{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,29]],"date-time":"2026-01-29T22:36:30Z","timestamp":1769726190498,"version":"3.49.0"},"reference-count":56,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"14","license":[{"start":{"date-parts":[[2025,10,6]],"date-time":"2025-10-06T00:00:00Z","timestamp":1759708800000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J Neurosurg Case Lessons"],"published-print":{"date-parts":[[2025,10,6]]},"abstract":"\n BACKGROUND<\/jats:title>\n \n Epithelioid hemangioendothelioma (EHE) is a rare vascular tumor with intermediate malignant potential.\n TFE3<\/jats:italic>\n -rearranged intracerebral EHEs (iEHEs) have not been reported to date. Herein, the authors describe a rare case of recurrent multiple\n TFE3<\/jats:italic>\n -rearranged iEHEs involving the lung and liver, which exhibited a favorable clinical course after repeated surgeries, radiation therapy, and active surveillance.\n <\/jats:p>\n <\/jats:sec>\n \n OBSERVATIONS<\/jats:title>\n \n A 20-year-old man presented with multiple pulmonary, hepatic, and intracerebral lesions. The patient was diagnosed with EHE via biopsy of pulmonary lesions. During follow-up without treatment, progressive perilesional edema was observed in the left temporal lobe, leading to resection. Histological findings were consistent with EHE, and immunohistochemical analysis revealed overexpression of TFE3 in the tumor cells. Hence, a diagnosis of\n TFE3<\/jats:italic>\n -rearranged iEHE was established. Immediately after detecting progressive lesions, the patient received multiple interventions including surgery and radiation therapy. Radiological findings revealed multiple cystic lesions with hemorrhagic components. The tumor has been successfully controlled for 13 years with repeated surgeries, radiation therapy, and active surveillance.\n <\/jats:p>\n <\/jats:sec>\n \n LESSONS<\/jats:title>\n \n TFE3<\/jats:italic>\n -rearranged iEHE is an extremely rare type of tumor and can present with multiple cystic lesions containing hemorrhagic components on imaging.\n TFE3<\/jats:italic>\n -rearranged iEHE can be successfully managed with repeated intervention and active surveillance.\n <\/jats:p>\n \n https:\/\/thejns.org\/doi\/10.3171\/CASE25416<\/jats:ext-link>\n <\/jats:p>\n <\/jats:sec>","DOI":"10.3171\/case25416","type":"journal-article","created":{"date-parts":[[2025,10,7]],"date-time":"2025-10-07T00:02:40Z","timestamp":1759795360000},"source":"Crossref","is-referenced-by-count":0,"title":["Successful management of recurrent multiple intracerebral TFE3-rearranged epithelioid hemangioendothelioma with repeated intervention and active surveillance: illustrative case"],"prefix":"10.3171","volume":"10","author":[{"given":"Yasuzumi","family":"Matsui","sequence":"first","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shigeki","family":"Takada","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"},{"name":"Regulatory Science of Medical Device Development and Innovation, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1262-2355","authenticated-orcid":true,"given":"Yasuhide","family":"Takeuchi","sequence":"additional","affiliation":[{"name":"Department of Diagnostic Pathology, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shinya","family":"Tokunaga","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2975-774X","authenticated-orcid":true,"given":"Etsuko Yamamoto","family":"Hattori","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5710-7456","authenticated-orcid":true,"given":"Hiroyuki","family":"Ikeda","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8999-1976","authenticated-orcid":true,"given":"Noritaka","family":"Sano","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Masahiro","family":"Tanji","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"},{"name":"Regulatory