{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,11]],"date-time":"2025-10-11T01:36:15Z","timestamp":1760146575086,"version":"build-2065373602"},"reference-count":37,"publisher":"MDPI AG","issue":"11","license":[{"start":{"date-parts":[[2024,11,20]],"date-time":"2024-11-20T00:00:00Z","timestamp":1732060800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"name":"S\u00e3o Paulo State Research Support Foundation (FAPESP)","award":["2021\/02189-0"],"award-info":[{"award-number":["2021\/02189-0"]}]}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Children"],"abstract":"<jats:p>Background: Hirschsprung\u2019s disease (HD) is a congenital malformation of the enteric nervous system clinically manifested by intestinal obstruction in the neonatal period or severe constipation in childhood. Several surveys on HD have been conducted to evaluate experiences in its management around the world. For the first time in Brazil, we analyze and report the management patterns of HD among pediatric surgeons in Brazil. Methods: A validated questionnaire was disseminated in print at the Congress of Pediatric Surgery in S\u00e3o Paulo-Brazil, and an online version was sent to all the active members of the Brazilian and Paulista Institute of Pediatric Surgery. Results: In total, 361 pediatric surgeons answered the survey. Of these, 329 completed all questions (response rate: 91%). Most Brazilian services treat fewer than 10 cases of HD annually. The preferred diagnostic method was rectal biopsy. For newborns (NBs) and infants, open biopsy was the most commonly used technique. For NBs with HD clinically stable 50% of specialists chose immediate surgery. In NBs and infants with classic HD, the Soave technique (69%) is the most common surgical intervention, and the transanal route (80%) is the preferred surgical approach. In children over 3 years of age with classic HD, the most-used technique is the Duhamel method (54%), with the open approach being the most common (52%). Conclusions: Our study in Brazil found that HD patient management aligns with scientific evidence and international guidelines.<\/jats:p>","DOI":"10.3390\/children11111405","type":"journal-article","created":{"date-parts":[[2024,11,20]],"date-time":"2024-11-20T03:57:04Z","timestamp":1732075024000},"page":"1405","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Management of Hirschsprung\u2019s Disease: A Survey with Brazilian Pediatric Surgeons"],"prefix":"10.3390","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6327-1367","authenticated-orcid":false,"given":"Cesar Saul Quevedo","family":"Penaloza","sequence":"first","affiliation":[{"name":"Botucatu Medical School, S\u00e3o Paulo State University (UNESP), Botucatu 18618-970, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alana Carnevale","family":"Barreto","sequence":"additional","affiliation":[{"name":"Botucatu Medical School, S\u00e3o Paulo State University (UNESP), Botucatu 18618-970, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9697-3450","authenticated-orcid":false,"given":"Erika Veruska Paiva","family":"Ortolan","sequence":"additional","affiliation":[{"name":"Botucatu Medical School, S\u00e3o Paulo State University (UNESP), Botucatu 18618-970, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Augusto","family":"Zani","sequence":"additional","affiliation":[{"name":"Department of Surgery, Division of General and Thoracic Surgery, The Hospital for Sick Children, University of Toronto, Toronto, ON M5G 1E8, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8753-646X","authenticated-orcid":false,"given":"Pedro Luiz Toledo de Arruda","family":"Lourenc\u0327\u00e3o","sequence":"additional","affiliation":[{"name":"Botucatu Medical School, S\u00e3o Paulo State University (UNESP), Botucatu 18618-970, S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1968","published-online":{"date-parts":[[2024,11,20]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"942","DOI":"10.1067\/j.cpsurg.2004.09.004","article-title":"Hirschsprung disease","volume":"41","author":"Dasgupta","year":"2004","journal-title":"Curr. 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