{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,3]],"date-time":"2026-07-03T06:21:46Z","timestamp":1783059706319,"version":"3.54.6"},"reference-count":26,"publisher":"Frontiers Media SA","license":[{"start":{"date-parts":[[2026,7,3]],"date-time":"2026-07-03T00:00:00Z","timestamp":1783036800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["frontiersin.org"],"crossmark-restriction":true},"short-container-title":["Front. Surg."],"abstract":"<jats:sec>\n                    <jats:title>Objectives<\/jats:title>\n                    <jats:p>Several syndromes, including Jeune's syndrome and Sensenbrenner's syndrome, can cause thoracic chondrodysplasia in children, leading to various degrees of thoracic insufficiency syndrome. Surgical management if often necessary and numerous surgical techniques have been described in the past, but all of these offer rigid solutions, which are incompatible with growth, and full recovery of ventilatory dynamics. We describe a new surgical technique for these patients, which offers a complete mobile thoracic replacement.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>We present the case of two patients with Jeune and Sensenbrenner syndromes in whom we performed a complete thoracic replacement. We used the Multidirectional Thoracic Wall Stabilization (MTS) system, (StraTos\u2122 MedXpert's), in order to recreate a mobile thorax, allow for recovery of ventilatory dynamics and enable thoracic growth.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>Both surgeries were successful. Long-term follow-up (&amp;gt;4 years), shows both patients regained respiratory autonomy for acts of daily routine, increased their walking perimeter and increased their lung volumes.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion<\/jats:title>\n                    <jats:p>Total thoracic replacement is safe and feasible for thoracic dysplasia in children. Further experience is needed to formally compare outcomes with the traditional techniques.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.3389\/fsurg.2026.1725855","type":"journal-article","created":{"date-parts":[[2026,7,3]],"date-time":"2026-07-03T05:40:58Z","timestamp":1783057258000},"update-policy":"https:\/\/doi.org\/10.3389\/crossmark-policy","source":"Crossref","is-referenced-by-count":0,"title":["Case Report: Surgical management of thoracic chondrodysplasia in children: complete mobile thoracic replacement"],"prefix":"10.3389","volume":"13","author":[{"given":"Lucie","family":"Louis","sequence":"first","affiliation":[{"name":"CHU de Bordeaux, Service de Chirurgie P\u00e9diatrique","place":["Bordeaux, France"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Luke","family":"Harper","sequence":"additional","affiliation":[{"name":"CHU de Bordeaux, Service de Chirurgie P\u00e9diatrique","place":["Bordeaux, France"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jean-David","family":"Maes","sequence":"additional","affiliation":[{"name":"CHU de Bordeaux, Service D\u2019Imagerie Cardiaque et Thoracique","place":["Pessac, France"]}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fr\u00e9d\u00e9ric","family":"Lavrand","sequence":"additional","affiliation":[{"name":"CHU de Bordeaux, Service de Chirurgie P\u00e9diatrique","place":["Bordeaux, France"]}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1965","published-online":{"date-parts":[[2026,7,3]]},"reference":[{"key":"B1","doi-asserted-by":"publisher","first-page":"18","DOI":"10.1055\/s-0036-1593841","article-title":"Ciliopathies: genetics in pediatric medicine","volume":"6","author":"Oud","year":"2017","journal-title":"J Pediatr Genet."},{"key":"B2","doi-asserted-by":"publisher","first-page":"163","DOI":"10.1016\/j.jgyn.2008.12.005","article-title":"Dysplasie thoracique asphyxiante ou syndrome de jeune: \u00e0 propos de deux cas","volume":"39","author":"Harou","year":"2010","journal-title":"J Gynecol Obstet Biol Reprod"},{"key":"B3","doi-asserted-by":"publisher","first-page":"77","DOI":"10.1007\/s00431-009-0991-3","article-title":"Jeune syndrome: description of 13 cases and a proposal for follow-up protocol","volume":"169","author":"de Vries","year":"2010","journal-title":"Eur J Pediatr"},{"key":"B4","doi-asserted-by":"publisher","first-page":"758","DOI":"10.1136\/adc.52.10.758","article-title":"Asphyxiating thoracic dysplasia. 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