Science of Medical Device Development and Innovation, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yohei","family":"Mineharu","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4626-4645","authenticated-orcid":true,"given":"Yoshiki","family":"Arakawa","sequence":"additional","affiliation":[{"name":"Department of Neurosurgery, Kyoto University Graduate School of Medicine, Kyoto, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"issue":"5","key":"bib1","series-title":"Cancer","first-page":"970","article-title":"Epithelioid hemangioendothelioma: a vascular tumor often mistaken for a carcinoma","volume":"50","author":"Weiss","year":"1982","unstructured":"Weiss SWEnzinger FM.Epithelioid hemangioendothelioma: a vascular tumor often mistaken for a carcinoma. Cancer. 1982;50(5):970-981."},{"issue":"2","key":"bib2","series-title":"Oncol Rev","first-page":"259","article-title":"Epithelioid hemangioendothelioma: an overview and update on a rare vascular tumor","volume":"8","author":"Sardaro","year":"2014","unstructured":"Sardaro ABardoscia LPetruzzelli MFPortaluri M.Epithelioid hemangioendothelioma: an overview and update on a rare vascular tumor. Oncol Rev. 2014;8(2):259."},{"issue":"4","key":"bib3","series-title":"Semin Diagn Pathol","first-page":"259","article-title":"Epithelioid hemangioendothelioma and related lesions","volume":"3","author":"Weiss","year":"1986","unstructured":"Weiss SWIshak KGDail DHSweet DEEnzinger FM.Epithelioid hemangioendothelioma and related lesions. Semin Diagn Pathol. 1986;3(4):259-287."},{"issue":"3","key":"bib4","series-title":"Acta Clin Croat","first-page":"570","article-title":"Primary epithelioid hemangioendothelioma in the cerebellum: case report with reference to drastic change in the who classification","volume":"57","author":"Omerhod\u017ei\u0107","year":"2018","unstructured":"Omerhod\u017ei\u0107 IBilalovi\u0107 NRov\u010danin BPrimary epithelioid hemangioendothelioma in the cerebellum: case report with reference to drastic change in the who classification. Acta Clin Croat. 2018;57(3):570-576."},{"issue":"7","key":"bib5","series-title":"Jpn J Clin Oncol","first-page":"739","article-title":"Epithelioid hemangioendothelioma\u2014its history, clinical features, molecular biology and current therapy","volume":"54","author":"Tsuchihashi","year":"2024","unstructured":"Tsuchihashi KBaba E.Epithelioid hemangioendothelioma\u2014its history, clinical features, molecular biology and current therapy. Jpn J Clin Oncol. 2024;54(7):739-747."},{"key":"bib6","series-title":"Eur J Cancer","first-page":"113262","article-title":"Epithelioid hemangio-endothelioma (EHE) in NETSARC: the nationwide series of 267 patients over 12 years","volume":"192","author":"Blay","year":"2023","unstructured":"Blay JYPiperno-Neumann SWatson SEpithelioid hemangio-endothelioma (EHE) in NETSARC: the nationwide series of 267 patients over 12 years. Eur J Cancer. 2023;192:113262."},{"key":"bib7","series-title":"J Oncol","first-page":"2349991","article-title":"Epithelioid hemangioendothelioma: incidence, mortality, prognostic factors, and survival analysis using the surveillance, epidemiology, and end results database","volume":"2022","author":"Liu","year":"2022","unstructured":"Liu ZHe S.Epithelioid hemangioendothelioma: incidence, mortality, prognostic factors, and survival analysis using the surveillance, epidemiology, and end results database. J Oncol. 2022;2022:2349991."},{"issue":"6","key":"bib8","series-title":"Am J Surg Pathol","first-page":"619","article-title":"Epithelioid hemangioendothelioma of the brain","volume":"16","author":"Chow","year":"1992","unstructured":"Chow LTChow WHFong DT.Epithelioid hemangioendothelioma of the brain. Am J Surg Pathol. 