{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,9]],"date-time":"2026-01-09T13:30:12Z","timestamp":1767965412766,"version":"3.49.0"},"reference-count":13,"publisher":"MDPI AG","issue":"6","license":[{"start":{"date-parts":[[2022,12,14]],"date-time":"2022-12-14T00:00:00Z","timestamp":1670976000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Clinics and Practice"],"abstract":"<jats:p>Polycythemia vera (PV) is one of the three main classic disorders of Philadelphia-negative myeloproliferative neoplasms (MPNs), with the other two being essential thrombocythemia (ET) and primary myelofibrosis (PMF). PV may develop (15%) in women of childbearing age (15\u201345 years), with an anticipated rate of roughly 0.3 per 100,000 people, although maintaining a male to female ratio predominance of about 2:1 and a peak prevalence in the sixth and seventh decades of life. Without always being presented with its actual clinical manifestations due to pregnancy itself, and most commonly due to iron deficiency, PV can be frequently missed and therefore belatedly diagnosed. We describe the case of a primipara woman in her 40s, without risk factors for thrombosis, who developed a portal vein occlusion 1.5 month postpartum after C-section and who had a delayed diagnosis of PV.<\/jats:p>","DOI":"10.3390\/clinpract12060109","type":"journal-article","created":{"date-parts":[[2022,12,14]],"date-time":"2022-12-14T03:21:52Z","timestamp":1670988112000},"page":"1069-1077","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["Portal Vein Thrombosis after C-Section in a Patient with Polycythemia Vera (PV) Due to Pregnancy and Iron Deficiency Anemia (IDA)"],"prefix":"10.3390","volume":"12","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-4594-8308","authenticated-orcid":false,"given":"Thomas","family":"Ntounis","sequence":"first","affiliation":[{"name":"1st Department of Obstetrics and Gynecology, National and Kapodistrian University of Athens, General Hospital of Athens \u2018ALEXANDRA\u2019, Lourou and Vasilissis Sofias Ave, 11528 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Konstantinos A.","family":"Zioutos","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology-Kastoria General Hospital, Mavriotissis 33, 52100 Kastoria, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7229-9983","authenticated-orcid":false,"given":"Antonios","family":"Koutras","sequence":"additional","affiliation":[{"name":"1st Department of Obstetrics and Gynecology, National and Kapodistrian University of Athens, General Hospital of Athens \u2018ALEXANDRA\u2019, Lourou and Vasilissis Sofias Ave, 11528 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ioannis","family":"Prokopakis","sequence":"additional","affiliation":[{"name":"1st Department of Obstetrics and Gynecology, National and Kapodistrian University of Athens, General Hospital of Athens \u2018ALEXANDRA\u2019, Lourou and Vasilissis Sofias Ave, 11528 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-0216-3420","authenticated-orcid":false,"given":"Zacharias","family":"Fasoulakis","sequence":"additional","affiliation":[{"name":"1st Department of Obstetrics and Gynecology, National and Kapodistrian University of Athens, General Hospital of Athens \u2018ALEXANDRA\u2019, Lourou and Vasilissis Sofias Ave, 11528 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ioakeim","family":"Sapantzoglou","sequence":"additional","affiliation":[{"name":"1st Department of Obstetrics and Gynecology, National and Kapodistrian University of Athens, General Hospital of Athens \u2018ALEXANDRA\u2019, Lourou and Vasilissis Sofias Ave, 11528 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Paraskevas","family":"Perros","sequence":"additional","affiliation":[{"name":"1st Department of Obstetrics and Gynecology, National and Kapodistrian University of Athens, General Hospital of Athens \u2018ALEXANDRA\u2019, Lourou and Vasilissis Sofias Ave, 11528 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6177-7281","authenticated-orcid":false,"given":"Athina A.","family":"Samara","sequence":"additional","affiliation":[{"name":"Department of Embryology, University General Hospital of Larissa, Mezourlo, 41110 Larissa, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4985-5862","authenticated-orcid":false,"given":"Emmanouil","family":"Spanoudakis","sequence":"additional","affiliation":[{"name":"Department