{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,3,19]],"date-time":"2025-03-19T14:13:44Z","timestamp":1742393624689},"reference-count":24,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2019,3]]},"abstract":"<jats:p>Pediatric hydrocephalus is a well-studied and still incompletely understood entity. One of the physiological means by which hydrocephalus and intracranial hypertension evolve is through perturbations to normal vascular dynamics. Here the authors report a unique case of an extracranial vascular anomaly resulting in persistently elevated intracranial pressures (ICPs) independent of CSF diversion in a patient with a Joubert syndrome\u2013related disorder. The patient developed worsening intracranial hypertension after successful CSF diversion of Dandy-Walker malformation\u2013associated hydrocephalus via endoscopic third ventriculostomy\u2013choroid plexus cauterization (ETV\/CPC). Vascular workup and imaging revealed an extracranial arteriovenous fistula of the superficial temporal artery at the site of a prior scalp intravenous catheter. Following microsurgical obliteration of the lesion, ICP normalized from &gt; 30 cm H<jats:sub>2<\/jats:sub>O preoperatively to 11 cm H<jats:sub>2<\/jats:sub>O postoperatively. A repeat lumbar puncture at 4 months postoperatively again demonstrated normal pressure, and the patient remained asymptomatic for 9 months. Recurrent symptoms at 9 months were attributed to inadequate CSF diversion, and the patient underwent ventriculoperitoneal shunt placement. This is the first report of an extracranial-to-extracranial vascular anastomosis resulting in intracranial hypertension. This case report demonstrates the need to consider extracranial vascular anomalies as potential sources of persistently elevated ICP in the syndromic pediatric population.<\/jats:p>","DOI":"10.3171\/2018.10.peds18235","type":"journal-article","created":{"date-parts":[[2019,2,27]],"date-time":"2019-02-27T00:51:48Z","timestamp":1551228708000},"page":"369-373","source":"Crossref","is-referenced-by-count":2,"title":["Reversible intracranial hypertension following treatment of an extracranial vascular malformation: case report"],"prefix":"10.3171","volume":"23","author":[{"given":"Katie","family":"Pricola Fehnel","sequence":"first","affiliation":[{"name":"Vascular Biology Program,"},{"name":"Department of Neurosurgery, and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jennifer","family":"Klein","sequence":"additional","affiliation":[{"name":"Vascular Biology Program,"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Benjamin C.","family":"Warf","sequence":"additional","affiliation":[{"name":"Vascular Biology Program,"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Edward R.","family":"Smith","sequence":"additional","affiliation":[{"name":"Vascular Biology Program,"},{"name":"Department of Neurosurgery, and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Darren B.","family":"Orbach","sequence":"additional","affiliation":[{"name":"Neurointerventional Radiology, Boston Children\u2019s Hospital, Boston, Massachusetts"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"b1","series-title":"J Neurosurg Pediatr","doi-asserted-by":"publisher","first-page":"125","DOI":"10.3171\/2013.10.PEDS13343","article-title":"Hemodynamically significant venous collapse underlying neonatal hydrocephalus","volume":"13","author":"Bateman GA","year":"2014","unstructured":"Bateman GA: Hemodynamically significant venous collapse underlying neonatal hydrocephalus. 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