{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,26]],"date-time":"2026-01-26T09:47:42Z","timestamp":1769420862567,"version":"3.49.0"},"reference-count":45,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[1981,7]]},"abstract":"<jats:p content-type=\"fine-print\">\u2713 A clinical analysis of 23 patients with Dandy-Walker malformation indicates that more than 85% of them were diagnosed at or before 1 year of age, and that the incidence of associated anomalies is approximately 50%, with a 17% incidence for agenesis of the corpus callosum. The significance of the presence of these anomalies is substantiated by the fact that of the seven deaths recorded, six were related to this disease and five were affected by associated anomalies. The high mortality rate (26%) is comparable to that of other series. The differential diagnosis with posterior fossa extra-axial cysts is discussed.<\/jats:p>\n<jats:p content-type=\"fine-print\">Ten patients were primarily treated with excision of the cyst membrane; all of them required subsequent shunting to control the intracranial pressure, demonstrating the futility of this approach. None of the patients treated with lateral ventricle shunting suffered an upward herniation of the posterior fossa contents, suggesting that combined shunting of the lateral and fourth ventricles is rarely necessary. The technical advantages of posterior fossa shunting alone are outlined. Of the 16 survivors, 14 were assessed for their mental development by means of standard psychometric testing. The results of the intelligence quotient (IQ) scoring have indicated that 71% of the patients have subnormal mental development (IQ &lt; 83). There was no significant relationship between retardation and associated anomalies, although agenesis of the corpus callosum was related to poor intellectual development in the two patients so affected (IQ's of 50 and 73).<\/jats:p>","DOI":"10.3171\/jns.1981.55.1.0089","type":"journal-article","created":{"date-parts":[[2009,5,8]],"date-time":"2009-05-08T13:45:14Z","timestamp":1241790314000},"page":"89-98","source":"Crossref","is-referenced-by-count":102,"title":["Dandy-Walker syndrome"],"prefix":"10.3171","volume":"55","author":[{"given":"Raymond","family":"Sawaya","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Robert L.","family":"McLaurin","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"b1","series-title":"Radiology","doi-asserted-by":"publisher","first-page":"681","DOI":"10.1148\/127.3.681","article-title":"Enlarged cisternae magnae and posterior fossa cysts simulating Dandy-Walker syndrome on computed tomography.","volume":"127","author":"Archer","year":"1978"},{"key":"b2","series-title":"J Neuropathol Exp Neurol","doi-asserted-by":"publisher","first-page":"14","DOI":"10.1093\/jnen\/13.1.14","article-title":"The Dandy-Walker syndrome or the so-called atresia of the foramen Magendie.","volume":"13","author":"Benda","year":"1954"},{"key":"b3","series-title":"J Neurol Neurosurg Psychiatry","doi-asserted-by":"publisher","first-page":"99","DOI":"10.1136\/jnnp.22.2.99","article-title":"Congenital hydrocephalus with defective development of the cerebellar vermis (Dandy-Walker syndrome).","volume":"22","author":"Brodal","year":"1959"},{"key":"b4","series-title":"Surg Neurol","first-page":"132","article-title":"Dandy-Walker syndrome: clinicopathological features and re-evaluation of modes of treatment.","volume":"8","author":"Carmel","year":"1977"},{"key":"b5","series-title":"J Anat","first-page":"525","article-title":"A specific factor in extracts of the choroid plexus influencing the permeability of the myelencephalic roof.","volume":"73","author":"Cohen","year":"1939"},{"key":"b6","series-title":"J Neurosurg","doi-asserted-by":"publisher","first-page":"84","DOI":"10.3171\/jns.1948.5.1.0084","article-title":"Congenital atresia of the foramina of Luschka and Magendie with report of two cases of surgical cure.","volume":"5","author":"Coleman","year":"1948"},{"key":"b7","series-title":"Am J Roentgenol","doi-asserted-by":"publisher","first-page":"306","DOI":"10.2214\/ajr.112.2.306","article-title":"Radionuclide evaluation of the Dandy-Walker malformation and congenital arachnoid cyst of the posterior fossa.","volume":"112","author":"Conway","year":"1971"},{"key":"b8","series-title":"J Neuropathol Exp Neurol","doi-asserted-by":"publisher","first-page":"450","DOI":"10.1097\/00005072-196307000-00007","article-title":"The Dandy-Walker syndrome.","volume":"22","author":"D'Agostino","year":"1963"},{"key":"b9","series-title":"Surg Gynecol Obstet","first-page":"113","article-title":"The diagnosis and treatment of hydrocephalus due to occlusions of the foramina of Magendie and Luschka.","volume":"32","author":"Dandy","year":"1921"},{"key":"b10","series-title":"Am J Dis Child","first-page":"406","article-title":"Internal hydrocephalus. 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