1992;16(6):619-625."},{"issue":"5","key":"bib9","series-title":"Neuropathology","first-page":"338","article-title":"Hemorrhage from metastatic brain epithelioid hemangioendothelioma: a case report","volume":"44","author":"Fusegawa","year":"2024","unstructured":"Fusegawa TTomita TOkuno NAkai TKuroda S.Hemorrhage from metastatic brain epithelioid hemangioendothelioma: a case report. Neuropathology. 2024;44(5):338-343."},{"issue":"3","key":"bib10","series-title":"Neuropathology","first-page":"201","article-title":"Aggressive intracranial and extra-cranial epithelioid hemangioendothelioma: a case report and review of the literature","volume":"26","author":"Fernandes","year":"2006","unstructured":"Fernandes ALRatilal BMafra MMagalhaes C.Aggressive intracranial and extra-cranial epithelioid hemangioendothelioma: a case report and review of the literature. Neuropathology. 2006;26(3):201-205."},{"issue":"3","key":"bib11","series-title":"Eur Respir J","first-page":"483","article-title":"Central nervous system metastases of a pulmonary epitheloid haemangioendothelioma","volume":"23","author":"D\u00edaz","year":"2004","unstructured":"D\u00edaz RSegura ACalderero VCentral nervous system metastases of a pulmonary epitheloid haemangioendothelioma. Eur Respir J. 2004;23(3):483-486."},{"issue":"suppl 23","key":"bib12","series-title":"Surg Neurol Int","first-page":"S596","article-title":"Suprasellar epithelioid hemangioendothelioma: case report and review of the literature","volume":"7","author":"Barger","year":"2016","unstructured":"Barger JTanweer OLiechty BSnuderl MJafar JJ.Suprasellar epithelioid hemangioendothelioma: case report and review of the literature. Surg Neurol Int. 2016;7(suppl 23):S596-S602."},{"issue":"3","key":"bib13","series-title":"J Neurooncol","first-page":"337","article-title":"Malignant intracranial epithelioid hemangioendothelioma presumably originating from the lung: case report","volume":"67","author":"Endo","year":"2004","unstructured":"Endo TSu CCNumagami YShirane R.Malignant intracranial epithelioid hemangioendothelioma presumably originating from the lung: case report. J Neurooncol. 2004;67(3):337-343."},{"issue":"4","key":"bib14","series-title":"Mod Pathol","first-page":"591","article-title":"Prognostic stratification of clinical and molecular epithelioid hemangioendothelioma subsets","volume":"33","author":"Rosenbaum","year":"2020","unstructured":"Rosenbaum EJadeja BXu BPrognostic stratification of clinical and molecular epithelioid hemangioendothelioma subsets. Mod Pathol. 2020;33(4):591-602."},{"issue":"3","key":"bib15","series-title":"ESMO Open","first-page":"100170","article-title":"Epithelioid hemangioendothelioma, an ultra-rare cancer: a consensus paper from the community of experts","volume":"6","author":"Stacchiotti","year":"2021","unstructured":"Stacchiotti SMiah ABFrezza AMEpithelioid hemangioendothelioma, an ultra-rare cancer: a consensus paper from the community of experts. ESMO Open. 2021;6(3):100170."},{"issue":"1","key":"bib16","series-title":"BMC Cancer","first-page":"993","article-title":"Clinical characteristics of Japanese patients with epithelioid hemangioendothelioma: a multicenter retrospective study","volume":"18","author":"Shiba","year":"2018","unstructured":"Shiba SImaoka HShioji KClinical characteristics of Japanese patients with epithelioid hemangioendothelioma: a multicenter retrospective study. BMC Cancer. 2018;18(1):993."