{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,31]],"date-time":"2026-08-31T15:20:12Z","timestamp":1788189612008,"version":"build-2803163510"},"reference-count":13,"publisher":"Frontiers Media SA","license":[{"start":{"date-parts":[[2026,6,16]],"date-time":"2026-06-16T00:00:00Z","timestamp":1781568000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["frontiersin.org"],"crossmark-restriction":true},"short-container-title":["Front. Med."],"abstract":"<jats:p>Primary cutaneous adenoid cystic carcinoma (PCACC) is a rare, slow-growing malignant adnexal tumor of the skin first described in the 1970s. We present the case of a 63-year-old man who developed a slow-growing nodule on the right forearm, an atypical location for this tumor. The diagnosis of PCACC was confirmed by histopathological examination. This report discusses the pathological, dermoscopic, and radiological characteristics of the lesion, as well as its successful management with wide local excision. This case underscores the importance of considering PCACC in the differential diagnosis of slow-growing cutaneous nodules, even when it occurs at unusual sites. While dermoscopy can provide valuable diagnostic clues, a definitive diagnosis necessitates histopathological evaluation. Wide local excision remains the standard therapeutic approach to minimize the risk of local recurrence, and long-term follow-up is imperative due to the potential for delayed recurrence.<\/jats:p>","DOI":"10.3389\/fmed.2026.1872296","type":"journal-article","created":{"date-parts":[[2026,6,16]],"date-time":"2026-06-16T04:27:29Z","timestamp":1781584049000},"update-policy":"https:\/\/doi.org\/10.3389\/crossmark-policy","source":"Crossref","is-referenced-by-count":0,"title":["Primary cutaneous adenoid cystic carcinoma of the right forearm: a case report and dermoscopic features"],"prefix":"10.3389","volume":"13","author":[{"given":"Si","family":"Li","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Xue","family":"Cheng","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ronggui","family":"Xing","sequence":"additional","affiliation":[{"name":"Department of Dermatology, South China Hospital, Medical School, Shenzhen University","place":["Shenzhen, China"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Zhenyin","family":"Peng","sequence":"additional","affiliation":[{"name":"Department of Dermatology, South China Hospital, Medical School, Shenzhen University","place":["Shenzhen, China"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tianyou","family":"Xiong","sequence":"additional","affiliation":[{"name":"Department of Dermatology, South China Hospital, Medical School, Shenzhen University","place":["Shenzhen, China"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yanan","family":"Jiang","sequence":"additional","affiliation":[{"name":"Department of Dermatology, South China Hospital, Medical School, Shenzhen University","place":["Shenzhen, China"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Xianbiao","family":"Zou","sequence":"additional","affiliation":[{"name":"Department of Dermatology, South China Hospital, Medical School, Shenzhen University","place":["Shenzhen, China"]}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1965","published-online":{"date-parts":[[2026,6,16]]},"reference":[{"key":"ref1","doi-asserted-by":"publisher","first-page":"589","DOI":"10.1111\/his.12767","article-title":"Malignant sweat gland tumours: an update","volume":"67","author":"Cardoso","year":"2015","journal-title":"Histopathology"},{"key":"ref2","doi-asserted-by":"publisher","first-page":"793","DOI":"10.1001\/archderm.1975.01630180121024","article-title":"Letter: adenoid cystic carcinoma of scalp","volume":"111","author":"Boggio","year":"1975","journal-title":"Arch Dermatol"},{"key":"ref3","doi-asserted-by":"publisher","first-page":"1669171","DOI":"10.3389\/fonc.2025.1669171","article-title":"Multiline treatment of primary cutaneous adenoid cystic carcinoma with multiple metastases: a case report and literature review","author":"Geng","year":"2025","journal-title":"Front Oncol"},{"key":"ref4","doi-asserted-by":"publisher","first-page":"e118","DOI":"10.1002\/ski2.118","article-title":"Primary cutaneous adenoid cystic carcinoma of the scalp: a case report, immunohistochemistry and review of the literature","volume":"2","author":"Temnithikul","year":"2022","journal-title":"Skin Health Dis"},{"key":"ref5","doi-asserted-by":"publisher","first-page":"407","DOI":"10.1111\/his.14565","article-title":"Primary cutaneous adenoid cystic carcinoma: a clinicopathologic, immunohistochemical, and fluorescence in-situ hybridisation study of 13 cases","volume":"80","author":"Lv","year":"2022","journal-title":"Histopathology"},{"key":"ref6","doi-asserted-by":"publisher","first-page":"1603","DOI":"10.1097\/PAS.0b013e318299fcac","article-title":"Primary cutaneous adenoid cystic carcinoma: a clinicopathologic and immunohistochemical study of 27 cases","volume":"37","author":"Ramakrishnan","year":"2013","journal-title":"Am J Surg Pathol"},{"key":"ref7","doi-asserted-by":"publisher","first-page":"e3","DOI":"10.4081\/rt.2011.e3","article-title":"A primary cutaneous adenoid-cystic carcinoma in a young woman. 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