{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,4]],"date-time":"2026-05-04T10:20:02Z","timestamp":1777890002982,"version":"3.51.4"},"reference-count":19,"publisher":"SAGE Publications","issue":"5","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["VES"],"published-print":{"date-parts":[[2022,10,20]]},"abstract":"<jats:p>OBJECTIVE: To evaluate the benefit of vestibular rehabilitation therapy (VRT) in the management of patients with idiopathic cerebellar ataxia with bilateral vestibulopathy (iCABV). BACKGROUND: iCABV is a hindbrain degenerative disorder with impairment of both central and peripheral vestibular pathways. There is combined failure of four compensatory eye movement systems including the vestibulo-ocular reflex (VOR), optokinetic reflex, smooth pursuit and the visually enhanced vestibulo-ocular reflex (VVOR). Phenotypic presentation includes postural and gait instability, oscillopsia and dizziness with active head movement. The benefit of VRT in iCABV patients has not been established. METHODS: A retrospective review was performed on a cohort of twelve patients diagnosed with iCABV in a multidisciplinary neuro-otology clinic. All participated in VRT and completed their suggested course of VRT. The following clinical measures were assessed before starting and after finishing VRT: 1) Dizziness Handicap Inventory (DHI), 2) Activities-Specific Balance Confidence (ABC) Scale, 3) Catastrophization scale, 4) Positive Affective Negative Affective Score (PANAS), 5) Dynamic Gait Index (DGI) and 6) Modified Clinical Test of Sensory Interaction in Balance (mCTSIB). The number of falls historically was recorded in addition to gait speed (ft.\/sec). RESULTS: Following VRT, patients were found to have improved balance on mCTSIB (condition 4\u200a:\u200a7 vs 18 seconds, P\u200a=\u200a0.04) and a better postural stability with a reduced number of falls (p\u200a=\u200a0.01). No statistically significant improvement was seen in the DHI, ABC, Catastrophization scale, DGI, PANAS and gait speed (p\u200a&gt;\u200a0.05). CONCLUSIONS: iCABV patients who underwent VRT were found to have a better postural stability and reduced risk of falls. VRT was not found to significantly improve patients\u2019 overall subjective perception of their symptoms or their psychological status.<\/jats:p>","DOI":"10.3233\/ves-210058","type":"journal-article","created":{"date-parts":[[2022,5,6]],"date-time":"2022-05-06T11:31:00Z","timestamp":1651836660000},"page":"479-485","source":"Crossref","is-referenced-by-count":8,"title":["Effectiveness of vestibular rehabilitation therapy in patients with idiopathic Cerebellar Ataxia with Bilateral Vestibulopathy (iCABV)"],"prefix":"10.1177","volume":"32","author":[{"given":"Fatemeh","family":"Hassannia","sequence":"first","affiliation":[{"name":"Department of Otolaryngology-Head and Neck Surgery, Division of Otology\/Neurotology, Toronto General Hospital, University Health Network, University of Toronto, Toronto, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Priyanka","family":"Misale","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology-Head and Neck Surgery, Division of Otology\/Neurotology, Toronto General Hospital, University Health Network, University of Toronto, Toronto, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shaleen","family":"Sulway","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology-Head and Neck Surgery, Division of Otology\/Neurotology, Toronto General Hospital, University Health Network, University of Toronto, Toronto, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gabriela Vergara","family":"Olmos","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology-Head and Neck Surgery, Division of Otology\/Neurotology, Toronto General Hospital, University Health Network, University of Toronto, Toronto, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sasan","family":"Dabiri","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology-Head and Neck Surgery, Division of Otology\/Neurotology, Toronto General Hospital, University Health Network, University of Toronto, Toronto, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Paul","family":"Ranalli","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology-Head and Neck Surgery, Division of Otology\/Neurotology, Toronto General Hospital, University Health Network, University of Toronto, Toronto, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"John Alexander","family":"Rutka","sequence":"additional","affiliation":[{"name":"Department of Otolaryngology-Head and Neck Surgery, Division of Otology\/Neurotology, Toronto General Hospital, University Health Network, University of Toronto, Toronto, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"179","reference":[{"issue":"5-6","key":"10.3233\/VES-210058_ref1","doi-asserted-by":"crossref","first-page":"406","DOI":"10.1007\/BF03325236","article-title":"Measurement error and minimum detectable change in 4-meter gait speed in older adults","volume":"23","author":"Goldberg","year":"2011","journal-title":"Aging Clin Exp Res"},{"key":"10.3233\/VES-210058_ref2","first-page":"124","article-title":"et al. 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