of Hematology, Democritus University of Thrace, University General Hospital of Alexandroupolis, 6th km Alexandroupolis\u2013Makris, Dragana, 68100 Alexandroupolis, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Asimina","family":"Valsamaki","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, General Hospital of Larisa, Tsakalof 1, 41221 Larisa, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sevasti-Effraimia","family":"Krouskou","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology, Democritus University of Thrace, 6th km Alexandroupolis\u2013Makris, 68100 Alexandroupolis, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Konstantinos","family":"Nikolettos","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology, Democritus University of Thrace, 6th km Alexandroupolis\u2013Makris, 68100 Alexandroupolis, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Vasileios-Chrysovalantis","family":"Palios","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology, University General Hospital of Larissa, Mezourlo, 41110 Larissa, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Paschalis","family":"Mousios","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology, University General Hospital of Larissa, Mezourlo, 41110 Larissa, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kallirroi","family":"Goula","sequence":"additional","affiliation":[{"name":"Department of Pathology, Alexandra General Hospital of Athens, 11528 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kyriakos","family":"Konis","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology, General Hospital of Arta, 47100 Arta, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Athanasios","family":"Chionis","sequence":"additional","affiliation":[{"name":"Department of Gynecology, Laiko General Hospital of Athens, Agiou Thoma 17, 11527 Athens, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Emmanuel N.","family":"Kontomanolis","sequence":"additional","affiliation":[{"name":"Department of Obstetrics and Gynecology, Democritus University of Thrace, 6th km Alexandroupolis\u2013Makris, 68100 Alexandroupolis, Greece"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1968","published-online":{"date-parts":[[2022,12,14]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"31","DOI":"10.1111\/bjh.14289","article-title":"Pregnancy outcomes in myeloproliferative neoplasms: UK prospective cohort study","volume":"175","author":"Alimam","year":"2016","journal-title":"Br. 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Blood Marrow Transplant."},{"key":"ref_11","doi-asserted-by":"crossref","first-page":"15","DOI":"10.1038\/s41408-018-0054-y","article-title":"The 2016 WHO classification and diagnostic criteria for myeloproliferative neoplasms: Document summary and in-depth discussion","volume":"8","author":"Barbui","year":"2018","journal-title":"Blood Cancer J."},{"key":"ref_12","doi-asserted-by":"crossref","first-page":"422","DOI":"10.1055\/s-2006-942763","article-title":"Essential thrombocythemia\/polycythemia vera and pregnancy: The need for an observational study in Europe","volume":"32","author":"Griesshammer","year":"2006","journal-title":"Semin. Thromb. Hemost."},{"key":"ref_13","doi-asserted-by":"crossref","first-page":"697","DOI":"10.1080\/17474086.2018.1506325","article-title":"Contemporary management of patients with BCR-ABL1-negative myeloproliferative neoplasms during pregnancy","volume":"11","author":"Griesshammer","year":"2018","journal-title":"J. Expert Rev. Hematol."}],"container-title":["Clinics and Practice"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.mdpi.com\/2039-7283\/12\/6\/109\/pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,10,11]],"date-time":"2025-10-11T01:40:53Z","timestamp":1760146853000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.mdpi.com\/2039-7283\/12\/6\/109"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,12,14]]},"references-count":13,"journal-issue":{"issue":"6","published-online":{"date-parts":[[2022,12]]}},"alternative-id":["clinpract12060109"],"URL":"https:\/\/doi.org\/10.3390\/clinpract12060109","relation":{},"ISSN":["2039-7283"],"issn-type":[{"value":"2039-7283","type":"electronic"}],"subject":[],"published":{"date-parts":[[2022,12,14]]}}}