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The field is also renowned for its collaborative spirit and use of standardized reagents, assays, datasets, models, and clinical measures, so the use of standardized terms is especially important. We have set out to determine, through a consensus exercise involving basic and clinical scientists working in the field, the most appropriate language to use across disciplines. Nominally, this article will serve as the style guide for the Journal of Huntington\u2019s Disease (JHD), the only journal devoted exclusively to HD, and we lay out the preferred and standardized terminology and nomenclature for use in JHD publications. However, we hope that this article will also serve as a useful resource to the HD research community at large and that these recommended naming conventions will be adopted widely.<\/jats:p>","DOI":"10.3233\/jhd-240044","type":"journal-article","created":{"date-parts":[[2024,7,5]],"date-time":"2024-07-05T11:50:04Z","timestamp":1720180204000},"page":"119-131","source":"Crossref","is-referenced-by-count":12,"title":["Towards Standardizing Nomenclature in Huntington\u2019s Disease Research"],"prefix":"10.1177","volume":"13","author":[{"given":"Marian","family":"DiFiglia","sequence":"first","affiliation":[{"name":"Department of Neurology, MassGeneral Institute for Neurodegenerative Disease, Harvard Medical School, Charlestown, MA, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"name":"Huntington\u2019s Disease Nomenclature Working Group: BatesGillian P.University College London, Elena Cattaneo, University of Milan ChaJang-HoLatus Bio FaullRichardUniversity of Aukland FeiginAndrewNew York University GantmanEmily C.CHDI Management, Inc. GusellaJames F.Harvard University HaydenMichaelUniversity of British Columbia HousmanDavidMassachusetts Institute of Technology HowlandDavidCHDI Management, Inc. LangbehnDougUniversity of Iowa LandwehrmeyerBernhard G.ULM University LongJeffrey D.University of I","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Blair R.","family":"Leavitt","sequence":"additional","affiliation":[{"name":"Center for Molecular Medicine and Therapeutics and Departments of Medical Genetics and Medicine, University of British Columbia, Vancouver, BC, Canada"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Douglas","family":"Macdonald","sequence":"additional","affiliation":[{"name":"CHDI Management, Inc., The Company that Manages the Scientific Activities of CHDI Foundation, Inc, Los Angeles, CA, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Leslie M.","family":"Thompson","sequence":"additional","affiliation":[{"name":"Departments of Psychiatry and Human Behavior and Neurobiology and Behavior, University of California, Irvine, CA, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"179","reference":[{"issue":"9557","key":"10.3233\/JHD-240044_ref1","doi-asserted-by":"crossref","first-page":"218","DOI":"10.1016\/S0140-6736(07)60111-1","article-title":"Huntington\u2019s disease","volume":"369","author":"Walker","year":"2007","journal-title":"Lancet"},{"key":"10.3233\/JHD-240044_ref2","doi-asserted-by":"crossref","unstructured":"Unified Huntington\u2019s Disease Rating Scale: Reliability and consistency. 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