{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,5,30]],"date-time":"2022-05-30T07:40:03Z","timestamp":1653896403238},"reference-count":40,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"4","license":[{"start":{"date-parts":[[2021,1,25]],"date-time":"2021-01-25T00:00:00Z","timestamp":1611532800000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2021,1,25]]},"abstract":"<jats:sec><jats:title>BACKGROUND<\/jats:title><jats:p>Camurati-Engelmann disease (CED) is a rare condition characterized by hyperostosis of the long bones and skull base. Symptoms include contractures and pain in affected extremities but can also include manifestations of cranial hyperostosis such as intracranial hypertension, Chiari malformation, exophthalmia, frontal bossing, and several cranial neuropathies due to cranial foraminal stenosis.<\/jats:p><\/jats:sec><jats:sec><jats:title>OBSERVATIONS<\/jats:title><jats:p>This report describes a 27-year-old patient with suspected CED who developed progressive intermittent facial nerve paresis, hemifacial spasms, and a decrease in hearing. There were no symptoms of increased intracranial pressure or vertigo. Radiological evaluation showed a significant thickening of the skull base with serious bilateral internal auditory canal stenosis. Because of the progressive nature of the aforementioned cranial neuropathies in combination with the correlating severe radiological compression, a surgical decompression of the facial nerve and vestibulocochlear nerve was performed via a retrosigmoid approach with intraoperative monitoring. Postoperative facial nerve function was intact. Hearing and vestibular function were unchanged. There were no more episodes of facial nerve palsy or spasm.<\/jats:p><\/jats:sec><jats:sec><jats:title>LESSONS<\/jats:title><jats:p>To the authors\u2019 knowledge, this is the first report to describe decompression of the internal auditory canal via a retrosigmoid approach for symptomatic facial and cochlear nerve compression in a patient with CED.<\/jats:p><\/jats:sec>","DOI":"10.3171\/case2039","type":"journal-article","created":{"date-parts":[[2021,1,29]],"date-time":"2021-01-29T20:32:18Z","timestamp":1611952338000},"source":"Crossref","is-referenced-by-count":0,"title":["Decompression of the internal auditory canal via the retrosigmoid approach in a patient with Camurati-Engelmann disease: illustrative case"],"prefix":"10.3171","volume":"1","author":[{"given":"Salah-Eddine","family":"Achahbar","sequence":"first","affiliation":[{"name":"Department of Neurosurgery, University Hospital Antwerp, Edegem, Antwerp, Belgium; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas","family":"Somers","sequence":"additional","affiliation":[{"name":"Departments of Otorhinolaryngology and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tony","family":"Van Havenbergh","sequence":"additional","affiliation":[{"name":"Neurosurgery, GZA Sint-Augustinus Hospital, Wilrijk, Antwerp, Belgium"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"ref281","doi-asserted-by":"crossref","first-page":"566","DOI":"10.1001\/archoto.2010.68","article-title":"Skull base manifestations of Camurati-Engelmann disease","volume":"136","author":"Carlson","year":"2010","journal-title":"Arch Otolaryngol Head Neck Surg"},{"key":"ref201","doi-asserted-by":"crossref","first-page":"48","DOI":"10.1016\/j.bone.2013.12.003","article-title":"Sclerosing bone dysplasias with involvement of the craniofacial skeleton","volume":"60","author":"Waterval","year":"2014","journal-title":"Bone"},{"key":"ref361","doi-asserted-by":"crossref","first-page":"1004","DOI":"10.1016\/j.otohns.2004.02.029","article-title":"Internal auditory canal decompression and cochlear implantation in Camurati-Engelmann disease","volume":"131","author":"Tibesar","year":"2004","journal-title":"Otolaryngol Head Neck Surg"},{"key":"ref151","doi-asserted-by":"crossref","first-page":"210","DOI":"10.1001\/archotol.1980.00790280018002","article-title":"Neurotologic manifestations of the osteopetroses","volume":"106","author":"Miyamoto","year":"1980","journal-title":"Arch Otolaryngol"},{"key":"ref371","doi-asserted-by":"crossref","first-page":"462","DOI":"10.1017\/S0022215100133985","article-title":"Vestibular nerve dysfunction and decompression in Engelmann\u2019s disease","volume":"110","author":"Hellier","year":"1996","journal-title":"J Laryngol Otol"},{"key":"ref251","doi-asserted-by":"crossref","first-page":"3","DOI":"10.1016\/j.mce.2015.12.021","article-title":"Genetic control of bone mass","volume":"432","author":"Boudin","year":"2016","journal-title":"Mol Cell Endocrinol"},{"key":"ref311","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1080\/17843286.1998.11754162","article-title":"Camurati-Engelmann disease. 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