{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,8]],"date-time":"2026-09-08T17:27:33Z","timestamp":1788888453871,"version":"build-2803163510"},"reference-count":22,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["PED"],"published-print":{"date-parts":[[2008,1]]},"abstract":"<jats:p>\u2713 Osteopetrosis is a heterogeneous group of disorders characterized by abnormal bone sclerosis. As a result, patients often require input regarding various neurological complications. Although autosomal-recessive osteopetrosis has been associated with hydrocephalus, it has not been linked to hindbrain abnormalities. The authors present 3 cases of auto-somal-recessive osteopetrosis in patients who presented with hydrocephalus. In each of these patients, cerebrospinal fluid diversion procedures were required and hindbrain compression developed. To date, only 1 patient has needed craniocervical decompression due to symptomatic brainstem compression.<\/jats:p>","DOI":"10.3171\/ped-08\/01\/103","type":"journal-article","created":{"date-parts":[[2008,1,2]],"date-time":"2008-01-02T13:41:41Z","timestamp":1199281301000},"page":"103-106","source":"Crossref","is-referenced-by-count":47,"title":["Patients with autosomal-recessive osteopetrosis presenting with hydrocephalus and hindbrain posterior fossa crowding"],"prefix":"10.3171","volume":"1","author":[{"given":"Yahia Z.","family":"Al-Tamimi","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Atul K.","family":"Tyagi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paul D.","family":"Chumas","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Darach W.","family":"Crimmins","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1754","reference":[{"key":"b1-0010103","series-title":"J Neurosurg","doi-asserted-by":"publisher","first-page":"80","DOI":"10.3171\/jns.1988.68.1.0080","article-title":"Optic nerve decompression in osteopetrosis","volume":"68","author":"Al-Mefty","year":"1988"},{"key":"b2-0010103","series-title":"Childs Brain","first-page":"257","article-title":"Neurological complications of osteopetrosis","volume":"3","author":"Amacher","year":"1977"},{"key":"b3-0010103","series-title":"Can Med Assoc J","first-page":"362","article-title":"Congenital osteopetrosis: an unusual cause of hydrocephalus","volume":"98","author":"Baird","year":"1968"},{"key":"b4-0010103","series-title":"Acta Orthop Belg","first-page":"528","article-title":"Association of severe autosomal recessive osteopetrosis and Dandy-Walker syndrome with agenesis of the corpus callosum","volume":"67","author":"Ben Hamouda","year":"2001"},{"key":"b5-0010103","series-title":"Neurosurgery","doi-asserted-by":"publisher","first-page":"960","DOI":"10.1097\/00006123-199710000-00039","article-title":"Foramen magnum decompression for cervicomedullary encroachment in cranio-metaphyseal dysplasia: case report","volume":"41","author":"Day","year":"1997"},{"key":"b6-0010103","series-title":"Am J Med Genet","doi-asserted-by":"publisher","first-page":"811","DOI":"10.1002\/ajmg.1320230308","article-title":"Lethal osteopetrosis with multiple fractures in utero","volume":"23","author":"el Khazen","year":"1986"},{"key":"b7-0010103","series-title":"Radiology","doi-asserted-by":"publisher","first-page":"137","DOI":"10.1148\/radiology.183.1.1549660","article-title":"Cranial imaging in autosomal recessive osteopetrosis. 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