{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,18]],"date-time":"2026-08-18T04:02:08Z","timestamp":1787025728983,"version":"build-2736575974"},"reference-count":27,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"6","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2014,6]]},"abstract":"<jats:p>\n                    Currarino syndrome is a rare constellation of congenital anomalies characterized by the triad of sacral dysgenesis, presacral mass, and anorectal malformation. It is frequently associated with other congenital anomalies, often including occult spinal dysraphism. Mutations in the\n                    <jats:italic>MNX1<\/jats:italic>\n                    gene are identified in the majority of cases. The authors report a rare case of Currarino syndrome in an infant with tethered cord syndrome and a dorsal lipomyelomeningocele continuous with a presacral intradural spinal lipoma, in addition to an imperforate anus and a scimitar sacrum. They review the literature to highlight patterns of occult spinal dysraphism in patients with Currarino syndrome and their relationship to tethered cord syndrome. Approximately 60% of the patients with Currarino syndrome reported in the literature have an occult spinal dysraphism. Published studies suggest that the risk of tethered cord syndrome may be higher among patients with a lipoma and lower among those with a teratoma or anterior meningocele.\n                  <\/jats:p>","DOI":"10.3171\/2014.3.peds13534","type":"journal-article","created":{"date-parts":[[2014,4,18]],"date-time":"2014-04-18T10:28:22Z","timestamp":1397816902000},"page":"685-689","source":"Crossref","is-referenced-by-count":33,"title":["Currarino syndrome and spinal dysraphism"],"prefix":"10.3171","volume":"13","author":[{"given":"Matthew J.","family":"Kole","sequence":"first","affiliation":[{"name":"Department of Neurosurgery, Baylor College of Medicine;"},{"name":"Division of Pediatric Neurosurgery, Texas Children's Hospital, Houston, Texas;"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jared S.","family":"Fridley","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Baylor College of Medicine;"},{"name":"Division of Pediatric Neurosurgery, Texas Children's Hospital, Houston, Texas;"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andrew","family":"Jea","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Baylor College of Medicine;"},{"name":"Division of Pediatric Neurosurgery, Texas Children's Hospital, Houston, Texas;"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robert J.","family":"Bollo","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Baylor College of Medicine;"},{"name":"Division of Pediatric Neurosurgery, Texas Children's Hospital, Houston, Texas;"},{"name":"Department of Neurosurgery, University of Utah School of Medicine; and"},{"name":"Division of Pediatric Neurosurgery, Primary Children's Medical Center, Salt Lake City, Utah"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1754","reference":[{"key":"b1-peds13534","series-title":"Colorectal 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