{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,5]],"date-time":"2026-03-05T15:04:39Z","timestamp":1772723079739,"version":"3.50.1"},"reference-count":21,"publisher":"MDPI AG","issue":"1","license":[{"start":{"date-parts":[[2020,12,28]],"date-time":"2020-12-28T00:00:00Z","timestamp":1609113600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["IJERPH"],"abstract":"<jats:p>Ectodermal dysplasia (ED) refers to a heterogeneous group of genetic diseases of the skin, skin appendages, and teeth. People with ED experience a poorer oral health-related quality of life (OHRQoL) compared to the general population. The aim of this study was to examine the OHRQoL of people with ED and to measure their objective physical oral health to confirm or disprove evidence of poorer oral health in this population. To determine OHRQoL, the German version of the 14-item Oral Health Impact Profile (OHIP-14G) was used. All the participants in the study were clinically examined, and the measured parameters were recorded using the Physical Oral Health Index (PhOX). In total, 10 male and 11 female participants, with an average age of 22.0 \u00b1 9.0 years, were included in this study. The OHIP-14G summary score was 23.9 (\u00b115.2) points (range: 0\u201356 points). The PhOX summary score was 61.2 (\u00b15.1) points (range: 22\u201380 points). The findings indicated that both the OHRQoL and physical oral health of the participants were highly impaired and that their objective and subjective oral health were worse than those of the general population in Germany.<\/jats:p>","DOI":"10.3390\/ijerph18010143","type":"journal-article","created":{"date-parts":[[2020,12,28]],"date-time":"2020-12-28T10:33:56Z","timestamp":1609151636000},"page":"143","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":10,"title":["Subjective Oral Health-Related Quality of Life and Objective Oral Health in People with Ectodermal Dysplasia"],"prefix":"10.3390","volume":"18","author":[{"given":"Nils","family":"Niekamp","sequence":"first","affiliation":[{"name":"Department of Cranio-Maxillofacial Surgery, Research Unit Rare Diseases with Orofacial Manifestations, University Hospital M\u00fcnster, Albert-Schweitzer-Campus 1, Building W 30, D-48149 M\u00fcnster, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Johannes","family":"Kleinheinz","sequence":"additional","affiliation":[{"name":"Department of Cranio-Maxillofacial Surgery, Research Unit Rare Diseases with Orofacial Manifestations, University Hospital M\u00fcnster, Albert-Schweitzer-Campus 1, Building W 30, D-48149 M\u00fcnster, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Daniel R.","family":"Reissmann","sequence":"additional","affiliation":[{"name":"Department of Prosthetic Dentistry, Center for Dental and Oral Medicine, University Medical Center Hamburg-Eppendorf, Martinistrasse 52, D-20251 Hamburg, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3637-3928","authenticated-orcid":false,"given":"Lauren","family":"Bohner","sequence":"additional","affiliation":[{"name":"Department of Cranio-Maxillofacial Surgery, Research Unit Rare Diseases with Orofacial Manifestations, University Hospital M\u00fcnster, Albert-Schweitzer-Campus 1, Building W 30, D-48149 M\u00fcnster, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marcel","family":"Hanisch","sequence":"additional","affiliation":[{"name":"Department of Cranio-Maxillofacial Surgery, Research Unit Rare Diseases with Orofacial Manifestations, University Hospital M\u00fcnster, Albert-Schweitzer-Campus 1, Building W 30, D-48149 M\u00fcnster, Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1968","published-online":{"date-parts":[[2020,12,28]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"1035","DOI":"10.1016\/j.ijom.2016.03.011","article-title":"Clinical outcomes of implant therapy in ectodermal dysplasia patients: A systematic review","volume":"45","author":"Wang","year":"2016","journal-title":"Int. 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