{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,7]],"date-time":"2026-09-07T09:12:01Z","timestamp":1788772321169,"version":"build-2803163510"},"reference-count":26,"publisher":"Frontiers Media SA","license":[{"start":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T00:00:00Z","timestamp":1777593600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["frontiersin.org"],"crossmark-restriction":true},"short-container-title":["Front. Dent. Med."],"abstract":"<jats:sec>\n                    <jats:title>Introduction<\/jats:title>\n                    <jats:p>Oromandibular limb hypogenesis syndrome (OLHS) Type IIIA is an exceptionally rare congenital anomaly, with only a few cases documented in the literature. It is characterized by developmental hypoplasia of the tongue, mandible, and limbs, manifesting as hypoglossia, micrognathia, and hypomelia.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Case presentation<\/jats:title>\n                    <jats:p>We report the case of a 9-year-old patient presenting with restricted mouth opening and feeding difficulties. Clinical examination revealed fusion of the tongue to the palate with synechia. Surgical intervention involved the release of the dense fibrous band between the tongue and palate, followed by palatoplasty to correct the cleft palate. The cleft palate was successfully repaired using the Von Langenbeck technique, restoring oral functionality.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion<\/jats:title>\n                    <jats:p>This case highlights the clinical manifestations, differential diagnosis, and surgical management of OLHS Type IIIA. It underscores the importance of timely intervention to improve functional outcomes in patients with this rare syndrome.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.3389\/fdmed.2026.1776248","type":"journal-article","created":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T05:35:41Z","timestamp":1777613741000},"update-policy":"https:\/\/doi.org\/10.3389\/crossmark-policy","source":"Crossref","is-referenced-by-count":0,"title":["A rare variant of oromandibular limb hypogenesis syndrome: a case report of glossopalatal ankylosis"],"prefix":"10.3389","volume":"7","author":[{"given":"Sumit","family":"Chopra","sequence":"first","affiliation":[{"name":"SRD Dental Clinic and Maxillofacial Surgery Centre","place":["Dehradun, India"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vidya","family":"B","sequence":"additional","affiliation":[{"name":"Nitte (Deemed to be University), AB Shetty Memorial Institute of Dental Sciences (ABSMIDS), Department of Oral and Maxillofacial Surgery","place":["Mangalore, India"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ekta","family":"Singh","sequence":"additional","affiliation":[{"name":"SRD Dental Clinic and Maxillofacial Surgery Centre","place":["Dehradun, India"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ankit","family":"Parashar","sequence":"additional","affiliation":[{"name":"Private Practitioner","place":["Dehradun, Uttarakhand, India"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mahendra","family":"Dandge","sequence":"additional","affiliation":[{"name":"Altrus HealthCare Hospital","place":["Dehradun, India"]}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1965","published-online":{"date-parts":[[2026,5,1]]},"reference":[{"key":"B1","doi-asserted-by":"publisher","first-page":"17","DOI":"10.1051\/mbcb\/2021049","article-title":"Oromandibular limb hypogenesis syndrome: a singular variation of a rare syndrome: a case report","volume":"28","author":"Sahoo","year":"2022","journal-title":"J Oral Med Oral Surg"},{"key":"B2","doi-asserted-by":"publisher","first-page":"414","DOI":"10.4103\/0973-029X.102504","article-title":"Isolated aglossia congenita: a rare case of oromandibular limb hypogenesis syndrome type IB","volume":"16","author":"Gupta","year":"2012","journal-title":"J Oral MaxillofacPathol"},{"key":"B3","doi-asserted-by":"publisher","first-page":"276","DOI":"10.1111\/j.1600-0714.1982.tb00167.x","article-title":"Severe congenital hypoglossia and micrognathia with other multiple birth defects","volume":"11","author":"Oulis","year":"1982","journal-title":"J Oral Pathol Med"},{"key":"B4","doi-asserted-by":"publisher","first-page":"1092","DOI":"10.1016\/j.ijporl.2010.06.011","article-title":"Severe form of hypoglossia\u2013hypodactylia syndrome associated with complex cardiopathy: a case report","volume":"74","author":"Elalaoui","year":"2010","journal-title":"Int J Pediatr Otorhinolaryngol"},{"key":"B5","doi-asserted-by":"publisher","first-page":"403","DOI":"10.1016\/0030-4220(81)90150-x","article-title":"The hypoglossia-hypodactylia syndrome. 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