{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,24]],"date-time":"2026-01-24T07:17:32Z","timestamp":1769239052024,"version":"3.49.0"},"reference-count":40,"publisher":"MDPI AG","issue":"16","license":[{"start":{"date-parts":[[2022,8,11]],"date-time":"2022-08-11T00:00:00Z","timestamp":1660176000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"name":"Johannes Kepler Open Access Publishing Fund"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["IJERPH"],"abstract":"<jats:p>Individuals who are prelingually deaf and have intellectual disabilities experience great challenges in their language, cognitive and social development, leading to heterogeneous profiles of intellectual and adaptive functioning. The present study describes these profiles, paying particular attention to domain discrepancies, and explores their associations with quality of life and maladaptive behavior. Twenty-nine adults with prelingual deafness (31% female) and mild intellectual functioning deficits (mean IQ = 67.3, SD = 6.5) were administered the Vineland Adaptive Behavior Scales-II (VABS-II) and an adapted sign language version of a quality of life scale (EUROHIS-QOL 8). Intellectual disability domain discrepancies were characterized as at least one standard deviation difference between the social domain and IQ and the practical domain and IQ, and a significant difference, according to the VABS-II manual, between the social and practical domains. Domain discrepancies were found between intellectual functioning and both the practical (58.6%) and social domain (65.5%). A discrepancy between intellectual and social functioning was significantly associated with a higher level of internalizing maladaptive behavior (T = 1.89, p &lt; 0.05). The heterogeneous profiles highlight the importance of comprehensive assessments for adequate service provision.<\/jats:p>","DOI":"10.3390\/ijerph19169919","type":"journal-article","created":{"date-parts":[[2022,8,11]],"date-time":"2022-08-11T21:15:05Z","timestamp":1660252505000},"page":"9919","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":4,"title":["Intellectual Disability Profiles, Quality of Life and Maladaptive Behavior in Deaf Adults: An Exploratory Study"],"prefix":"10.3390","volume":"19","author":[{"given":"Johanna","family":"Eisinger","sequence":"first","affiliation":[{"name":"Research Institute for Developmental Medicine, Johannes Kepler University, 4020 Linz, Austria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Magdalena","family":"Dall","sequence":"additional","affiliation":[{"name":"Research Institute for Developmental Medicine, Johannes Kepler University, 4020 Linz, Austria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jason","family":"Fogler","sequence":"additional","affiliation":[{"name":"Research Institute for Developmental Medicine, Johannes Kepler University, 4020 Linz, Austria"},{"name":"Division of Developmental Medicine, Boston Children\u2019s Hospital, Boston, MA 02115, USA"},{"name":"Leadership Education in Neurodevelopmental and Related Disabilities\/Institute for Community Inclusion (LEND\/ICI), Boston Children\u2019s Hospital, Boston, MA 02115, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6634-6117","authenticated-orcid":false,"given":"Daniel","family":"Holzinger","sequence":"additional","affiliation":[{"name":"Research Institute for Developmental Medicine, Johannes Kepler University, 4020 Linz, Austria"},{"name":"Institute of Neurology of Senses and Language, Hospital of St. John of God, 4020 Linz, Austria"},{"name":"Institute of Linguistics, University of Graz, 8010 Graz, Austria"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Johannes","family":"Fellinger","sequence":"additional","affiliation":[{"name":"Research Institute for Developmental Medicine, Johannes Kepler University, 4020 Linz, Austria"},{"name":"Institute of Neurology of Senses and Language, Hospital of St. John of God, 4020 Linz, Austria"},{"name":"Division of Social Psychiatry, University Clinic for Psychiatry and Psychotherapy, Medical University of Vienna, 1090 Vienna, Austria"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1968","published-online":{"date-parts":[[2022,8,11]]},"reference":[{"key":"ref_1","unstructured":"World Health Organization (2022, July 12). 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