},{"issue":"12","key":"bib17","series-title":"Mod Pathol","first-page":"2211","article-title":"YAP1-TFE3-fused hemangioendothelioma: a multi-institutional clinicopathologic study of 24 genetically-confirmed cases","volume":"34","author":"Dermawan","year":"2021","unstructured":"Dermawan JKAzzato EMBillings SDYAP1-TFE3-fused hemangioendothelioma: a multi-institutional clinicopathologic study of 24 genetically-confirmed cases. Mod Pathol. 2021;34(12):2211-2221."},{"issue":"8","key":"bib18","series-title":"Genes Chromosomes Cancer","first-page":"775","article-title":"Novel YAP1-TFE3 fusion defines a distinct subset of epithelioid hemangioendothelioma","volume":"52","author":"Antonescu","year":"2013","unstructured":"Antonescu CRLe Loarer FMosquera JMNovel YAP1-TFE3 fusion defines a distinct subset of epithelioid hemangioendothelioma. Genes Chromosomes Cancer. 2013;52(8):775-784."},{"key":"bib19","series-title":"Surg Neurol Int","first-page":"156","article-title":"Multiple hemorrhagic intraparenchymal tumors presenting with fatal intracranial hypertension: a rare manifestation of systemic epithelioid hemangioendothelioma","volume":"6","author":"Tsuchiya","year":"2015","unstructured":"Tsuchiya TOya SMori HMatsui T.Multiple hemorrhagic intraparenchymal tumors presenting with fatal intracranial hypertension: a rare manifestation of systemic epithelioid hemangioendothelioma. Surg Neurol Int. 2015;6:156."},{"issue":"2","key":"bib20","series-title":"Neurosurgery","first-page":"410","article-title":"Pediatric intracranial hemangioendotheliomas: case report","volume":"40","author":"Chen","year":"1997","unstructured":"Chen TCGonzalez-Gomez IGilles FHMcComb JG.Pediatric intracranial hemangioendotheliomas: case report. Neurosurgery. 1997;40(2):410-414."},{"issue":"8","key":"bib21","series-title":"Arq Neuro Psiquiatr","first-page":"637","article-title":"Cerebral epithelioid hemangioendothelioma with thoracic simultaneous involvement: advanced MRI features","volume":"70","author":"Rocha Oliveira","year":"2012","unstructured":"Rocha Oliveira PCAlcantara FPSouza-Vianna PEBrito AP.Cerebral epithelioid hemangioendothelioma with thoracic simultaneous involvement: advanced MRI features. Arq Neuro Psiquiatr. 2012;70(8):637-638."},{"issue":"1","key":"bib22","series-title":"J Neurooncol","first-page":"119","article-title":"Primary intracranial epithelioid hemangioendothelioma: a low-proliferation tumor exhibiting clinically malignant behavior","volume":"110","author":"Zheng","year":"2012","unstructured":"Zheng JLiu LWang JWang SCao YZhao J.Primary intracranial epithelioid hemangioendothelioma: a low-proliferation tumor exhibiting clinically malignant behavior. J Neurooncol. 2012;110(1):119-127."},{"issue":"7","key":"bib23","series-title":"Int J Surg Pathol","first-page":"1694","article-title":"A lung epithelioid hemangioendothelioma subtype with YAP1::TFE3 fusion: a case report","volume":"33","author":"Xiao","year":"2025","unstructured":"Xiao CXu WShen MCao DLv J.A lung epithelioid hemangioendothelioma subtype with YAP1::TFE3 fusion: a case report. Int J Surg Pathol. 2025;33(7):1694-1699."},{"key":"bib24","series-title":"Front Oncol","first-page":"1478036","article-title":"CAMTA1-immunonegative epithelioid hemangioendotheliomas of the liver: a clinicopathological and molecular analysis of seven cases","volume":"15","author":"Nie","year":"2025","unstructured":"Nie YJing WZheng XHe XChen MZhang H.CAMTA1-immunonegative epithelioid hemangioendotheliomas of the liver: a clinicopathological and molecular analysis of seven cases. Front Oncol. 2025;15:1478036."},{"key":"bib25","series-title":"Front Oncol","first-page":"1442233","article-title":"Hepatic epithelioid hemangioendothelioma with TFE3 rearrangement: a case report and literature review","volume":"15","author":"Meng","year":"2025","unstructured":"Meng KYang XGuo STao J.Hepatic epithelioid hemangioendothelioma with TFE3 rearrangement: a case report and literature review. Front Oncol. 