{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,12]],"date-time":"2025-10-12T04:51:12Z","timestamp":1760244672977,"version":"build-2065373602"},"reference-count":25,"publisher":"MDPI AG","issue":"12","license":[{"start":{"date-parts":[[2022,11,26]],"date-time":"2022-11-26T00:00:00Z","timestamp":1669420800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"name":"Investigation Department of Fundaci\u00f3n Cardioinfantil-LaCardio"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["JCDD"],"abstract":"<jats:p>A 35-year-old female presented to our emergency department with clinical signs of acute heart failure. Clinical workup identified severe right heart (RH) dilation and dysfunction with a crossing membrane structure in the right atrium. Right heart catheterization confirmed high output heart failure (HOHF), pulmonary hypertension (PH), and left-to-right blood shunting followed by the documentation of multiple liver and pulmonary arteriovenous malformations (AVMs). Hereditary Hemorrhagic Telangiectasia (HHT) diagnosis was made according to clinical criteria and was established as the cause of HOHF because of chronic volume overload from systemic to pulmonary shunts. With this illustrative case, we aim to discuss the broad spectrum of clinical manifestations of HHT and the unusual phenotype of HOHF secondary to HHT. This case also highlights the broad diagnosis of atrial echocardiographic abnormalities and cardiac structural distortion secondary to high output that can be misleading at imaging evaluation.<\/jats:p>","DOI":"10.3390\/jcdd9120418","type":"journal-article","created":{"date-parts":[[2022,11,28]],"date-time":"2022-11-28T04:56:25Z","timestamp":1669611385000},"page":"418","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["An Unusual Cause of Right Heart Dysfunction and High Output Heart Failure in a Young Woman"],"prefix":"10.3390","volume":"9","author":[{"given":"Nicol\u00e1s","family":"Ariza Ordo\u00f1ez","sequence":"first","affiliation":[{"name":"Department of Internal Medicine, Fundaci\u00f3n Cardioinfantil\u2014La Cardio, Bogot\u00e1 110131, Colombia"},{"name":"School of Medicine and Health Sciences, Universidad del Rosario, Bogot\u00e1 110131, Colombia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6065-0078","authenticated-orcid":false,"given":"Antonia","family":"Pino Mar\u00edn","sequence":"additional","affiliation":[{"name":"School of Medicine and Health Sciences, Universidad del Rosario, Bogot\u00e1 110131, Colombia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4907-0398","authenticated-orcid":false,"given":"Juan Sebasti\u00e1n","family":"Bonilla Crespo","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Fundaci\u00f3n Cardioinfantil\u2014La Cardio, Bogot\u00e1 110131, Colombia"},{"name":"School of Medicine and Health Sciences, Universidad del Rosario, Bogot\u00e1 110131, Colombia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7428-1859","authenticated-orcid":false,"given":"Alberto","family":"Navarro Navajas","sequence":"additional","affiliation":[{"name":"Department of Cardiology, Fundaci\u00f3n Cardioinfantil\u2014La Cardio, Bogot\u00e1 110131, Colombia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gabriel Antonio","family":"Oliver","sequence":"additional","affiliation":[{"name":"Department of Cardiology, Fundaci\u00f3n Cardioinfantil\u2014La Cardio, Bogot\u00e1 110131, Colombia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hector M.","family":"Medina","sequence":"additional","affiliation":[{"name":"Division of Cardiovascular Imaging, Fundaci\u00f3n Cardioinfantil\u2014La Cardio, Bogot\u00e1 110131, Colombia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Juli\u00e1n F.","family":"Forero","sequence":"additional","affiliation":[{"name":"Division of Cardiovascular Imaging, Fundaci\u00f3n Cardioinfantil\u2014La Cardio, Bogot\u00e1 110131, Colombia"},{"name":"Department of Radiology and Diagnostic Imaging, Fundaci\u00f3n Cardioinfantil\u2014La Cardio, Bogot\u00e1 110131, Colombia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"1968","published-online":{"date-parts":[[2022,11,26]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"18","DOI":"10.7812\/TPP\/18-145","article-title":"Assessing the Hereditary Hemorrhagic Telangiectasia Algorithms in a Community-Based Patient Population","volume":"23","author":"Saparia","year":"2019","journal-title":"Perm. 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