{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,4]],"date-time":"2026-05-04T10:26:08Z","timestamp":1777890368990,"version":"3.51.4"},"reference-count":15,"publisher":"SAGE Publications","issue":"3","license":[{"start":{"date-parts":[[2018,7,14]],"date-time":"2018-07-14T00:00:00Z","timestamp":1531526400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":["journals.sagepub.com"],"crossmark-restriction":true},"short-container-title":["Journal of Neonatal-Perinatal Medicine"],"published-print":{"date-parts":[[2018,9,28]]},"abstract":"<jats:p>Alveolar capillary dysplasia (ACD) is a rare neonatal lung disease characterized anatomically by a defective and hypoplastic development of pulmonary alveoli leading to persistent pulmonary hypertension (PPHN) and finally lethal respiratory failure. It is often associated with congenital left heart obstruction. Given the fatal prognosis an early diagnosis is important. However, due to the fast onset of PPHN in neonates and lack of pathognomonic signs for its cause, safe and fast detection of ACD is challenging. Therefore, following the exclusion of cardiac and common pulmonary causes, lung biopsy becomes essential for diagnosis.<\/jats:p>\n                  <jats:p>We hereby report a case of ACD with atrial septal defect type one and hypoplastic aortic arch with an ante-mortem diagnosis and discuss the current state of medicine in relation to ACD.<\/jats:p>","DOI":"10.3233\/npm-17119","type":"journal-article","created":{"date-parts":[[2018,7,17]],"date-time":"2018-07-17T12:25:41Z","timestamp":1531830341000},"page":"289-293","update-policy":"https:\/\/doi.org\/10.1177\/sage-journals-update-policy","source":"Crossref","is-referenced-by-count":3,"title":["Alveolar capillary dysplasia with left heart obstruction \u2013 rare but lethal"],"prefix":"10.1177","volume":"11","author":[{"given":"V.C.","family":"Stark","sequence":"first","affiliation":[{"name":"University Heart Center, Pediatric Cardiology, Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"E.P.","family":"Schneider","sequence":"additional","affiliation":[{"name":"University Heart Center, Pediatric Cardiology, Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"D.","family":"Biermann","sequence":"additional","affiliation":[{"name":"University Heart Center, Pediatric Cardiac Surgery, Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P.A.","family":"Hauck","sequence":"additional","affiliation":[{"name":"University Heart Center, Pediatric Cardiology, Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"R.","family":"Kozlik-Feldmann","sequence":"additional","affiliation":[{"name":"University Heart Center, Pediatric Cardiology, Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H.","family":"Sch\u00e4fer","sequence":"additional","affiliation":[{"name":"University Hospital Hamburg-Eppendorf, Institute of Pathology, Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"U.","family":"Gottschalk","sequence":"additional","affiliation":[{"name":"University Heart Center, Pediatric Cardiology, Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","published-online":{"date-parts":[[2018,7,14]]},"reference":[{"key":"ref001","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201010-1697CI"},{"key":"ref002","doi-asserted-by":"publisher","DOI":"10.1007\/s00246-007-0049-0"},{"key":"ref003","doi-asserted-by":"publisher","DOI":"10.1017\/S1047951112001904"},{"issue":"4","key":"ref004","first-page":"919","volume":"24","author":"MacMahon HE","year":"1948","journal-title":"Am J Pathol"},{"key":"ref005","doi-asserted-by":"publisher","DOI":"10.1016\/S0378-3782(99)00065-1"},{"key":"ref006","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2013.06.014"},{"key":"ref007","doi-asserted-by":"publisher","DOI":"10.3109\/15513819209024200"},{"key":"ref008","doi-asserted-by":"publisher","DOI":"10.1080\/15513819709168352"},{"key":"ref009","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(89)80800-5"},{"key":"ref010","doi-asserted-by":"publisher","DOI":"10.1007\/s100240010125"},{"key":"ref011","doi-asserted-by":"publisher","DOI":"10.1016\/j.ajhg.2009.05.005"},{"key":"ref012","doi-asserted-by":"publisher","DOI":"10.1016\/j.prrv.2011.01.002"},{"key":"ref013","doi-asserted-by":"publisher","DOI":"10.1136\/thx.2003.010793"},{"key":"ref014","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2016.11.031"},{"key":"ref015","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2015.11.041"}],"container-title":["Journal of Neonatal-Perinatal Medicine"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.3233\/NPM-17119","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/full-xml\/10.3233\/NPM-17119","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/journals.sagepub.com\/doi\/pdf\/10.3233\/NPM-17119","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T05:36:19Z","timestamp":1777613779000},"score":1,"resource":{"primary":{"URL":"https:\/\/journals.sagepub.com\/doi\/10.3233\/NPM-17119"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,7,14]]},"references-count":15,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2018,9,28]]}},"alternative-id":["10.3233\/NPM-17119"],"URL":"https:\/\/doi.org\/10.3233\/npm-17119","relation":{},"ISSN":["1934-5798","1878-4429"],"issn-type":[{"value":"1934-5798","type":"print"},{"value":"1878-4429","type":"electronic"}],"subject":[],"published":{"date-parts":[[2018,7,14]]}}}