2025;15:1442233."},{"key":"bib26","series-title":"World Health Organization Classification of Soft Tissue and Bone Tumours","author":"WHO Classification of Tumours Editorial Board","year":"2020","unstructured":"WHO Classification of Tumours Editorial BoardWorld Health Organization Classification of Soft Tissue and Bone Tumours. 5th ed. IARC Press; 2020."},{"key":"bib27","series-title":"Case Rep Neurol Med","first-page":"396097","article-title":"A tragical paediatric case history of intraorbital and intracranial epithelioid hemangioendothelioma","volume":"2012","author":"Aniba","year":"2012","unstructured":"Aniba KLaghmari MLmejjati MGhannane HAit Benali S.A tragical paediatric case history of intraorbital and intracranial epithelioid hemangioendothelioma. Case Rep Neurol Med. 2012;2012:396097."},{"issue":"9","key":"bib28","series-title":"Anticancer Res","first-page":"4891","article-title":"The role of local therapy in multi-focal epithelioid haemangioendothelioma","volume":"39","author":"Tong","year":"2019","unstructured":"Tong DConstantinidou AEngelmann BThe role of local therapy in multi-focal epithelioid haemangioendothelioma. Anticancer Res. 2019;39(9):4891-4896."},{"issue":"5","key":"bib1","series-title":"Cancer","first-page":"970","article-title":"Epithelioid hemangioendothelioma: a vascular tumor often mistaken for a carcinoma","volume":"50","author":"Weiss","year":"1982","unstructured":"Weiss SWEnzinger FM.Epithelioid hemangioendothelioma: a vascular tumor often mistaken for a carcinoma. Cancer. 1982;50(5):970-981."},{"issue":"2","key":"bib2","series-title":"Oncol Rev","first-page":"259","article-title":"Epithelioid hemangioendothelioma: an overview and update on a rare vascular tumor","volume":"8","author":"Sardaro","year":"2014","unstructured":"Sardaro ABardoscia LPetruzzelli MFPortaluri M.Epithelioid hemangioendothelioma: an overview and update on a rare vascular tumor. Oncol Rev. 2014;8(2):259."},{"issue":"4","key":"bib3","series-title":"Semin Diagn Pathol","first-page":"259","article-title":"Epithelioid hemangioendothelioma and related lesions","volume":"3","author":"Weiss","year":"1986","unstructured":"Weiss SWIshak KGDail DHSweet DEEnzinger FM.Epithelioid hemangioendothelioma and related lesions. Semin Diagn Pathol. 1986;3(4):259-287."},{"issue":"3","key":"bib4","series-title":"Acta Clin Croat","first-page":"570","article-title":"Primary epithelioid hemangioendothelioma in the cerebellum: case report with reference to drastic change in the who classification","volume":"57","author":"Omerhod\u017ei\u0107","year":"2018","unstructured":"Omerhod\u017ei\u0107 IBilalovi\u0107 NRov\u010danin BPrimary epithelioid hemangioendothelioma in the cerebellum: case report with reference to drastic change in the who classification. Acta Clin Croat. 2018;57(3):570-576."},{"issue":"7","key":"bib5","series-title":"Jpn J Clin Oncol","first-page":"739","article-title":"Epithelioid hemangioendothelioma\u2014its history, clinical features, molecular biology and current therapy","volume":"54","author":"Tsuchihashi","year":"2024","unstructured":"Tsuchihashi KBaba E.Epithelioid hemangioendothelioma\u2014its history, clinical features, molecular biology and current therapy. Jpn J Clin Oncol. 2024;54(7):739-747."},{"key":"bib6","series-title":"Eur J Cancer","first-page":"113262","article-title":"Epithelioid hemangio-endothelioma (EHE) in NETSARC: the nationwide series of 267 patients over 12 years","volume":"192","author":"Blay","year":"2023","unstructured":"Blay JYPiperno-Neumann SWatson SEpithelioid hemangio-endothelioma (EHE) in NETSARC: the nationwide series of 267 patients over 12 years. Eur J Cancer. 