fetal development and phenotype of its synostosis","volume":"38","author":"Mathijssen","year":"2008"},{"key":"b9-peds1378","series-title":"Plast Reconstr Surg","doi-asserted-by":"publisher","first-page":"700","DOI":"10.1097\/00006534-199604000-00002","article-title":"The concept of the sagittal orbital-globe relationship in craniofacial surgery","volume":"97","author":"Mulliken","year":"1996"},{"key":"b10-peds1378","series-title":"Plast Reconstr Surg","doi-asserted-by":"publisher","first-page":"1341","DOI":"10.1097\/00006534-199904020-00001","article-title":"Prospective anthropometric analysis of sagittal orbital-globe relationship following fronto-orbital advancement in childhood","volume":"103","author":"Pai","year":"1999"},{"key":"b11-peds1378","series-title":"J Craniomaxillofac Surg","doi-asserted-by":"publisher","first-page":"162","DOI":"10.1016\/j.jcms.2008.10.005","article-title":"Unilateral craniosynostosis of the frontosphenoidal suture: a case report and a review of literature","volume":"37","author":"Plooij","year":"2009"},{"key":"b12-peds1378","series-title":"Plast Reconstr Surg","doi-asserted-by":"publisher","first-page":"1887","DOI":"10.1097\/01.PRS.0000165073.64309.BD","article-title":"Involvement of the basilar coronal ring in unilateral coronal synostosis","volume":"115","author":"Rogers","year":"2005"},{"key":"b13-peds1378","series-title":"Plast Reconstr Surg","first-page":"1011","article-title":"Unilateral fusion of the frontosphenoidal suture: a rare cause of synostotic frontal plagiocephaly","volume":"110","author":"Rogers","year":"2002"},{"key":"b14-peds1378","series-title":"J Craniofac Surg","doi-asserted-by":"publisher","first-page":"1267","DOI":"10.1097\/SCS.0b013e3182519a97","article-title":"Involvement of the sphenosquamosal suture for unilateral coronal synostosis","volume":"23","author":"Sakamoto","year":"2012"},{"key":"b15-peds1378","series-title":"Radiology","doi-asserted-by":"publisher","first-page":"631","DOI":"10.1148\/101.3.631","article-title":"Premature closure of the frontosphenoidal suture in synostosis of the coronal suture","volume":"101","author":"Seeger","year":"1971"},{"key":"b16-peds1378","series-title":"Pediatrics","doi-asserted-by":"publisher","first-page":"829","DOI":"10.1542\/peds.41.4.829","article-title":"Craniosynostosis: a review of 519 surgical patients","volume":"41","author":"Shillito","year":"1968"},{"key":"b17-peds1378","series-title":"Plast Reconstr Surg","doi-asserted-by":"publisher","first-page":"165","DOI":"10.1097\/PRS.0b013e318254b271","article-title":"Squamosal suture synostosis: a cause of atypical skull asymmetry","volume":"130","author":"Smartt","year":"2012"}],"container-title":["Journal of Neurosurgery: Pediatrics"],"original-title":[],"link":[{"URL":"https:\/\/thejns.org\/view\/journals\/j-neurosurg-pediatr\/13\/5\/article-p553.xml","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/thejns.org\/downloadpdf\/journals\/j-neurosurg-pediatr\/13\/5\/article-p553.xml","content-type":"text\/html","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/thejns.org\/downloadpdf\/journals\/j-neurosurg-pediatr\/13\/5\/article-p553.xml","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,4,15]],"date-time":"2023-04-15T10:16:47Z","timestamp":1681553807000},"score":1,"resource":{"primary":{"URL":"https:\/\/thejns.org\/view\/journals\/j-neurosurg-pediatr\/13\/5\/article-p553.xml"}},"subtitle":["Clinical article"],"short-title":[],"issued":{"date-parts":[[2014,5]]},"references-count":17,"journal-issue":{"issue":"5"},"URL":"https:\/\/doi.org\/10.3171\/2014.1.peds1378","relation":{},"ISSN":["1933-0707","1933-0715"],"issn-type":[{"value":"1933-0707","type":"print"},{"value":"1933-0715","type":"electronic"}],"subject":[],"published":{"date-parts":[[2014,5]]}}}