{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,9,25]],"date-time":"2023-09-25T09:20:54Z","timestamp":1695633654865},"reference-count":0,"publisher":"Croatia Scientific Society for the History of Health Culture","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["AMHA"],"published-print":{"date-parts":[[2019,7,29]]},"abstract":"<jats:p>La beta thalassemia rappresenta una delle pi\u00f9 comuni patologie autosomiche recessive nel mondo. I Paesi mediterranei, del Medio Oriente e del Sud Est Asiatico sono regioni ad alta prevalenza di beta thalassemia. Le pi\u00f9 alte incidenze sono riportate a Cipro, nel Sud Est Asiatico e in Sardegna, correlate molto probabilmente alla pressione selettiva esercitata dal Pl. falciparum, agente eziologico della malaria. In Sardegna, per la rilevanza sanitaria della patologia e in seguito alla pubblicazione dei primi studi scientifici sul morbo di Cooley, sono fiorite importanti scuole di pediatria e genetica medica, che contribuiranno alla definizione dei criteri diagnostici, della terapia e della prevenzione, anche neonatale, dell\u2019anemia mediterranea e delle emoglobinopatie.<\/jats:p>","DOI":"10.31952\/amha.17.1.4","type":"journal-article","created":{"date-parts":[[2019,7,2]],"date-time":"2019-07-02T12:02:56Z","timestamp":1562068976000},"page":"65-90","source":"Crossref","is-referenced-by-count":3,"title":["La storia della beta talassemia in Sardegna","The history of beta thalassaemia in Sardinia"],"prefix":"10.31952","volume":"17","author":[{"given":"Mariano","family":"Martini","sequence":"first","affiliation":[{"name":"Department of Health Sciences \u2013 Section of Medical Humanities and Ethics, University of Genoa Italy; UNESCO CHAIR \u201cAnthropology of Health \u2013 Biosphere and Healing System\u201d, University of Genoa, Genoa."}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Cristina","family":"Tornali","sequence":"additional","affiliation":[{"name":"Department of Biomedical and Biotechnological Sciences, University of Catania, Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nicola Luigi","family":"Bragazzi","sequence":"additional","affiliation":[{"name":"Department of Health Sciences, University of Genoa, Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Filippo","family":"Paluan","sequence":"additional","affiliation":[{"name":"Department of Cardiac, Thoracic and Vascular Sciences, University of Padua, Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Maria Francesca","family":"Vardeu","sequence":"additional","affiliation":[{"name":"ATS Sardegna \u2013 Azienda Tutela Salute (ASSL Cagliari), Cagliari, Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"17243","published-online":{"date-parts":[[2019,7,1]]},"container-title":["Acta medico-historica Adriatica"],"original-title":[],"link":[{"URL":"http:\/\/www.amha-journal.com\/index.php\/AMHA\/article\/view\/14\/519","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,24]],"date-time":"2023-09-24T16:36:01Z","timestamp":1695573361000},"score":1,"resource":{"primary":{"URL":"https:\/\/hrcak.srce.hr\/ojs\/index.php\/amha\/article\/view\/17068"}},"subtitle":["il contributo delle Scuole Italiane di pediatria","the contribution of the Italian Schools of Pediatrics"],"short-title":[],"issued":{"date-parts":[[2019,7,1]]},"references-count":0,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2019,7,1]]},"published-print":{"date-parts":[[2019,7,29]]}},"URL":"https:\/\/doi.org\/10.31952\/amha.17.1.4","relation":{},"ISSN":["1334-6253","1334-4366"],"issn-type":[{"value":"1334-6253","type":"electronic"},{"value":"1334-4366","type":"print"}],"subject":[],"published":{"date-parts":[[2019,7,1]]}}}