2023;192:113262."},{"key":"bib7","series-title":"J Oncol","first-page":"2349991","article-title":"Epithelioid hemangioendothelioma: incidence, mortality, prognostic factors, and survival analysis using the surveillance, epidemiology, and end results database","volume":"2022","author":"Liu","year":"2022","unstructured":"Liu ZHe S.Epithelioid hemangioendothelioma: incidence, mortality, prognostic factors, and survival analysis using the surveillance, epidemiology, and end results database. J Oncol. 2022;2022:2349991."},{"issue":"6","key":"bib8","series-title":"Am J Surg Pathol","first-page":"619","article-title":"Epithelioid hemangioendothelioma of the brain","volume":"16","author":"Chow","year":"1992","unstructured":"Chow LTChow WHFong DT.Epithelioid hemangioendothelioma of the brain. Am J Surg Pathol. 1992;16(6):619-625."},{"issue":"5","key":"bib9","series-title":"Neuropathology","first-page":"338","article-title":"Hemorrhage from metastatic brain epithelioid hemangioendothelioma: a case report","volume":"44","author":"Fusegawa","year":"2024","unstructured":"Fusegawa TTomita TOkuno NAkai TKuroda S.Hemorrhage from metastatic brain epithelioid hemangioendothelioma: a case report. Neuropathology. 2024;44(5):338-343."},{"issue":"3","key":"bib10","series-title":"Neuropathology","first-page":"201","article-title":"Aggressive intracranial and extra-cranial epithelioid hemangioendothelioma: a case report and review of the literature","volume":"26","author":"Fernandes","year":"2006","unstructured":"Fernandes ALRatilal BMafra MMagalhaes C.Aggressive intracranial and extra-cranial epithelioid hemangioendothelioma: a case report and review of the literature. Neuropathology. 2006;26(3):201-205."},{"issue":"3","key":"bib11","series-title":"Eur Respir J","first-page":"483","article-title":"Central nervous system metastases of a pulmonary epitheloid haemangioendothelioma","volume":"23","author":"D\u00edaz","year":"2004","unstructured":"D\u00edaz RSegura ACalderero VCentral nervous system metastases of a pulmonary epitheloid haemangioendothelioma. Eur Respir J. 2004;23(3):483-486."},{"issue":"suppl 23","key":"bib12","series-title":"Surg Neurol Int","first-page":"S596","article-title":"Suprasellar epithelioid hemangioendothelioma: case report and review of the literature","volume":"7","author":"Barger","year":"2016","unstructured":"Barger JTanweer OLiechty BSnuderl MJafar JJ.Suprasellar epithelioid hemangioendothelioma: case report and review of the literature. Surg Neurol Int. 2016;7(suppl 23):S596-S602."},{"issue":"3","key":"bib13","series-title":"J Neurooncol","first-page":"337","article-title":"Malignant intracranial epithelioid hemangioendothelioma presumably originating from the lung: case report","volume":"67","author":"Endo","year":"2004","unstructured":"Endo TSu CCNumagami YShirane R.Malignant intracranial epithelioid hemangioendothelioma presumably originating from the lung: case report. J Neurooncol. 2004;67(3):337-343."},{"issue":"4","key":"bib14","series-title":"Mod Pathol","first-page":"591","article-title":"Prognostic stratification of clinical and molecular epithelioid hemangioendothelioma subsets","volume":"33","author":"Rosenbaum","year":"2020","unstructured":"Rosenbaum EJadeja BXu BPrognostic stratification of clinical and molecular epithelioid hemangioendothelioma subsets. Mod Pathol. 2020;33(4):591-602."},{"issue":"3","key":"bib15","series-title":"ESMO Open","first-page":"100170","article-title":"Epithelioid hemangioendothelioma, an ultra-rare cancer: a consensus paper from the community of experts","volume":"6","author":"Stacchiotti","year":"2021","unstructured":"Stacchiotti SMiah ABFrezza AMEpithelioid hemangioendothelioma, an ultra-rare cancer: a consensus paper from the community of experts. ESMO Open. 2021;6(3):100170."