{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,22]],"date-time":"2026-08-22T18:56:20Z","timestamp":1787424980845,"version":"build-2736575974"},"reference-count":19,"publisher":"SAGE Publications","issue":"1","license":[{"start":{"date-parts":[[2022,1,4]],"date-time":"2022-01-04T00:00:00Z","timestamp":1641254400000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["JND"],"published-print":{"date-parts":[[2022,1,4]]},"abstract":"<jats:p>Some patients with Oculopharyngeal Muscular Dystrophy (OPMD) develop frontotemporal dementia (FTD). The prevalence and clinical correlates of behavioural impairment, including FTD, is unknown in OPMD. 24 OPMD patients and their proxies completed a questionnaire concerning behavioural impairment (ALS-FTD-Q). We examined proportions with mild or severe behavioural changes, according to validated cut-off proxy scores. We examined correlations with the Hospital Anxiety and Depression Scale (HADS), the Short Form Health Survey (SF-36), motor symptoms, genotype and disease duration. In this small patient sample, behavioural impairment was present in 29%of OPMD patients; in 17%the severity of symptoms was compatible with bvFTD. Correlations were small to medium.<\/jats:p>","DOI":"10.3233\/jnd-200592","type":"journal-article","created":{"date-parts":[[2021,7,30]],"date-time":"2021-07-30T10:59:38Z","timestamp":1627642778000},"page":"129-135","source":"Crossref","is-referenced-by-count":4,"title":["Behavioural Impairment and Frontotemporal Dementia in Oculopharyngeal Muscular Dystrophy"],"prefix":"10.1177","volume":"9","author":[{"given":"Maurits","family":"Tankink","sequence":"first","affiliation":[{"name":"Department of Neurology, Radboud University Medical Center, EX Nijmegen, the Netherlands"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Corinne G.C.","family":"Horlings","sequence":"additional","affiliation":[{"name":"Department of Neurology, Donders Institute for Brain, Cognition and Behaviour, Radboud University Medical Center, EX Nijmegen, the Netherlands"},{"name":"Department of Neurology, Medical University Innsbruck, Innsbruck, Austria"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nicol","family":"Voermans","sequence":"additional","affiliation":[{"name":"Department of Neurology, Donders Institute for Brain, Cognition and Behaviour, Radboud University Medical Center, EX Nijmegen, the Netherlands"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Barbara","family":"van der Sluijs","sequence":"additional","affiliation":[{"name":"Department of Neurology, Gelre Hospital Zutphen, Zutphen, The Netherlands"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Roy P.C.","family":"Kessels","sequence":"additional","affiliation":[{"name":"Donders Institute for Brain, Cognition and Behaviour, Radboud University. 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