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This report is the first description of a case of intermittent visual snow syndrome, which transformed into a persistent form following a posterior circulation stroke due to vertebral artery dissection. At 1 and 2 years after experiencing the acute cerebellar infarct, the patient's only neurological sequalae was visual snow. This case provides a description of how visual snow syndrome may be caused by an underlying brain disorder, and highlights the importance of the cerebellum in the pathophysiology of this relatively unknown condition. It further shows evidence of how existing predispositions might be relevant to the development of visual snow, in certain subjects and following specific circumstances.<\/jats:p>","DOI":"10.3389\/fneur.2022.811490","type":"journal-article","created":{"date-parts":[[2022,2,15]],"date-time":"2022-02-15T06:49:17Z","timestamp":1644907757000},"update-policy":"https:\/\/doi.org\/10.3389\/crossmark-policy","source":"Crossref","is-referenced-by-count":13,"title":["Case Report: Transformation of Visual Snow Syndrome From Episodic to Chronic Associated With Acute Cerebellar Infarct"],"prefix":"10.3389","volume":"13","author":[{"given":"Francesca","family":"Puledda","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mar\u00eda Dolores","family":"Villar-Mart\u00ednez","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Peter J.","family":"Goadsby","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1965","published-online":{"date-parts":[[2022,2,15]]},"reference":[{"key":"B1","doi-asserted-by":"publisher","first-page":"1419","DOI":"10.1093\/brain\/awu050","article-title":"\u2018Visual snow' - a disorder distinct from persistent migraine aura","volume":"137","author":"Schankin","year":"2014","journal-title":"Brain"},{"key":"B2","doi-asserted-by":"publisher","first-page":"764","DOI":"10.1111\/ene.14150","article-title":"Prevalence of visual snow syndrome in the UK","volume":"27","author":"Kondziella","year":"2020","journal-title":"Eur J Neurol."},{"key":"B3","doi-asserted-by":"publisher","first-page":"e564","DOI":"10.1212\/WNL.0000000000008909","article-title":"Visual snow syndrome. 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