},{"issue":"1","key":"bib16","series-title":"BMC Cancer","first-page":"993","article-title":"Clinical characteristics of Japanese patients with epithelioid hemangioendothelioma: a multicenter retrospective study","volume":"18","author":"Shiba","year":"2018","unstructured":"Shiba SImaoka HShioji KClinical characteristics of Japanese patients with epithelioid hemangioendothelioma: a multicenter retrospective study. BMC Cancer. 2018;18(1):993."},{"issue":"12","key":"bib17","series-title":"Mod Pathol","first-page":"2211","article-title":"YAP1-TFE3-fused hemangioendothelioma: a multi-institutional clinicopathologic study of 24 genetically-confirmed cases","volume":"34","author":"Dermawan","year":"2021","unstructured":"Dermawan JKAzzato EMBillings SDYAP1-TFE3-fused hemangioendothelioma: a multi-institutional clinicopathologic study of 24 genetically-confirmed cases. Mod Pathol. 2021;34(12):2211-2221."},{"issue":"8","key":"bib18","series-title":"Genes Chromosomes Cancer","first-page":"775","article-title":"Novel YAP1-TFE3 fusion defines a distinct subset of epithelioid hemangioendothelioma","volume":"52","author":"Antonescu","year":"2013","unstructured":"Antonescu CRLe Loarer FMosquera JMNovel YAP1-TFE3 fusion defines a distinct subset of epithelioid hemangioendothelioma. Genes Chromosomes Cancer. 2013;52(8):775-784."},{"key":"bib19","series-title":"Surg Neurol Int","first-page":"156","article-title":"Multiple hemorrhagic intraparenchymal tumors presenting with fatal intracranial hypertension: a rare manifestation of systemic epithelioid hemangioendothelioma","volume":"6","author":"Tsuchiya","year":"2015","unstructured":"Tsuchiya TOya SMori HMatsui T.Multiple hemorrhagic intraparenchymal tumors presenting with fatal intracranial hypertension: a rare manifestation of systemic epithelioid hemangioendothelioma. Surg Neurol Int. 2015;6:156."},{"issue":"2","key":"bib20","series-title":"Neurosurgery","first-page":"410","article-title":"Pediatric intracranial hemangioendotheliomas: case report","volume":"40","author":"Chen","year":"1997","unstructured":"Chen TCGonzalez-Gomez IGilles FHMcComb JG.Pediatric intracranial hemangioendotheliomas: case report. Neurosurgery. 1997;40(2):410-414."},{"issue":"8","key":"bib21","series-title":"Arq Neuro Psiquiatr","first-page":"637","article-title":"Cerebral epithelioid hemangioendothelioma with thoracic simultaneous involvement: advanced MRI features","volume":"70","author":"Rocha Oliveira","year":"2012","unstructured":"Rocha Oliveira PCAlcantara FPSouza-Vianna PEBrito AP.Cerebral epithelioid hemangioendothelioma with thoracic simultaneous involvement: advanced MRI features. Arq Neuro Psiquiatr. 2012;70(8):637-638."},{"issue":"1","key":"bib22","series-title":"J Neurooncol","first-page":"119","article-title":"Primary intracranial epithelioid hemangioendothelioma: a low-proliferation tumor exhibiting clinically malignant behavior","volume":"110","author":"Zheng","year":"2012","unstructured":"Zheng JLiu LWang JWang SCao YZhao J.Primary intracranial epithelioid hemangioendothelioma: a low-proliferation tumor exhibiting clinically malignant behavior. J Neurooncol. 2012;110(1):119-127."},{"issue":"7","key":"bib23","series-title":"Int J Surg Pathol","first-page":"1694","article-title":"A lung epithelioid hemangioendothelioma subtype with YAP1::TFE3 fusion: a case report","volume":"33","author":"Xiao","year":"2025","unstructured":"Xiao CXu WShen MCao DLv J.A lung epithelioid hemangioendothelioma subtype with YAP1::TFE3 fusion: a case report. 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