{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,20]],"date-time":"2026-10-20T16:48:25Z","timestamp":1792514905771,"version":"4.5.0"},"reference-count":28,"publisher":"MDPI AG","issue":"9","license":[{"start":{"date-parts":[[2020,9,11]],"date-time":"2020-09-11T00:00:00Z","timestamp":1599782400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"DOI":"10.13039\/501100012190","name":"Ministry of Science and Higher Education of the Russian Federation","doi-asserted-by":"publisher","award":["\u2116075-15-2019-1789 to the Center for Precision Genome Editing and Genetic Technologies for Biomedicine"],"award-info":[{"award-number":["\u2116075-15-2019-1789 to the Center for Precision Genome Editing and Genetic Technologies for Biomedicine"]}],"id":[{"id":"10.13039\/501100012190","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Diagnostics"],"abstract":"<jats:p>This prospective study enrolled 144 patients after surgical treatment of biliary atresia in early infancy. We analyzed the immediate effectiveness of the surgery and the age-related structure of complications in the up to 16-year follow-up. The immediate 2-year survival rate after the surgery constituted 49.5%. At the time of this writing, 17 of the patients had celebrated their 10th birthdays with good quality of life and no indications for transplantation of the liver. The obtained results underscore the critical importance of surgical correction of biliary atresia by Kasai surgery in the first 60 days of life and subsequent dynamic follow-up of patients for the purpose of the early detection and timely correction of possible complications.<\/jats:p>","DOI":"10.3390\/diagnostics10090686","type":"journal-article","created":{"date-parts":[[2020,9,11]],"date-time":"2020-09-11T09:05:16Z","timestamp":1599815116000},"page":"686","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":13,"title":["Long-Term Effects of Kasai Portoenterostomy for Biliary Atresia Treatment in Russia"],"prefix":"10.3390","volume":"10","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-0822-751X","authenticated-orcid":false,"given":"Anna","family":"Degtyareva","sequence":"first","affiliation":[{"name":"Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology, 4 Oparina Street, 117997 Moscow, Russia"},{"name":"Neonatology Department, Sechenov University, 8 Trubetskaya Street, 119991 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alexander","family":"Razumovskiy","sequence":"additional","affiliation":[{"name":"Center for Precision Genome Editing and Genetic Technologies for Biomedicine, Pirogov Russian National Research Medical University, 1 Ostrovityanova Street, 117997 Moscow, Russia"},{"name":"Filatov Munitsipal Children\u2019s Hospital, 15 Sadovaya-Kudrinskaya Street, 123001 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nadezhda","family":"Kulikova","sequence":"additional","affiliation":[{"name":"Filatov Munitsipal Children\u2019s Hospital, 15 Sadovaya-Kudrinskaya Street, 123001 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sergey","family":"Ratnikov","sequence":"additional","affiliation":[{"name":"National Medical Research Center for Children\u2019s Health, 2 Lomonosovsky Prospect, 119296 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Elena","family":"Filippova","sequence":"additional","affiliation":[{"name":"Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology, 4 Oparina Street, 117997 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ekaterina","family":"Gordeeva","sequence":"additional","affiliation":[{"name":"Filatov Munitsipal Children\u2019s Hospital, 15 Sadovaya-Kudrinskaya Street, 123001 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marina","family":"Albegova","sequence":"additional","affiliation":[{"name":"Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology, 4 Oparina Street, 117997 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1884-1807","authenticated-orcid":false,"given":"Denis","family":"Rebrikov","sequence":"additional","affiliation":[{"name":"Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology, 4 Oparina Street, 117997 Moscow, Russia"},{"name":"Center for Precision Genome Editing and Genetic Technologies for Biomedicine, Pirogov Russian National Research Medical University, 1 Ostrovityanova Street, 117997 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anna","family":"Puchkova","sequence":"additional","affiliation":[{"name":"Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology, 4 Oparina Street, 117997 Moscow, Russia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1968","published-online":{"date-parts":[[2020,9,11]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"175","DOI":"10.1053\/j.sempedsurg.2012.05.010","article-title":"Biliary atresia: Clinical aspects","volume":"21","author":"Davenport","year":"2012","journal-title":"Semin. Pediatr. Surg."},{"key":"ref_2","doi-asserted-by":"crossref","unstructured":"Chardot, C. (2006). Biliary atresia. Orphanet J. Rare Dis., 28.","DOI":"10.1186\/1750-1172-1-28"},{"key":"ref_3","doi-asserted-by":"crossref","first-page":"129","DOI":"10.1620\/tjem.99.129","article-title":"Intrahepatic Biliary Obstruction in Congenital Bile Duct Atresia","volume":"99","author":"Kasai","year":"1969","journal-title":"Tohoku J. Exp. Med."},{"key":"ref_4","doi-asserted-by":"crossref","first-page":"1341","DOI":"10.1007\/s00383-017-4171-7","article-title":"Laparoscopic portoenterostomy for biliary atresia: Single-center experience and review of literatures","volume":"33","author":"Cazares","year":"2017","journal-title":"Pediatr. Surg. Int."},{"key":"ref_5","first-page":"234","article-title":"Long-term prognosis and factors affecting atresia from experience over a 25 year period","volume":"29","author":"Lai","year":"2006","journal-title":"Chang. Gung Med. 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