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CM1 can cause dysfunction of the brainstem, spinal cord, and cranial nerves. This functional alteration of the nervous system can be detected by various modalities of neurophysiological tests, such as brainstem auditory evoked potentials, somatosensory evoked potentials, motor evoked potentials, electromyography and nerve conduction studies of the cranial nerves and spinal roots, as well as brainstem reflexes. The main goal of this study is to review the findings of multimodal neurophysiological examinations in published studies of patients with CM1 and their indication in the diagnosis, treatment, and follow-up of these patients, as well as their utility in intraoperative monitoring.<\/jats:p>","DOI":"10.3390\/jcm12206472","type":"journal-article","created":{"date-parts":[[2023,10,12]],"date-time":"2023-10-12T03:14:32Z","timestamp":1697080472000},"page":"6472","update-policy":"https:\/\/doi.org\/10.3390\/mdpi_crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["The Role of Neurophysiology in Managing Patients with Chiari Malformations"],"prefix":"10.3390","volume":"12","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-2877-8239","authenticated-orcid":false,"given":"Dulce","family":"Moncho","sequence":"first","affiliation":[{"name":"Department of Clinical Neurophysiology, Vall d\u2019Hebron University Hospital, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"},{"name":"Neurotraumatology and Neurosurgery Research Unit, Vall d\u2019Hebron Institut de Recerca (VHIR), Vall d\u2019Hebron Barcelona Hospital Campus, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3831-0536","authenticated-orcid":false,"given":"Maria A.","family":"Poca","sequence":"additional","affiliation":[{"name":"Neurotraumatology and Neurosurgery Research Unit, Vall d\u2019Hebron Institut de Recerca (VHIR), Vall d\u2019Hebron Barcelona Hospital Campus, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"},{"name":"Department of Neurosurgery, Vall d\u2019Hebron University Hospital, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"},{"name":"Department of Surgery, Universitat Aut\u00f2noma de Barcelona, Bellaterra, 08193 Barcelona, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kimia","family":"Rahnama","sequence":"additional","affiliation":[{"name":"Department of Clinical Neurophysiology, Vall d\u2019Hebron University Hospital, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7952-6755","authenticated-orcid":false,"given":"M. \u00c1ngeles","family":"S\u00e1nchez Rold\u00e1n","sequence":"additional","affiliation":[{"name":"Department of Clinical Neurophysiology, Vall d\u2019Hebron University Hospital, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Daniela","family":"Santa-Cruz","sequence":"additional","affiliation":[{"name":"Department of Clinical Neurophysiology, Vall d\u2019Hebron University Hospital, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-0713-5875","authenticated-orcid":false,"given":"Juan","family":"Sahuquillo","sequence":"additional","affiliation":[{"name":"Neurotraumatology and Neurosurgery Research Unit, Vall d\u2019Hebron Institut de Recerca (VHIR), Vall d\u2019Hebron Barcelona Hospital Campus, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"},{"name":"Department of Neurosurgery, Vall d\u2019Hebron University Hospital, Passeig Vall d\u2019Hebron 119-129, 08035 Barcelona, Spain"},{"name":"Department of Surgery, Universitat Aut\u00f2noma de Barcelona, Bellaterra, 08193 Barcelona, Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1968","published-online":{"date-parts":[[2023,10,11]]},"reference":[{"key":"ref_1","first-page":"257","article-title":"Contribution to the Study of Spina Bifida, Encephalocele, and Anencephalus","volume":"17","author":"Cleland","year":"1883","journal-title":"J. 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