{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,7]],"date-time":"2026-10-07T20:38:19Z","timestamp":1791405499531,"version":"4.3.3"},"reference-count":72,"publisher":"MDPI AG","issue":"12","license":[{"start":{"date-parts":[[2022,6,18]],"date-time":"2022-06-18T00:00:00Z","timestamp":1655510400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["IJERPH"],"abstract":"<jats:p>Hajdu\u2013Cheney syndrome is a rare genetic disease. Its main features include phenotypic variability, age-dependent progression and the presence of acroosteolysis of the distal phalanges and generalized osteoporosis, which have significant disabling potential. Currently, there is no effective curative treatment, so nursing care is essential to ensure the maintenance of the quality of life of these patients. The main objective of this study was to establish a specific standardized nursing care plan using the NANDA\u2013NIC\u2013NOC taxonomy. The application of a care plan as such would improve the quality of life of patients affected by this rare disease, will contribute to increasing healthcare professionals\u2019 knowledge on this matter and will support future studies on this disease.<\/jats:p>","DOI":"10.3390\/ijerph19127489","type":"journal-article","created":{"date-parts":[[2022,6,18]],"date-time":"2022-06-18T09:51:11Z","timestamp":1655545871000},"page":"7489","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":4,"title":["Nursing Care Plan for Patients with Hajdu\u2013Cheney Syndrome"],"prefix":"10.3390","volume":"19","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-4019-8555","authenticated-orcid":false,"given":"Jonathan","family":"Cort\u00e9s-Mart\u00edn","sequence":"first","affiliation":[{"name":"Research Group CTS1068, Andalusia Research Plan, Junta de Andaluc\u00eda, 18014 Granada, Spain"},{"name":"Faculty of Health Sciences, School of Nursing, University of Granada, 18071 Granada, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7906-5656","authenticated-orcid":false,"given":"Lourdes","family":"D\u00edaz-Rodr\u00edguez","sequence":"additional","affiliation":[{"name":"Research Group CTS1068, Andalusia Research Plan, Junta de Andaluc\u00eda, 18014 Granada, Spain"},{"name":"Faculty of Health Sciences, School of Nursing, University of Granada, 18071 Granada, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Beatriz","family":"Piqueras-Sola","sequence":"additional","affiliation":[{"name":"Research Group CTS1068, Andalusia Research Plan, Junta de Andaluc\u00eda, 18014 Granada, Spain"},{"name":"Hospital University Virgen de las Nieves, 18014 Granada, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4650-2159","authenticated-orcid":false,"given":"Juan Carlos","family":"S\u00e1nchez-Garc\u00eda","sequence":"additional","affiliation":[{"name":"Research Group CTS1068, Andalusia Research Plan, Junta de Andaluc\u00eda, 18014 Granada, Spain"},{"name":"Faculty of Health Sciences, School of Nursing, University of Granada, 18071 Granada, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-0425-9135","authenticated-orcid":false,"given":"Mar\u00eda Jos\u00e9","family":"Menor-Rodr\u00edguez","sequence":"additional","affiliation":[{"name":"Subdirectora de Humanizaci\u00f3n y Atenci\u00f3n al Ciudadano, \u00c1rea Sanitaria Santiago-Barbanza, 15706 Santiago de Compostela, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Raquel","family":"Rodr\u00edguez-Blanque","sequence":"additional","affiliation":[{"name":"Research Group CTS1068, Andalusia Research Plan, Junta de Andaluc\u00eda, 18014 Granada, Spain"},{"name":"Faculty of Health Sciences, School of Nursing, University of Granada, 18071 Granada, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1968","published-online":{"date-parts":[[2022,6,18]]},"reference":[{"key":"ref_1","unstructured":"(2022, April 20). 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