{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,7]],"date-time":"2025-11-07T08:48:36Z","timestamp":1762505316078},"reference-count":19,"publisher":"Journal of Neurosurgery Publishing Group (JNSPG)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["SPI"],"published-print":{"date-parts":[[2007,8]]},"abstract":"<jats:p>\u2713The authors describe the clinical course and treatment of a patient with cleidocranial dysplasia in whom spastic myelopathy developed due to atlantoaxial subluxation. This 27-year-old woman with cleidocranial dysplasia and a history of atlantoaxial subluxation presented with spastic myelopathy. Surgery was performed twice for cervical myelopathy and atlantoaxial subluxation, including laminectomy at the atlas and cervicooccipital fusion in which the Luque rod system was used, as well as C1\u20132 fusion via the transpharyngeal route. Solid bone fusion was achieved by 7 months postsurgery. Postoperative magnetic resonance imaging studies demonstrated that spinal cord compression was relieved, but atrophy persisted. At 2 years postsurgery there was no neurological disease progression, but spasticity persisted. The patient could walk with a cane. Cleidocranial dysplasia is an extremely rare cause of myelopathy in patients with atlantoaxial subluxation; the authors know of only two reports of this condition. When managing cleidocranial dysplasia, the practitioner should always be aware that atlantoaxial subluxation may be the cause of cervical myelopathy.<\/jats:p>","DOI":"10.3171\/spi-07\/08\/243","type":"journal-article","created":{"date-parts":[[2008,1,24]],"date-time":"2008-01-24T13:19:02Z","timestamp":1201180742000},"page":"243-247","source":"Crossref","is-referenced-by-count":7,"title":["Atlantoaxial subluxation\u2013induced myelopathy in cleidocranial dysplasia"],"prefix":"10.3171","volume":"7","author":[{"given":"Shigeru","family":"Kobayashi","sequence":"first","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation Medicine, Fukui University School of Medicine, Fukui;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kenzo","family":"Uchida","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation Medicine, Fukui University School of Medicine, Fukui;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hisatoshi","family":"Baba","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation Medicine, Fukui University School of Medicine, Fukui;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kenichi","family":"Takeno","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation Medicine, Fukui University School of Medicine, Fukui;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takasi","family":"Yayama","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation Medicine, Fukui University School of Medicine, Fukui;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hideaki","family":"Nakajima","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics and Rehabilitation Medicine, Fukui University School of Medicine, Fukui;"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Eiki","family":"Nomura","sequence":"additional","affiliation":[{"name":"Department of Orthopedic Surgery, Kawasaki Municipal Hospital, Kanagawa; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hidezo","family":"Yoshizawa","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics, Tachikawa Kyousai Hospital, Tokyo, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1754","reference":[{"key":"b1-0070243","series-title":"Shounika Rinsyou","first-page":"401","article-title":"[Familial cases of dysotosis cleidocranialis. 89 cases in Japan.]","volume":"29","author":"Aritaki","year":"1976"},{"key":"b2-0070243","series-title":"Pediatr Clin North Am","doi-asserted-by":"publisher","first-page":"397","DOI":"10.1016\/S0031-3955(16)31982-4","article-title":"Congenital defects of shoulder girdle, sternum, spine and pelvis","volume":"14","author":"Bell","year":"1967"},{"key":"b3-0070243","series-title":"Am J Orthop","first-page":"383","article-title":"Unilateral absence of the clavicle with rapidly progressive scoliosis in an 8-year-old","volume":"29","author":"Codsi","year":"2000"},{"key":"b4-0070243","series-title":"Clin Orthop Relat Res","first-page":"229","article-title":"Cleidocranial dysostosis and syringomyelia. 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