{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,11,10]],"date-time":"2026-11-10T15:26:00Z","timestamp":1794324360474,"version":"4.9.0"},"reference-count":14,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2016,9]]},"abstract":"<jats:p>Hemiconvulsion-hemiplegia-epilepsy (HHE) is an uncommon epileptic syndrome that affects young children. Typical management includes early initiation of benzodiazepines to abate the initial seizure activity quickly. Patients in whom epilepsy develops require prolonged use of antiepileptic agents. Herniation due to diffuse cerebral edema from HHE is rare; however, decompressive craniectomy has been described as a lifesaving measure. The authors present the case of a patient in whom a decompressive craniectomy was performed. They advocate a proactive approach in the detection and management of cerebral edema in HHE causing intracranial hypertension. In HHE cases that exhibit radiographic evidence of malignant cerebral edema (although not previously described in this disease, but similar to the setting of stroke and trauma), the authors advocate early neurosurgical consultation and evaluation for insertion of an intracranial pressure monitor for those patients who do not have a reliable neurological examination (i.e., Glasgow Coma Scale score \u2264 8).<\/jats:p>","DOI":"10.3171\/2016.3.peds15677","type":"journal-article","created":{"date-parts":[[2016,5,13]],"date-time":"2016-05-13T11:00:30Z","timestamp":1463137230000},"page":"344-349","source":"Crossref","is-referenced-by-count":1,"title":["Survival following decompressive hemicraniectomy for hemiconvulsion-hemiplegia-epilepsy syndrome: case report"],"prefix":"10.3171","volume":"18","author":[{"given":"Alexandra D.","family":"Beier","sequence":"first","affiliation":[{"name":"Division of Pediatric Neurosurgery, University of Florida Health;"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gemi E.","family":"Jannotta","sequence":"additional","affiliation":[{"name":"Division of Pediatric Neurosurgery, University of Florida Health;"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"E. Dayan","family":"Sandler","sequence":"additional","affiliation":[{"name":"Jacksonville Pathology Consultants, Chief of Pathology; and"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Harry S.","family":"Abram","sequence":"additional","affiliation":[{"name":"Department of Neurology, Nemours Children's Specialty Care, Jacksonville, Florida"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Raj D.","family":"Sheth","sequence":"additional","affiliation":[{"name":"Department of Neurology, Nemours Children's Specialty Care, Jacksonville, Florida"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Philipp R.","family":"Aldana","sequence":"additional","affiliation":[{"name":"Division of Pediatric Neurosurgery, University of Florida Health;"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1754","reference":[{"key":"b1-peds15677","series-title":"Curr Treat Options Neurol","doi-asserted-by":"publisher","first-page":"262","DOI":"10.1007\/s11940-009-0030-8","article-title":"Convulsive and nonconvulsive status epilepticus in children","volume":"11","author":"Abend","year":"2009"},{"key":"b2-peds15677","series-title":"Eur J Paediatr Neurol","doi-asserted-by":"publisher","first-page":"413","DOI":"10.1016\/j.ejpn.2012.01.007","article-title":"Hemiconvulsion-hemiplegia-epilepsy syndrome: current understandings","volume":"16","author":"Auvin","year":"2012"},{"key":"b3-peds15677","series-title":"Clin Neurol Neurosurg","doi-asserted-by":"publisher","first-page":"914","DOI":"10.1016\/j.clineuro.2007.07.027","article-title":"Decompressive hemicraniectomy in a space-occupying presentation of hemiconvulsion-hemiplegia-epilepsy syndrome","volume":"109","author":"Berhouma","year":"2007"},{"key":"b4-peds15677","series-title":"J Neurotrauma","doi-asserted-by":"publisher","first-page":"479","DOI":"10.1089\/neu.2000.17.479","article-title":"Guidelines for the management of severe head injury. 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